ICD-10-CM Codes
E00-E89 Endocrine, nutritional and metabolic diseases
E70-E88 Metabolic disorders
E76- Disorders of glycosaminoglycan metabolism

2018/2019 ICD-10-CM Diagnosis Code E76.211

Morquio B mucopolysaccharidoses

2016

2017

2018

2019

Billable/Specific Code

E76.211 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2018/2019 edition of ICD-10-CM E76.211 became effective on October 1, 2018.
This is the American ICD-10-CM version of E76.211 - other international versions of ICD-10 E76.211 may differ.

Applicable To

Morquio-like mucopolysaccharidoses
Morquio-like syndrome
Morquio syndrome B
Mucopolysaccharidosis, type IVB

The following code(s) above E76.211 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to E76.211:

E00-E89
2019 ICD-10-CM Range E00-E89
Endocrine, nutritional and metabolic diseases
Note
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Type 1 Excludes
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Endocrine, nutritional and metabolic diseases
E70-E88
2019 ICD-10-CM Range E70-E88
Metabolic disorders
Type 1 Excludes
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- Ehlers-Danlos syndrome (Q79.6)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan's syndrome (Q87.4)
- 5-alpha-reductase deficiency (E29.1)
Metabolic disorders

Approximate Synonyms

Mucopolysaccharidosis mps-iv-b

Clinical Information

A rare autosomal recessive lysosomal storage disease caused by deficiency of the enzyme beta galactosidase. It is characterized by skeletal dysplasia and short stature.

ICD-10-CM E76.211 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):

642 Inborn and other disorders of metabolism

Convert E76.211 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change

Diagnosis Index entries containing back-references to E76.211:

Mucopolysaccharidosis E76.3
ICD-10-CM Diagnosis Code E76.3
Mucopolysaccharidosis, unspecified
- Morquio syndrome E76.219
  ICD-10-CM Diagnosis Code E76.219
  Morquio mucopolysaccharidoses, unspecified
  2016 2017 2018 2019 Billable/Specific Code
  Applicable To
  Morquio syndrome
  Mucopolysaccharidosis, type IV
  - B E76.211
- type
  - IVB E76.211

ICD-10-CM Codes Adjacent To E76.211

E75.6 Lipid storage disorder, unspecified

E76 Disorders of glycosaminoglycan metabolism

E76.0 Mucopolysaccharidosis, type I

E76.01 Hurler's syndrome

E76.02 Hurler-Scheie syndrome

E76.03 Scheie's syndrome

E76.1 Mucopolysaccharidosis, type II

E76.2 Other mucopolysaccharidoses

E76.21 Morquio mucopolysaccharidoses

E76.210 Morquio A mucopolysaccharidoses

E76.211 Morquio B mucopolysaccharidoses

E76.219 …… unspecified

E76.22 Sanfilippo mucopolysaccharidoses

E76.29 Other mucopolysaccharidoses

E76.3 Mucopolysaccharidosis, unspecified

E76.8 Other disorders of glucosaminoglycan metabolism

E76.9 Glucosaminoglycan metabolism disorder, unspecified

E77 Disorders of glycoprotein metabolism

E77.0 Defects in post-translational modification of lysosomal enzymes

E77.1 Defects in glycoprotein degradation

E77.8 Other disorders of glycoprotein metabolism

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2018/2019 ICD-10-CM Diagnosis Code E76.211

Morquio B mucopolysaccharidoses

Endocrine, nutritional and metabolic diseases

Metabolic disorders

Mucopolysaccharidosis, unspecified

Morquio mucopolysaccharidoses, unspecified