2019 ICD-10-CM Diagnosis Code E71.19

Other disorders of branched-chain amino-acid metabolism

    2016 2017 2018 2019 Billable/Specific Code
  • E71.19 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM E71.19 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of E71.19 - other international versions of ICD-10 E71.19 may differ.
Applicable To
  • Hyperleucine-isoleucinemia
  • Hypervalinemia
The following code(s) above E71.19 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to E71.19:
  • E00-E89
    2019 ICD-10-CM Range E00-E89

    Endocrine, nutritional and metabolic diseases

    Note
    • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
    Type 1 Excludes
    • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
    Endocrine, nutritional and metabolic diseases
  • E70-E88
    2019 ICD-10-CM Range E70-E88

    Metabolic disorders

    Type 1 Excludes
    • androgen insensitivity syndrome (E34.5-)
    • congenital adrenal hyperplasia (E25.0)
    • Ehlers-Danlos syndrome (Q79.6)
    • hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan's syndrome (Q87.4)
    • 5-alpha-reductase deficiency (E29.1)
    Metabolic disorders
ICD-10-CM E71.19 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 642 Inborn and other disorders of metabolism

Convert E71.19 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change

Diagnosis Index entries containing back-references to E71.19:
  • Disorder (of) - see also Disease
    • branched-chain amino-acid metabolism E71.2
      ICD-10-CM Diagnosis Code E71.2

      Disorder of branched-chain amino-acid metabolism, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      • specified NEC E71.19
    • metabolism NOS E88.9
      ICD-10-CM Diagnosis Code E88.9

      Metabolic disorder, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      • amino-acid E72.9
        ICD-10-CM Diagnosis Code E72.9

        Disorder of amino-acid metabolism, unspecified

          2016 2017 2018 2019 Billable/Specific Code
        • branched chain E71.2
          ICD-10-CM Diagnosis Code E71.2

          Disorder of branched-chain amino-acid metabolism, unspecified

            2016 2017 2018 2019 Billable/Specific Code
          • hyperleucine-isoleucinemia E71.19
          • hypervalinemia E71.19
          • other specified E71.19
      • isoleucine E71.19
      • leucine E71.19
      • valine E71.19
    • hyperleucine-isoleucinemia E71.19
    • hypervalinemia E71.19
  • Hyperleucine-isoleucinemia E71.19
  • Hypervalinemia E71.19
  • Hypoglycemia (spontaneous) E16.2
    ICD-10-CM Diagnosis Code E16.2

    Hypoglycemia, unspecified

      2016 2017 2018 2019 Billable/Specific Code
    Type 1 Excludes
    • leucine-induced E71.19
  • Isoleucinosis E71.19

ICD-10-CM Codes Adjacent To E71.19
E71.0 Maple-syrup-urine disease
E71.1 Other disorders of branched-chain amino-acid metabolism
E71.11 Branched-chain organic acidurias
E71.110 Isovaleric acidemia
E71.111 3-methylglutaconic aciduria
E71.118 Other branched-chain organic acidurias
E71.12 Disorders of propionate metabolism
E71.120 Methylmalonic acidemia
E71.121 Propionic acidemia
E71.128 Other disorders of propionate metabolism
E71.19 Other disorders of branched-chain amino-acid metabolism
E71.2 Disorder of branched-chain amino-acid metabolism, unspecified
E71.3 Disorders of fatty-acid metabolism
E71.30 Disorder of fatty-acid metabolism, unspecified
E71.31 Disorders of fatty-acid oxidation
E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency
E71.311 Medium chain acyl CoA dehydrogenase deficiency
E71.312 Short chain acyl CoA dehydrogenase deficiency
E71.313 Glutaric aciduria type II
E71.314 Muscle carnitine palmitoyltransferase deficiency
E71.318 Other disorders of fatty-acid oxidation

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.