-
ICD-10-CM Codes
›
-
E00-E89
Endocrine, nutritional and metabolic diseases
›
-
E70-E88
Metabolic disorders
›
-
E76-
Disorders of glycosaminoglycan metabolism
›
-
2022 ICD-10-CM Diagnosis Code E76.01
2022 ICD-10-CM Diagnosis Code E76.01
Hurler's syndrome
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
- E76.01 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
- The 2022 edition of ICD-10-CM E76.01 became effective on October 1, 2021.
- This is the American ICD-10-CM version of E76.01 - other international versions of ICD-10 E76.01 may differ.
The following code(s) above
E76.01 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
- Applicable To annotations, or
- Code Also annotations, or
- Code First annotations, or
- Excludes1 annotations, or
- Excludes2 annotations, or
- Includes annotations, or
- Note annotations, or
- Use Additional annotations
that may be applicable to
E76.01:
Approximate Synonyms
- Mucopolysaccharidosis, mps-i-h
Clinical Information
- An autosomal recessive inherited disorder of mucopolysaccharide metabolism. It is the most severe form of mucopolysaccharidosis type i. It is characterized by deficiency of the enzyme alpha-l-iduronidase resulting in the accumulation of mucopolysaccharides in the tissues.
ICD-10-CM E76.01 is grouped within Diagnostic Related Group(s) (MS-DRG v39.0):
- 642 Inborn and other disorders of metabolism
Convert E76.01 to ICD-9-CM
Code History
- 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
- 2017 (effective 10/1/2016): No change
- 2018 (effective 10/1/2017): No change
- 2019 (effective 10/1/2018): No change
- 2020 (effective 10/1/2019): No change
- 2021 (effective 10/1/2020): No change
- 2022 (effective 10/1/2021): No change
- Dysostosis
- Gargoylism E76.01
- Lipochondrodystrophy E76.01
- Mucopolysaccharidosis E76.3
ICD-10-CM Diagnosis Code E76.3
Mucopolysaccharidosis, unspecified
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
- type
- Hurler's syndrome E76.01
ICD-10-CM Codes Adjacent To E76.01
E75.25 Metachromatic leukodystrophy
E75.3 Sphingolipidosis, unspecified
E75.4 Neuronal ceroid lipofuscinosis
E75.5 Other lipid storage disorders
E75.6 Lipid storage disorder, unspecified
E76 Disorders of glycosaminoglycan metabolism
E76.0 Mucopolysaccharidosis, type I
E76.01
Hurler's syndrome
E76.1 Mucopolysaccharidosis, type II
E76.2 Other mucopolysaccharidoses
E76.21 Morquio mucopolysaccharidoses
E76.210 Morquio A mucopolysaccharidoses
E76.211 Morquio B mucopolysaccharidoses
E76.22 Sanfilippo mucopolysaccharidoses
E76.29 Other mucopolysaccharidoses
Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.