2020 ICD-10-CM Diagnosis Code E74.09

Other glycogen storage disease

    2016 2017 2018 2019 2020 Billable/Specific Code
  • E74.09 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM E74.09 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of E74.09 - other international versions of ICD-10 E74.09 may differ.
Applicable To
  • Andersen disease
  • Hers disease
  • Tauri disease
  • Glycogen storage disease, types 0, IV, VI-XI
  • Liver phosphorylase deficiency
  • Muscle phosphofructokinase deficiency
The following code(s) above E74.09 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to E74.09:
  • E00-E89
    2020 ICD-10-CM Range E00-E89

    Endocrine, nutritional and metabolic diseases

    Note
    • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
    Type 1 Excludes
    • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
    Endocrine, nutritional and metabolic diseases
  • E70-E88
    2020 ICD-10-CM Range E70-E88

    Metabolic disorders

    Type 1 Excludes
    • androgen insensitivity syndrome (E34.5-)
    • congenital adrenal hyperplasia (E25.0)
    • Ehlers-Danlos syndrome (Q79.6-)
    • hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan's syndrome (Q87.4)
    • 5-alpha-reductase deficiency (E29.1)
    Metabolic disorders
  • E74
    ICD-10-CM Diagnosis Code E74

    Other disorders of carbohydrate metabolism

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Other disorders of carbohydrate metabolism
Approximate Synonyms
  • Glycogen storage disease type viii
  • Glycogen storage disease, type 4
  • Glycogen storage disease, type 6
  • Glycogen storage disease, type 7
  • Glycogen storage disease, type 8
  • Glycogen storage disease, type 9
  • Glycogen storage disease, type iv
  • Glycogen storage disease, type ix
  • Glycogen storage disease, type vi
  • Glycogen storage disease, type vii
Clinical Information
  • A hepatic glycogen storage disease in which there is an apparent deficiency of hepatic phosphorylase (glycogen phosphorylase, liver form) activity.
  • A rare inherited type of glycogen storage disease caused by deficiency of amylo-1,4-1,6 transglucosidase.
  • An autosomal recessive glycogen storage disease in which there is deficient expression of 6-phosphofructose 1-kinase in muscle (phosphofructokinase-1, muscle type) resulting in abnormal deposition of glycogen in muscle tissue. These patients have severe congenital muscular dystrophy and are exercise intolerant.
  • An autosomal recessive metabolic disorder due to a deficiency in expression of glycogen branching enzyme 1 (alpha-1,4-glucan-6-alpha-glucosyltransferase), resulting in an accumulation of abnormal glycogen with long outer branches. Clinical features are muscle hypotonia and cirrhosis. Death from liver disease usually occurs before age 2.
  • Autosomal recessive glycogen storage disease in which there is deficient expression of 6-phosphofructose 1-kinase in muscle resulting in abnormal deposition of glycogen in muscle tissue; patients have severe congenital muscular dystrophy and are exercise intolerant.
  • Autosomal recessive metabolic disorder due to a deficiency in expression of branching enzyme (alpha-1,4-glucan-6-alpha-glucosyltransferase), resulting in an accumulation of abnormal glycogen with long outer branches; clinical features are muscle hypotonia and cirrhosis; death from liver disease usually occurs before age 2.
  • Hepatic glycogen storage disease in which there is an apparent deficiency of hepatic phosphorylase activity.
ICD-10-CM E74.09 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 642 Inborn and other disorders of metabolism

Convert E74.09 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to E74.09:
  • Type 1 Excludes: E74.1
    ICD-10-CM Diagnosis Code E74.1

    Disorders of fructose metabolism

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • muscle phosphofructokinase deficiency (E74.09)

Diagnosis Index entries containing back-references to E74.09:
  • Andersen's disease E74.09 (glycogen storage)
  • Deficiency, deficient
    • muscle
      • phosphofructokinase E74.09
    • glycogen synthetase E74.09
    • hepatophosphorylase E74.09
    • liver phosphorylase E74.09
    • phosphorylase kinase, liver E74.09
  • Disease, diseased - see also Syndrome
    • glycogen storage E74.00
      ICD-10-CM Diagnosis Code E74.00

      Glycogen storage disease, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code
      • Andersen's E74.09
      • hepatorenal E74.09
      • Hers' E74.09
      • liver and kidney E74.09
      • muscle phosphofructokinase E74.09
      • Tauri's E74.09
      • type 0 E74.09
      • type IV E74.09
      • type VI-XI E74.09
    • liver (chronic) (organic) K76.9
      ICD-10-CM Diagnosis Code K76.9

      Liver disease, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code
      • glycogen storage E74.09
    • Andersen's E74.09 (glycogenosis IV)
    • Hers' E74.09 (glycogenosis VI)
    • Tauri's E74.09
  • Disorder (of) - see also Disease
    • metabolism NOS E88.9
      ICD-10-CM Diagnosis Code E88.9

      Metabolic disorder, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code
      • glycogen storage E74.09 (hepatorenal)
  • Hers' disease E74.09
  • Pyelonephritis - see also Nephritis, tubulo-interstitial
    • in (due to)
      • glycogen storage disease E74.09
  • Tauri's disease E74.09

ICD-10-CM Codes Adjacent To E74.09
E73.1 Secondary lactase deficiency
E73.8 Other lactose intolerance
E73.9 Lactose intolerance, unspecified
E74 Other disorders of carbohydrate metabolism
E74.0 Glycogen storage disease
E74.00 …… unspecified
E74.01 von Gierke disease
E74.02 Pompe disease
E74.03 Cori disease
E74.04 McArdle disease
E74.09 Other glycogen storage disease
E74.1 Disorders of fructose metabolism
E74.10 Disorder of fructose metabolism, unspecified
E74.11 Essential fructosuria
E74.12 Hereditary fructose intolerance
E74.19 Other disorders of fructose metabolism
E74.2 Disorders of galactose metabolism
E74.20 …… unspecified
E74.21 Galactosemia
E74.29 Other disorders of galactose metabolism
E74.3 Other disorders of intestinal carbohydrate absorption

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.