ICD-10-CM Codes
E00-E89 Endocrine, nutritional and metabolic diseases
E70-E88 Metabolic disorders
E75- Disorders of sphingolipid metabolism and other lipid storage disorders

2018/2019 ICD-10-CM Diagnosis Code E75.26

Sulfatase deficiency

2019 - New Code

Billable/Specific Code

E75.26 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
ICD-10-CM E75.26 is a new 2019 ICD-10-CM code that became effective on October 1, 2018.
This is the American ICD-10-CM version of E75.26 - other international versions of ICD-10 E75.26 may differ.

Applicable To

Multiple sulfatase deficiency (MSD)

The following code(s) above E75.26 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to E75.26:

E00-E89
2019 ICD-10-CM Range E00-E89
Endocrine, nutritional and metabolic diseases
Note
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Type 1 Excludes
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Endocrine, nutritional and metabolic diseases
E70-E88
2019 ICD-10-CM Range E70-E88
Metabolic disorders
Type 1 Excludes
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- Ehlers-Danlos syndrome (Q79.6)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan's syndrome (Q87.4)
- 5-alpha-reductase deficiency (E29.1)
Metabolic disorders
E75
ICD-10-CM Diagnosis Code E75
Disorders of sphingolipid metabolism and other lipid storage disorders
Type 1 Excludes
- mucolipidosis, types I-III (E77.0-E77.1)
- Refsum's disease (G60.1)
Disorders of sphingolipid metabolism and other lipid storage disorders
E75.2
ICD-10-CM Diagnosis Code E75.2
Other sphingolipidosis
Type 1 Excludes
- adrenoleukodystrophy [Addison-Schilder] (E71.528)
Other sphingolipidosis

ICD-10-CM E75.26 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):

056 Degenerative nervous system disorders with mcc
057 Degenerative nervous system disorders without mcc

Code History

2019 (effective 10/1/2018): New code

Diagnosis Index entries containing back-references to E75.26:

Deficiency, deficient
- multiple sulfatase E75.26 (MSD)
- sulfatase E75.26
MSD E75.26 (multiple sulfatase deficiency)

ICD-10-CM Codes Adjacent To E75.26

E75.22 Gaucher disease

E75.23 Krabbe disease

E75.24 Niemann-Pick disease

E75.240 …… type A

E75.241 …… type B

E75.242 …… type C

E75.243 …… type D

E75.248 Other Niemann-Pick disease

E75.249 …… unspecified

E75.25 Metachromatic leukodystrophy

E75.26 Sulfatase deficiency

E75.29 Other sphingolipidosis

E75.3 Sphingolipidosis, unspecified

E75.4 Neuronal ceroid lipofuscinosis

E75.5 Other lipid storage disorders

E75.6 Lipid storage disorder, unspecified

E76 Disorders of glycosaminoglycan metabolism

E76.0 Mucopolysaccharidosis, type I

E76.01 Hurler's syndrome

E76.02 Hurler-Scheie syndrome

E76.03 Scheie's syndrome

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.