ICD-10-CM Codes
E00-E89 Endocrine, nutritional and metabolic diseases
E70-E88 Metabolic disorders
E71- Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
2020 ICD-10-CM Diagnosis Code E71.4

2020 ICD-10-CM Diagnosis Code E71.4

Disorders of carnitine metabolism

2016

2017

2018

2019

2020

Non-Billable/Non-Specific Code

E71.4 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
The 2020 edition of ICD-10-CM E71.4 became effective on October 1, 2019.
This is the American ICD-10-CM version of E71.4 - other international versions of ICD-10 E71.4 may differ.

Type 1 Excludes

Type 1 Excludes Help

A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as E71.4. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

Muscle carnitine palmitoyltransferase deficiency (
ICD-10-CM Diagnosis Code E71.314
Muscle carnitine palmitoyltransferase deficiency
E71.314
)

The following code(s) above E71.4 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to E71.4:

E00-E89
2020 ICD-10-CM Range E00-E89
Endocrine, nutritional and metabolic diseases
Note
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Type 1 Excludes
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Endocrine, nutritional and metabolic diseases
E70-E88
2020 ICD-10-CM Range E70-E88
Metabolic disorders
Type 1 Excludes
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- Ehlers-Danlos syndrome (Q79.6-)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan's syndrome (Q87.4)
- 5-alpha-reductase deficiency (E29.1)
Metabolic disorders

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change

ICD-10-CM Codes Adjacent To E71.4

E71.30 Disorder of fatty-acid metabolism, unspecified

E71.31 Disorders of fatty-acid oxidation

E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency

E71.311 Medium chain acyl CoA dehydrogenase deficiency

E71.312 Short chain acyl CoA dehydrogenase deficiency

E71.313 Glutaric aciduria type II

E71.314 Muscle carnitine palmitoyltransferase deficiency

E71.318 Other disorders of fatty-acid oxidation

E71.32 Disorders of ketone metabolism

E71.39 Other disorders of fatty-acid metabolism

E71.4 Disorders of carnitine metabolism

E71.40 Disorder of carnitine metabolism, unspecified

E71.41 Primary carnitine deficiency

E71.42 Carnitine deficiency due to inborn errors of metabolism

E71.43 Iatrogenic carnitine deficiency

E71.44 Other secondary carnitine deficiency

E71.440 Ruvalcaba-Myhre-Smith syndrome

E71.448 Other secondary carnitine deficiency

E71.5 Peroxisomal disorders

E71.50 Peroxisomal disorder, unspecified

E71.51 Disorders of peroxisome biogenesis

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2020 ICD-10-CM Diagnosis Code E71.4

Disorders of carnitine metabolism

Muscle carnitine palmitoyltransferase deficiency

Endocrine, nutritional and metabolic diseases

Metabolic disorders