2022 ICD-10-CM Diagnosis Code E75.244

Niemann-Pick disease type A/B

    2022 - New Code Billable/Specific Code
  • E75.244 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • ICD-10-CM E75.244 is a new 2022 ICD-10-CM code that became effective on October 1, 2021.
  • This is the American ICD-10-CM version of E75.244 - other international versions of ICD-10 E75.244 may differ.
Applicable To
  • Acid sphingomyelinase deficiency type A/B (ASMD type A/B)
  • Chronic neurovisceral acid sphingomyelinase deficiency
The following code(s) above E75.244 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to E75.244:
  • E00-E89
    2022 ICD-10-CM Range E00-E89

    Endocrine, nutritional and metabolic diseases

    Note
    • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
    Type 1 Excludes
    • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
    Endocrine, nutritional and metabolic diseases
  • E70-E88
    2022 ICD-10-CM Range E70-E88

    Metabolic disorders

    Type 1 Excludes
    • androgen insensitivity syndrome (E34.5-)
    • congenital adrenal hyperplasia (E25.0)
    • hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan's syndrome (Q87.4)
    • 5-alpha-reductase deficiency (E29.1)
    Type 2 Excludes
    • Ehlers-Danlos syndromes (Q79.6-)
    Metabolic disorders
  • E75
    ICD-10-CM Diagnosis Code E75

    Disorders of sphingolipid metabolism and other lipid storage disorders

      2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Disorders of sphingolipid metabolism and other lipid storage disorders
  • E75.2
    ICD-10-CM Diagnosis Code E75.2

    Other sphingolipidosis

      2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • adrenoleukodystrophy [Addison-Schilder] (E71.528)
    Other sphingolipidosis
  • E75.24
    ICD-10-CM Diagnosis Code E75.24

    Niemann-Pick disease

      2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
    Applicable To
    • Acid sphingomyelinase deficiency (ASMD)
    Niemann-Pick disease
ICD-10-CM E75.244 is grouped within Diagnostic Related Group(s) (MS-DRG v39.0):
  • 642 Inborn and other disorders of metabolism
Code History
  • 2022 (effective 10/1/2021): New code

Diagnosis Index entries containing back-references to E75.244:
  • Deficiency, deficient
    • acid sphingomyelinase (ASMD) E75.249
      ICD-10-CM Diagnosis Code E75.249

      Niemann-Pick disease, unspecified

        2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
      Applicable To
      • Acid sphingomyelinase deficiency (ASMD) NOS
    • chronic neurovisceral acid sphingomyelinase E75.244
  • Niemann-Pick disease or syndrome E75.249
    ICD-10-CM Diagnosis Code E75.249

    Niemann-Pick disease, unspecified

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
    Applicable To
    • Acid sphingomyelinase deficiency (ASMD) NOS

ICD-10-CM Codes Adjacent To E75.244
E75.19 Other gangliosidosis
E75.2 Other sphingolipidosis
E75.21 Fabry (-Anderson) disease
E75.22 Gaucher disease
E75.23 Krabbe disease
E75.24 Niemann-Pick disease
E75.240 …… type A
E75.241 …… type B
E75.242 …… type C
E75.243 …… type D
E75.244 …… type A/B
E75.248 Other Niemann-Pick disease
E75.249 …… unspecified
E75.25 Metachromatic leukodystrophy
E75.26 Sulfatase deficiency
E75.29 Other sphingolipidosis
E75.3 Sphingolipidosis, unspecified
E75.4 Neuronal ceroid lipofuscinosis
E75.5 Other lipid storage disorders
E75.6 Lipid storage disorder, unspecified
E76 Disorders of glycosaminoglycan metabolism

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.