-
ICD-10-CM Codes
›
-
E00-E89
Endocrine, nutritional and metabolic diseases
›
-
E70-E88
Metabolic disorders
›
-
E76-
Disorders of glycosaminoglycan metabolism
›
-
2021 ICD-10-CM Diagnosis Code E76.211
2021 ICD-10-CM Diagnosis Code E76.211
Morquio B mucopolysaccharidoses
2016 2017 2018 2019 2020 2021 Billable/Specific Code
- E76.211 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
- The 2021 edition of ICD-10-CM E76.211 became effective on October 1, 2020.
- This is the American ICD-10-CM version of E76.211 - other international versions of ICD-10 E76.211 may differ.
Applicable To- Morquio-like mucopolysaccharidoses
- Morquio-like syndrome
- Morquio syndrome B
- Mucopolysaccharidosis, type IVB
The following code(s) above
E76.211 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
- Applicable To annotations, or
- Code Also annotations, or
- Code First annotations, or
- Excludes1 annotations, or
- Excludes2 annotations, or
- Includes annotations, or
- Note annotations, or
- Use Additional annotations
that may be applicable to
E76.211:
Approximate Synonyms
- Mucopolysaccharidosis mps-iv-b
Clinical Information
- A rare autosomal recessive lysosomal storage disease caused by deficiency of the enzyme beta galactosidase. It is characterized by skeletal dysplasia and short stature.
ICD-10-CM E76.211 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):
- 642 Inborn and other disorders of metabolism
Convert E76.211 to ICD-9-CM
Code History
- 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
- 2017 (effective 10/1/2016): No change
- 2018 (effective 10/1/2017): No change
- 2019 (effective 10/1/2018): No change
- 2020 (effective 10/1/2019): No change
- 2021 (effective 10/1/2020): No change
- Mucopolysaccharidosis E76.3
ICD-10-CM Diagnosis Code E76.3
Mucopolysaccharidosis, unspecified
2016 2017 2018 2019 2020 2021 Billable/Specific Code
- Morquio syndrome E76.219
ICD-10-CM Diagnosis Code E76.219
Morquio mucopolysaccharidoses, unspecified
2016 2017 2018 2019 2020 2021 Billable/Specific Code
Applicable To- Morquio syndrome
- Mucopolysaccharidosis, type IV
- type
ICD-10-CM Codes Adjacent To E76.211
E75.6 Lipid storage disorder, unspecified
E76 Disorders of glycosaminoglycan metabolism
E76.0 Mucopolysaccharidosis, type I
E76.1 Mucopolysaccharidosis, type II
E76.2 Other mucopolysaccharidoses
E76.21 Morquio mucopolysaccharidoses
E76.210 Morquio A mucopolysaccharidoses
E76.211
Morquio B mucopolysaccharidoses
E76.22 Sanfilippo mucopolysaccharidoses
E76.29 Other mucopolysaccharidoses
E76.3 Mucopolysaccharidosis, unspecified
E76.8 Other disorders of glucosaminoglycan metabolism
E76.9 Glucosaminoglycan metabolism disorder, unspecified
E77 Disorders of glycoprotein metabolism
E77.0 Defects in post-translational modification of lysosomal enzymes
E77.1 Defects in glycoprotein degradation
E77.8 Other disorders of glycoprotein metabolism
Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.