1. ICD-10-CM Codes
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2. E00-E89
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3. E70-E88
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4. E74-
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5. 2023 ICD-10-CM Diagnosis Code E74.03

2023 ICD-10-CM Diagnosis Code E74.03

Cori disease

2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

• E74.03 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
• The 2023 edition of ICD-10-CM E74.03 became effective on October 1, 2022.
• This is the American ICD-10-CM version of E74.03 - other international versions of ICD-10 E74.03 may differ.

• Glycogen storage disease type iii
• Glycogen storage disease, type 3

• An autosomal recessive inherited type of glycogen storage disease caused by deficiency of the glycogen debranching enzyme. It results in the accumulation of structurally abnormal glycogen in the heart, skeletal muscles, and/or liver.
• An autosomal recessive metabolic disorder due to deficient expression of amylo-1,6-glucosidase (one part of the glycogen debranching enzyme system). The clinical course of the disease is similar to that of glycogen storage disease type i, but milder. Massive hepatomegaly, which is present in young children, diminishes and occasionally disappears with age. Levels of glycogen with short outer branches are elevated in muscle, liver, and erythrocytes. Six subgroups have been identified, with subgroups type iiia and type iiib being the most prevalent.
• Autosomal recessive metabolic disorder due to deficient expression of amylo-1,6-glucosidase; clinical course is similar to that of glycogen storage disease type i, but milder; massive hepatomegaly, which is present in young children, diminishes and occasionally disappears with age; levels of glycogen with short outer branches are elevated in muscle, liver, and erythrocytes.

• 642 Inborn and other disorders of metabolism

Convert E74.03 to ICD-9-CM

• 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
• 2017 (effective 10/1/2016): No change
• 2018 (effective 10/1/2017): No change
• 2019 (effective 10/1/2018): No change
• 2020 (effective 10/1/2019): No change
• 2021 (effective 10/1/2020): No change
• 2022 (effective 10/1/2021): No change
• 2023 (effective 10/1/2022): No change

• Amylopectinosis E74.03 (brancher enzyme deficiency)
• Cori's disease E74.03 (glycogen storage)
• Deficiency, deficient
  • brancher enzyme E74.03 (amylopectinosis)
  • debrancher enzyme E74.03 (limit dextrinosis)
• Dextrinosis, limit E74.03 (debrancher enzyme deficiency)
• Disease, diseased - see also Syndrome
  • glycogen storage E74.00
    ICD-10-CM Diagnosis Code E74.00

    Glycogen storage disease, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • Cori's E74.03
    • Forbes' E74.03
    • type III E74.03
  • Cori's E74.03 (glycogenosis III)
  • Forbes' E74.03 (glycogenosis III)
• Forbes' glycogen storage disease E74.03
• Infiltrate, infiltration
  • liver K76.89
    ICD-10-CM Diagnosis Code K76.89

    Other specified diseases of liver

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Cyst (simple) of liver
    • Focal nodular hyperplasia of liver
    • Hepatoptosis
    • glycogen E74.03 - see also Disease, glycogen storage

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.