2020 ICD-10-CM Diagnosis Code E83.110

Hereditary hemochromatosis

    2016 2017 2018 2019 2020 Billable/Specific Code
  • E83.110 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM E83.110 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of E83.110 - other international versions of ICD-10 E83.110 may differ.
Applicable To
  • Bronzed diabetes
  • Pigmentary cirrhosis (of liver)
  • Primary (hereditary) hemochromatosis
The following code(s) above E83.110 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to E83.110:
  • E00-E89
    2020 ICD-10-CM Range E00-E89

    Endocrine, nutritional and metabolic diseases

    Note
    • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
    Type 1 Excludes
    • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
    Endocrine, nutritional and metabolic diseases
  • E70-E88
    2020 ICD-10-CM Range E70-E88

    Metabolic disorders

    Type 1 Excludes
    • androgen insensitivity syndrome (E34.5-)
    • congenital adrenal hyperplasia (E25.0)
    • Ehlers-Danlos syndrome (Q79.6-)
    • hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan's syndrome (Q87.4)
    • 5-alpha-reductase deficiency (E29.1)
    Metabolic disorders
  • E83
    ICD-10-CM Diagnosis Code E83

    Disorders of mineral metabolism

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • dietary mineral deficiency (E58-E61)
    • parathyroid disorders (E20-E21)
    • vitamin D deficiency (E55.-)
    Disorders of mineral metabolism
  • E83.1
    ICD-10-CM Diagnosis Code E83.1

    Disorders of iron metabolism

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Disorders of iron metabolism
  • E83.11
    ICD-10-CM Diagnosis Code E83.11

    Hemochromatosis

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • GALD (P78.84)
    • Gestational alloimmune liver disease (P78.84)
    • Neonatal hemochromatosis (P78.84)
    Hemochromatosis
Approximate Synonyms
  • Hemochromatosis, hereditary
Clinical Information
  • A condition in which the body takes up and stores more iron than it needs. The extra iron is stored in the liver, heart, and pancreas, which may cause liver disease, heart problems, organ failure, and cancer. It may also cause bronze skin, diabetes, pain in the joints and abdomen, tiredness, and impotence. Hemochromatosis may be inherited, or it may be caused by blood transfusions.
  • A disorder due to the deposition of hemosiderin in the parenchymal cells, causing tissue damage and dysfunction of the liver, pancreas, heart, and pituitary. Full development of the disease in women is restricted by menstruation, pregnancy, and lower dietary intake of iron. Acquired hemochromatosis may be the result of blood transfusions, excessive dietary iron, or secondary to other disease. Idiopathic or genetic hemochromatosis is an autosomal recessive disorder of metabolism associated with a gene tightly linked to the a locus of the hla complex on chromosome 6. (from Dorland, 27th ed)
  • An inherited metabolic disorder characterized by iron accumulation in the tissues.
  • Condition in which there is a deviation or interruption in the storage of iron in the body.
  • Disorder due to the deposition of hemosiderin in the parenchymal cells, causing tissue damage and dysfunction of the liver, pancreas, heart, and pituitary; full development of the disease in women is restricted by menstruation, pregnancy, and lower dietary intake of iron; an autosomal recessive disorder of metabolism associated with a gene tightly linked to the a locus of the hla complex on chromosome 6.
  • Hemochromatosis is an inherited disease in which too much iron builds up in your body. It is one of the most common genetic diseases in the United States. iron is a mineral found in many foods. Your body normally absorbs about 10 percent of the iron in the food you eat. If you have hemochromatosis, you absorb more iron than you need. Your body has no natural way to get rid of the extra iron. It stores it in body tissues, especially the liver, heart and pancreas. The extra iron can damage your organs. Without treatment, it can cause your organs to fail. The most common treatment is to remove some blood, just like when you donate blood. This is called therapeutic phlebotomy. Medicines may also help remove the extra iron. Your doctor might suggest some changes in your diet.
  • What: hemochromatosis: hemochromatosis: a disorder of iron metabolism characterized by excess deposition of iron in the tissues, especially the liver. It is characterized by pigmentation of the skin, hepatic cirrhosis, decreased carbohydrate tolerance, cardiomyopathy and endocrinopathy (especially hypogonadism). Mainly seen in men over the age of 40 years. It has an associated arthropathy distinguished by involvement of the metacarpophalangeal joints (particularly the second and third), wrists, knees, shoulders, and hips. There is often an associated chondrocalcinosis. Why: hemochromatosis is an autosomal recessive disease that produces an arthritis similar to osteoarthritis or pseudogout. How: hemochromatosis is diagnosed by the typical physical and radiographic findings supported by elevated serum iron concentrations and high transferrin saturations. Serum ferritin is also markedly elevated. Confirmation of the diagnosis can be done by demonstrating hepatic iron deposition on liver biopsy.
ICD-10-CM E83.110 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 642 Inborn and other disorders of metabolism

Convert E83.110 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to E83.110:
  • Type 1 Excludes: K74
    ICD-10-CM Diagnosis Code K74

    Fibrosis and cirrhosis of liver

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Code Also
    • , if applicable, viral hepatitis (acute) (chronic) (B15-B19)
    Type 1 Excludes
    • alcoholic cirrhosis (of liver) (K70.3)
    • alcoholic fibrosis of liver (K70.2)
    • cardiac sclerosis of liver (K76.1)
    • cirrhosis (of liver) with toxic liver disease (K71.7)
    • congenital cirrhosis (of liver) (P78.81)
    • pigmentary cirrhosis (of liver) (E83.110)
  • Type 2 Excludes: K76
    ICD-10-CM Diagnosis Code K76

    Other diseases of liver

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • alcoholic liver disease (K70.-)
    • amyloid degeneration of liver (E85.-)
    • cystic disease of liver (congenital) (Q44.6)
    • hepatic vein thrombosis (I82.0)
    • hepatomegaly NOS (R16.0)
    • pigmentary cirrhosis (of liver) (E83.110)
    • portal vein thrombosis (I81)
    • toxic liver disease (K71.-)

Diagnosis Index entries containing back-references to E83.110:
  • Cirrhosis, cirrhotic (hepatic) (liver) K74.60
    ICD-10-CM Diagnosis Code K74.60

    Unspecified cirrhosis of liver

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Cirrhosis (of liver) NOS
    • pigmentary E83.110
  • Diabetes, diabetic (mellitus) (sugar) E11.9
    ICD-10-CM Diagnosis Code E11.9

    Type 2 diabetes mellitus without complications

      2016 2017 2018 2019 2020 Billable/Specific Code Questionable As Admission Dx
    • bronzed E83.110
  • Hemochromatosis E83.119
    ICD-10-CM Diagnosis Code E83.119

    Hemochromatosis, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    • hereditary E83.110 (primary)
    • primary E83.110

ICD-10-CM Codes Adjacent To E83.110
E80.6 Other disorders of bilirubin metabolism
E80.7 Disorder of bilirubin metabolism, unspecified
E83 Disorders of mineral metabolism
E83.0 Disorders of copper metabolism
E83.00 Disorder of copper metabolism, unspecified
E83.01 Wilson's disease
E83.09 Other disorders of copper metabolism
E83.1 Disorders of iron metabolism
E83.10 Disorder of iron metabolism, unspecified
E83.11 Hemochromatosis
E83.110 Hereditary hemochromatosis
E83.111 …… due to repeated red blood cell transfusions
E83.118 Other hemochromatosis
E83.119 …… unspecified
E83.19 Other disorders of iron metabolism
E83.2 Disorders of zinc metabolism
E83.3 Disorders of phosphorus metabolism and phosphatases
E83.30 Disorder of phosphorus metabolism, unspecified
E83.31 Familial hypophosphatemia
E83.32 Hereditary vitamin D-dependent rickets (type 1) (type 2)
E83.39 Other disorders of phosphorus metabolism

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.