2021

  1. ICD-10-CM Codes
    2. ›
  2. E00-E89 Endocrine, nutritional and metabolic diseases
    3. ›
  3. E70-E88 Metabolic disorders
    4. ›
  4. E76- Disorders of glycosaminoglycan metabolism
    5. ›
  5. 2021 ICD-10-CM Diagnosis Code E76.211

2021 ICD-10-CM Diagnosis Code E76.211

Morquio B mucopolysaccharidoses

    2016 2017 2018 2019 2020 2021 Billable/Specific Code
  • E76.211 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2021 edition of ICD-10-CM E76.211 became effective on October 1, 2020.
  • This is the American ICD-10-CM version of E76.211 - other international versions of ICD-10 E76.211 may differ.
Applicable To
  • Morquio-like mucopolysaccharidoses
  • Morquio-like syndrome
  • Morquio syndrome B
  • Mucopolysaccharidosis, type IVB
The following code(s) above E76.211 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to E76.211:
  • E00-E89
    2021 ICD-10-CM Range E00-E89

    Endocrine, nutritional and metabolic diseases

    Note
    • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
    Type 1 Excludes
    • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
    Endocrine, nutritional and metabolic diseases
  • E70-E88
    2021 ICD-10-CM Range E70-E88

    Metabolic disorders

    Type 1 Excludes
    • androgen insensitivity syndrome (E34.5-)
    • congenital adrenal hyperplasia (E25.0)
    • Ehlers-Danlos syndromes (Q79.6-)
    • hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan's syndrome (Q87.4)
    • 5-alpha-reductase deficiency (E29.1)
    Metabolic disorders
Approximate Synonyms
  • Mucopolysaccharidosis mps-iv-b
Clinical Information
  • A rare autosomal recessive lysosomal storage disease caused by deficiency of the enzyme beta galactosidase. It is characterized by skeletal dysplasia and short stature.
ICD-10-CM E76.211 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):
  • 642 Inborn and other disorders of metabolism

Convert E76.211 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change

Diagnosis Index entries containing back-references to E76.211:
  • Mucopolysaccharidosis E76.3
    ICD-10-CM Diagnosis Code E76.3

    Mucopolysaccharidosis, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    • Morquio syndrome E76.219
      ICD-10-CM Diagnosis Code E76.219

      Morquio mucopolysaccharidoses, unspecified

        2016 2017 2018 2019 2020 2021 Billable/Specific Code
      Applicable To
      • Morquio syndrome
      • Mucopolysaccharidosis, type IV
      • B E76.211
    • type
      • IVB E76.211

ICD-10-CM Codes Adjacent To E76.211
E75.6 Lipid storage disorder, unspecified
E76 Disorders of glycosaminoglycan metabolism
E76.0 Mucopolysaccharidosis, type I
E76.01 Hurler's syndrome
E76.02 Hurler-Scheie syndrome
E76.03 Scheie's syndrome
E76.1 Mucopolysaccharidosis, type II
E76.2 Other mucopolysaccharidoses
E76.21 Morquio mucopolysaccharidoses
E76.210 Morquio A mucopolysaccharidoses
E76.211 Morquio B mucopolysaccharidoses
E76.219 …… unspecified
E76.22 Sanfilippo mucopolysaccharidoses
E76.29 Other mucopolysaccharidoses
E76.3 Mucopolysaccharidosis, unspecified
E76.8 Other disorders of glucosaminoglycan metabolism
E76.9 Glucosaminoglycan metabolism disorder, unspecified
E77 Disorders of glycoprotein metabolism
E77.0 Defects in post-translational modification of lysosomal enzymes
E77.1 Defects in glycoprotein degradation
E77.8 Other disorders of glycoprotein metabolism

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

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