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ICD-10-CM Codes
›
E00-E89
Endocrine, nutritional and metabolic diseases
›
E70-E88
Metabolic disorders
›
Disorders of glycosaminoglycan metabolism E76
Disorders of glycosaminoglycan metabolism
E76-
Codes
E76
Disorders of glycosaminoglycan metabolism
E76.0
Mucopolysaccharidosis, type I
E76.01
Hurler's syndrome
E76.02
Hurler-Scheie syndrome
E76.03
Scheie's syndrome
E76.1
Mucopolysaccharidosis, type II
E76.2
Other mucopolysaccharidoses
E76.21
Morquio mucopolysaccharidoses
E76.210
Morquio A mucopolysaccharidoses
E76.211
Morquio B mucopolysaccharidoses
E76.219
…… unspecified
E76.22
Sanfilippo mucopolysaccharidoses
E76.29
Other mucopolysaccharidoses
E76.3
Mucopolysaccharidosis, unspecified
E76.8
Other disorders of glucosaminoglycan metabolism
E76.9
Glucosaminoglycan metabolism disorder, unspecified