2020 ICD-10-CM Diagnosis Code E80.5

Crigler-Najjar syndrome

    2016 2017 2018 2019 2020 Billable/Specific Code
  • E80.5 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM E80.5 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of E80.5 - other international versions of ICD-10 E80.5 may differ.
The following code(s) above E80.5 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to E80.5:
  • E00-E89
    2020 ICD-10-CM Range E00-E89

    Endocrine, nutritional and metabolic diseases

    Note
    • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
    Type 1 Excludes
    • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
    Endocrine, nutritional and metabolic diseases
  • E70-E88
    2020 ICD-10-CM Range E70-E88

    Metabolic disorders

    Type 1 Excludes
    • androgen insensitivity syndrome (E34.5-)
    • congenital adrenal hyperplasia (E25.0)
    • Ehlers-Danlos syndrome (Q79.6-)
    • hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan's syndrome (Q87.4)
    • 5-alpha-reductase deficiency (E29.1)
    Metabolic disorders
  • E80
    ICD-10-CM Diagnosis Code E80

    Disorders of porphyrin and bilirubin metabolism

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Includes
    • defects of catalase and peroxidase
    Disorders of porphyrin and bilirubin metabolism
Approximate Synonyms
  • Crigler najjar syndrome
Clinical Information
  • A familial form of congenital hyperbilirubinemia transmitted as an autosomal recessive trait. It is characterized by icterus and brain damage caused by a glucuronyl transferase deficiency in the liver and faulty bilirubin conjugation.
  • A rare autosomal recessive inherited syndrome characterized by abnormalities in the metabolism of bilirubin. It results in the development of jaundice. It may cause brain damage in infancy.
ICD-10-CM E80.5 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 441 Disorders of liver except malignancy, cirrhosis or alcoholic hepatitis with mcc
  • 442 Disorders of liver except malignancy, cirrhosis or alcoholic hepatitis with cc
  • 443 Disorders of liver except malignancy, cirrhosis or alcoholic hepatitis without cc/mcc

Convert E80.5 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to E80.5:
  • Type 1 Excludes: P57.8
    ICD-10-CM Diagnosis Code P57.8

    Other specified kernicterus

      2016 2017 2018 2019 2020 Billable/Specific Code Code on Newborn Record
    Type 1 Excludes
    • Crigler-Najjar syndrome (E80.5)

Diagnosis Index entries containing back-references to E80.5:
  • Crigler-Najjar disease or syndrome E80.5
  • Deficiency, deficient
    • glucuronyl transferase E80.5
  • Jaundice (yellow) R17
    ICD-10-CM Diagnosis Code R17

    Unspecified jaundice

      2016 2017 2018 2019 2020 Billable/Specific Code
    Type 1 Excludes
    • familial nonhemolytic (congenital) (Gilbert) E80.4
      ICD-10-CM Diagnosis Code E80.4

      Gilbert syndrome

        2016 2017 2018 2019 2020 Billable/Specific Code
      • Crigler-Najjar E80.5
    • newborn P59.9
      ICD-10-CM Diagnosis Code P59.9

      Neonatal jaundice, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code Code on Newborn Record
      Applicable To
      • Neonatal physiological jaundice (intense)(prolonged) NOS

ICD-10-CM Codes Adjacent To E80.5
E79.9 Disorder of purine and pyrimidine metabolism, unspecified
E80 Disorders of porphyrin and bilirubin metabolism
E80.0 Hereditary erythropoietic porphyria
E80.1 Porphyria cutanea tarda
E80.2 Other and unspecified porphyria
E80.20 Unspecified porphyria
E80.21 Acute intermittent (hepatic) porphyria
E80.29 Other porphyria
E80.3 Defects of catalase and peroxidase
E80.4 Gilbert syndrome
E80.5 Crigler-Najjar syndrome
E80.6 Other disorders of bilirubin metabolism
E80.7 Disorder of bilirubin metabolism, unspecified
E83 Disorders of mineral metabolism
E83.0 Disorders of copper metabolism
E83.00 Disorder of copper metabolism, unspecified
E83.01 Wilson's disease
E83.09 Other disorders of copper metabolism
E83.1 Disorders of iron metabolism
E83.10 Disorder of iron metabolism, unspecified
E83.11 Hemochromatosis

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.