ICD-10-CM Codes
E00-E89
E70-E88
Disorders of lipoprotein metabolism and other lipidemias E78

Disorders of lipoprotein metabolism and other lipidemias E78-

Type 1 Excludes

Type 1 Excludes Help

A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as E78. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

sphingolipidosis (
ICD-10-CM Diagnosis Code E75.0
GM2 gangliosidosis
E75.0-
ICD-10-CM Diagnosis Code E75.3
Sphingolipidosis, unspecified
E75.3
)

Codes

E78 Disorders of lipoprotein metabolism and other lipidemias
- E78.0 Pure hypercholesterolemia
  - E78.00 …… unspecified
  - E78.01 Familial hypercholesterolemia
- E78.1 Pure hyperglyceridemia
- E78.2 Mixed hyperlipidemia
- E78.3 Hyperchylomicronemia
- E78.4 Other hyperlipidemia
  - E78.41 Elevated Lipoprotein(a)
  - E78.49 Other hyperlipidemia
- E78.5 Hyperlipidemia, unspecified
- E78.6 Lipoprotein deficiency
- E78.7 Disorders of bile acid and cholesterol metabolism
  - E78.70 Disorder of bile acid and cholesterol metabolism, unspecified
  - E78.71 Barth syndrome
  - E78.72 Smith-Lemli-Opitz syndrome
  - E78.79 Other disorders of bile acid and cholesterol metabolism
- E78.8 Other disorders of lipoprotein metabolism
  - E78.81 Lipoid dermatoarthritis
  - E78.89 Other lipoprotein metabolism disorders
- E78.9 Disorder of lipoprotein metabolism, unspecified

Disorders of lipoprotein metabolism and other lipidemias E78-

GM2 gangliosidosis

Sphingolipidosis, unspecified