ICD-10-CM Codes
E00-E89 Endocrine, nutritional and metabolic diseases
E70-E88 Metabolic disorders
E71- Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
2020 ICD-10-CM Diagnosis Code E71.118

2020 ICD-10-CM Diagnosis Code E71.118

Other branched-chain organic acidurias

2016

2017

2018

2019

2020

Billable/Specific Code

E71.118 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2020 edition of ICD-10-CM E71.118 became effective on October 1, 2019.
This is the American ICD-10-CM version of E71.118 - other international versions of ICD-10 E71.118 may differ.

The following code(s) above E71.118 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to E71.118:

E00-E89
2020 ICD-10-CM Range E00-E89
Endocrine, nutritional and metabolic diseases
Note
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Type 1 Excludes
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Endocrine, nutritional and metabolic diseases
E70-E88
2020 ICD-10-CM Range E70-E88
Metabolic disorders
Type 1 Excludes
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- Ehlers-Danlos syndrome (Q79.6-)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan's syndrome (Q87.4)
- 5-alpha-reductase deficiency (E29.1)
Metabolic disorders

ICD-10-CM E71.118 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):

642 Inborn and other disorders of metabolism

Convert E71.118 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to E71.118:

Disorder (of) - see also Disease
- metabolism NOS E88.9
  ICD-10-CM Diagnosis Code E88.9
  Metabolic disorder, unspecified
  2016 2017 2018 2019 2020 Billable/Specific Code
  - amino-acid E72.9
    ICD-10-CM Diagnosis Code E72.9
    Disorder of amino-acid metabolism, unspecified
    2016 2017 2018 2019 2020 Billable/Specific Code
    - branched chain E71.2
      ICD-10-CM Diagnosis Code E71.2
      Disorder of branched-chain amino-acid metabolism, unspecified
      2016 2017 2018 2019 2020 Billable/Specific Code
      - organic aciduria NEC E71.118

ICD-10-CM Codes Adjacent To E71.118

E70.49 Other disorders of histidine metabolism

E70.5 Disorders of tryptophan metabolism

E70.8 Other disorders of aromatic amino-acid metabolism

E70.9 Disorder of aromatic amino-acid metabolism, unspecified

E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

E71.0 Maple-syrup-urine disease

E71.1 Other disorders of branched-chain amino-acid metabolism

E71.11 Branched-chain organic acidurias

E71.110 Isovaleric acidemia

E71.111 3-methylglutaconic aciduria

E71.118 Other branched-chain organic acidurias

E71.12 Disorders of propionate metabolism

E71.120 Methylmalonic acidemia

E71.121 Propionic acidemia

E71.128 Other disorders of propionate metabolism

E71.19 Other disorders of branched-chain amino-acid metabolism

E71.2 Disorder of branched-chain amino-acid metabolism, unspecified

E71.3 Disorders of fatty-acid metabolism

E71.30 Disorder of fatty-acid metabolism, unspecified

E71.31 Disorders of fatty-acid oxidation

E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2020 ICD-10-CM Diagnosis Code E71.118

Other branched-chain organic acidurias

Endocrine, nutritional and metabolic diseases

Metabolic disorders

Metabolic disorder, unspecified

Disorder of amino-acid metabolism, unspecified

Disorder of branched-chain amino-acid metabolism, unspecified