2019 ICD-10-CM Diagnosis Code E71.511

Neonatal adrenoleukodystrophy

    2016 2017 2018 2019 Billable/Specific Code
  • E71.511 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM E71.511 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of E71.511 - other international versions of ICD-10 E71.511 may differ.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as E71.511. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • X-linked adrenoleukodystrophy (
    ICD-10-CM Diagnosis Code E71.42

    Carnitine deficiency due to inborn errors of metabolism

      2016 2017 2018 2019 Billable/Specific Code
    Code Also
    • associated inborn error or metabolism
    E71.42-
    )
The following code(s) above E71.511 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to E71.511:
  • E00-E89
    2019 ICD-10-CM Range E00-E89

    Endocrine, nutritional and metabolic diseases

    Note
    • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
    Type 1 Excludes
    • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
    Endocrine, nutritional and metabolic diseases
  • E70-E88
    2019 ICD-10-CM Range E70-E88

    Metabolic disorders

    Type 1 Excludes
    • androgen insensitivity syndrome (E34.5-)
    • congenital adrenal hyperplasia (E25.0)
    • Ehlers-Danlos syndrome (Q79.6)
    • hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan's syndrome (Q87.4)
    • 5-alpha-reductase deficiency (E29.1)
    Metabolic disorders
  • E71.5
    ICD-10-CM Diagnosis Code E71.5

    Peroxisomal disorders

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • Schilder's disease (G37.0)
    Peroxisomal disorders
  • E71.51
    ICD-10-CM Diagnosis Code E71.51

    Disorders of peroxisome biogenesis

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Applicable To
    • Group 1 peroxisomal disorders
    Type 1 Excludes
    Disorders of peroxisome biogenesis
Approximate Synonyms
  • Neonatal adrenoleucodystrophy
Clinical Information
  • A rare metabolic disorder that affects neonates. It is characterized by damage of the white matter in the brain and degeneration of the adrenal glands. It manifests with hyperactivity, paralysis, muscular weakness, crossed eyes, hearing loss, seizures, and coma.
ICD-10-CM E71.511 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 642 Inborn and other disorders of metabolism

Convert E71.511 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change

Diagnosis Index entries containing back-references to E71.511:
  • Adrenoleukodystrophy E71.529
    ICD-10-CM Diagnosis Code E71.529

    X-linked adrenoleukodystrophy, unspecified type

      2016 2017 2018 2019 Billable/Specific Code
    • neonatal E71.511
  • Disorder (of) - see also Disease
    • peroxisomal E71.50
      ICD-10-CM Diagnosis Code E71.50

      Peroxisomal disorder, unspecified

        2016 2017 2018 2019 Billable/Specific Code

ICD-10-CM Codes Adjacent To E71.511
E71.41 Primary carnitine deficiency
E71.42 Carnitine deficiency due to inborn errors of metabolism
E71.43 Iatrogenic carnitine deficiency
E71.44 Other secondary carnitine deficiency
E71.440 Ruvalcaba-Myhre-Smith syndrome
E71.448 Other secondary carnitine deficiency
E71.5 Peroxisomal disorders
E71.50 Peroxisomal disorder, unspecified
E71.51 Disorders of peroxisome biogenesis
E71.510 Zellweger syndrome
E71.511 Neonatal adrenoleukodystrophy
E71.518 Other disorders of peroxisome biogenesis
E71.52 X-linked adrenoleukodystrophy
E71.520 Childhood cerebral X-linked adrenoleukodystrophy
E71.521 Adolescent X-linked adrenoleukodystrophy
E71.522 Adrenomyeloneuropathy
E71.528 Other X-linked adrenoleukodystrophy
E71.529 …… unspecified type
E71.53 Other group 2 peroxisomal disorders
E71.54 Other peroxisomal disorders
E71.540 Rhizomelic chondrodysplasia punctata

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.