1. ICD-10-CM Codes
›
2. E00-E89
›
3. E70-E88
›
4. E83-
›
5. 2023 ICD-10-CM Diagnosis Code E83.01

2023 ICD-10-CM Diagnosis Code E83.01

Wilson's disease

2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

• E83.01 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
• The 2023 edition of ICD-10-CM E83.01 became effective on October 1, 2022.
• This is the American ICD-10-CM version of E83.01 - other international versions of ICD-10 E83.01 may differ.

• Bilateral kayser-fleischer rings
• Kayser-fleischer ring, both eyes
• Left kayser-fleischer ring
• Left kayser-fleischer ring (eye condition)
• Right kayser-fleischer ring
• Wilsons disease

• A rare autosomal recessive disease characterized by the deposition of copper in the brain; liver; cornea; and other organs. It is caused by defects in the atp7b gene encoding copper-transporting atpase 2 (ec 3.6.3.4), also known as the wilson disease protein. The overload of copper inevitably leads to progressive liver and neurological dysfunction such as liver cirrhosis; tremor; ataxia and intellectual deterioration. Hepatic dysfunction may precede neurologic dysfunction by several years.
• A rare autosomal recessive inherited disorder caused by mutations in the atp7b gene. It is characterized by copper accumulation in the tissues, particularly brain and liver. It results in liver failure, neurologic, and psychotic manifestations.
• Rare autosomal recessive disease characterized by the deposition of copper in the brain, liver, cornea and other organs; clinical features include liver cirrhosis, liver failure, splenomegaly, tremor, bradykinesia, dysarthria, chorea, muscle rigidity, kayser-fleischer rings (pigmented corneal lesions), ataxia and intellectual deterioration; hepatic dysfunction may precede neurologic dysfunction by several years.
• Wilson disease is a rare inherited disorder that prevents your body from getting rid of extra copper. You need a small amount of copper from food to stay healthy. Too much copper is poisonous.normally, your liver releases extra copper into bile, a digestive fluid. With wilson disease, the copper builds up in your liver, and it releases the copper directly into your bloodstream. This can cause damage to your brain, kidneys, and eyes.wilson disease is present at birth, but symptoms usually start between ages 5 and 35. It first attacks the liver, the central nervous system or both. The most characteristic sign is a rusty brown ring around the cornea of the eye. A physical exam and laboratory tests can diagnose it.treatment is with drugs to remove the extra copper from your body. You need to take medicine and follow a low-copper diet for the rest of your life. Don't eat shellfish or liver, as these foods may contain high levels of copper. At the beginning of treatment, you'll also need to avoid chocolate, mushrooms, and nuts. Have your drinking water checked for copper content and don't take multivitamins that contain copper.with early detection and proper treatment, you can enjoy good health.

• 642 Inborn and other disorders of metabolism

Convert E83.01 to ICD-9-CM

• 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
• 2017 (effective 10/1/2016): No change
• 2018 (effective 10/1/2017): No change
• 2019 (effective 10/1/2018): No change
• 2020 (effective 10/1/2019): No change
• 2021 (effective 10/1/2020): No change
• 2022 (effective 10/1/2021): No change
• 2023 (effective 10/1/2022): No change

• Code Also: H18.04
  ICD-10-CM Diagnosis Code H18.04

  Kayser-Fleischer ring

  2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code

  Code Also

  • associated Wilson's disease (E83.01)

• Cirrhosis, cirrhotic (hepatic) (liver) K74.60
  ICD-10-CM Diagnosis Code K74.60

  Unspecified cirrhosis of liver

  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

  Applicable To

  • Cirrhosis (of liver) NOS
  • due to
    • hepatolenticular degeneration E83.01
    • Wilson's disease E83.01
• Deficiency, deficient
  • ceruloplasmin E83.01 (Wilson)
• Degeneration, degenerative
  • hepatolenticular E83.01 (Wilson's)
  • lenticular E83.01 (familial) (progressive) (Wilson's) (with cirrhosis of liver)
  • Wilson's hepatolenticular E83.01
• Dementia (degenerative (primary)) (old age) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety) F03.90
  ICD-10-CM Diagnosis Code F03.90

  Unspecified dementia, unspecified severity, without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety

  2016 2017 2018 2019 2020 2021 2022 2023 - Revised Code Billable/Specific Code Adult Dx (15-124 years)

  Applicable To

  • Dementia NOS
  • in (due to)
    • hepatolenticular degeneration E83.01 - see also Dementia, in, diseases specified elsewhere
      • with behavioral disturbance E83.01 - see also Dementia, in, diseases specified elsewhere
• Disease, diseased - see also Syndrome
  • hepatolenticular E83.01
  • Kinnier Wilson's E83.01 (hepatolenticular degeneration)
  • Wilson's E83.01 (hepatolenticular degeneration)
• Disorder (of) - see also Disease
  • metabolism NOS E88.9
    ICD-10-CM Diagnosis Code E88.9

    Metabolic disorder, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • copper E83.00
      ICD-10-CM Diagnosis Code E83.00

      Disorder of copper metabolism, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      • Wilson's disease E83.01
  • tubulo-interstitial (in)
    • Wilson's disease E83.01
• Hepatolenticular degeneration E83.01
• Kinnier Wilson's disease E83.01 (hepatolenticular degeneration)
• Lenticular degeneration, progressive E83.01
• Pseudosclerosis (brain)
  • of Westphal E83.01 (Strümpell)
• Pyelonephritis - see also Nephritis, tubulo-interstitial
  • in (due to)
    • Wilson's disease E83.01
• Strümpell-Westphal pseudosclerosis E83.01
• Syndrome - see also Disease
  • amyostatic E83.01 (Wilson's disease)
  • lenticular, progressive E83.01
  • Westphal-Strümpell E83.01
  • Wilson's E83.01 (hepatolenticular degeneration)
• Westphal-Strümpell syndrome E83.01
• Wilson's
  • disease or syndrome E83.01
  • hepatolenticular degeneration E83.01

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.