2021 ICD-10-CM Diagnosis Code E83.31

Familial hypophosphatemia

    2016 2017 2018 2019 2020 2021 Billable/Specific Code
  • E83.31 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2021 edition of ICD-10-CM E83.31 became effective on October 1, 2020.
  • This is the American ICD-10-CM version of E83.31 - other international versions of ICD-10 E83.31 may differ.
Applicable To
  • Vitamin D-resistant osteomalacia
  • Vitamin D-resistant rickets
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as E83.31. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • vitamin D-deficiency rickets (
    ICD-10-CM Diagnosis Code E55.0

    Rickets, active

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Infantile osteomalacia
    • Juvenile osteomalacia
    Type 1 Excludes
    • celiac rickets (K90.0)
    • Crohn's rickets (K50.-)
    • hereditary vitamin D-dependent rickets (E83.32)
    • inactive rickets (E64.3)
    • renal rickets (N25.0)
    • sequelae of rickets (E64.3)
    • vitamin D-resistant rickets (E83.31)
    E55.0
    )
The following code(s) above E83.31 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to E83.31:
  • E00-E89
    2021 ICD-10-CM Range E00-E89

    Endocrine, nutritional and metabolic diseases

    Note
    • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
    Type 1 Excludes
    • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
    Endocrine, nutritional and metabolic diseases
  • E70-E88
    2021 ICD-10-CM Range E70-E88

    Metabolic disorders

    Type 1 Excludes
    • androgen insensitivity syndrome (E34.5-)
    • congenital adrenal hyperplasia (E25.0)
    • Ehlers-Danlos syndromes (Q79.6-)
    • hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan's syndrome (Q87.4)
    • 5-alpha-reductase deficiency (E29.1)
    Metabolic disorders
  • E83
    ICD-10-CM Diagnosis Code E83

    Disorders of mineral metabolism

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • dietary mineral deficiency (E58-E61)
    • parathyroid disorders (E20-E21)
    • vitamin D deficiency (E55.-)
    Disorders of mineral metabolism
  • E83.3
    ICD-10-CM Diagnosis Code E83.3

    Disorders of phosphorus metabolism and phosphatases

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Disorders of phosphorus metabolism and phosphatases
Approximate Synonyms
  • Familial x-linked hypophosphatemic vitamin d refractory rickets
  • Rickets, hypophosphatemic vit d refractory, familial
Clinical Information
  • An inherited condition of abnormally low serum levels of phosphates (below 1 mg/liter) which can occur in a number of genetic diseases with defective reabsorption of inorganic phosphorus by the proximal renal tubules. This leads to phosphaturia, hypophosphatemia, and disturbances of cellular and organ functions such as those in x-linked hypophosphatemic rickets; osteomalacia; and fanconi syndrome.
ICD-10-CM E83.31 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):
  • 642 Inborn and other disorders of metabolism

Convert E83.31 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
Code annotations containing back-references to E83.31:
  • Type 1 Excludes: E55.0
    ICD-10-CM Diagnosis Code E55.0

    Rickets, active

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Infantile osteomalacia
    • Juvenile osteomalacia
    Type 1 Excludes
    • celiac rickets (K90.0)
    • Crohn's rickets (K50.-)
    • hereditary vitamin D-dependent rickets (E83.32)
    • inactive rickets (E64.3)
    • renal rickets (N25.0)
    • sequelae of rickets (E64.3)
    • vitamin D-resistant rickets (E83.31)

Diagnosis Index entries containing back-references to E83.31:
  • Disorder (of) - see also Disease
    • metabolism NOS E88.9
      ICD-10-CM Diagnosis Code E88.9

      Metabolic disorder, unspecified

        2016 2017 2018 2019 2020 2021 Billable/Specific Code
      • phosphorus E83.30
        ICD-10-CM Diagnosis Code E83.30

        Disorder of phosphorus metabolism, unspecified

          2016 2017 2018 2019 2020 2021 Billable/Specific Code
        • hypophosphatemia E83.39
          ICD-10-CM Diagnosis Code E83.39

          Other disorders of phosphorus metabolism

            2016 2017 2018 2019 2020 2021 Billable/Specific Code
          Applicable To
          • Acid phosphatase deficiency
          • Hypophosphatasia
          • familial E83.31
  • Hypophosphatemia, hypophosphatasia (acquired) (congenital) (renal) E83.39
    ICD-10-CM Diagnosis Code E83.39

    Other disorders of phosphorus metabolism

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Acid phosphatase deficiency
    • Hypophosphatasia
    • familial E83.31
  • Osteomalacia M83.9
    ICD-10-CM Diagnosis Code M83.9

    Adult osteomalacia, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code Adult Dx (15-124 years)
    • vitamin-D-resistant in adults E83.31
      • carpus E83.31
      • clavicle E83.31
      • femur E83.31
      • fibula E83.31
      • finger E83.31
      • humerus E83.31
      • ilium E83.31
      • ischium E83.31
      • metacarpus E83.31
      • metatarsus E83.31
      • multiple sites E83.31
      • neck E83.31
      • radius E83.31
      • rib E83.31
      • scapula E83.31
      • skull E83.31
      • tarsus E83.31
      • tibia E83.31
      • toe E83.31
      • ulna E83.31
      • vertebra E83.31
  • Rickets (active) (acute) (adolescent) (chest wall) (congenital) (current) (infantile) (intestinal) E55.0
    ICD-10-CM Diagnosis Code E55.0

    Rickets, active

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Infantile osteomalacia
    • Juvenile osteomalacia
    Type 1 Excludes
    • celiac rickets (K90.0)
    • Crohn's rickets (K50.-)
    • hereditary vitamin D-dependent rickets (E83.32)
    • inactive rickets (E64.3)
    • renal rickets (N25.0)
    • sequelae of rickets (E64.3)
    • vitamin D-resistant rickets (E83.31)
    • vitamin-D-resistant E83.31

ICD-10-CM Codes Adjacent To E83.31
E83.10 Disorder of iron metabolism, unspecified
E83.11 Hemochromatosis
E83.110 Hereditary hemochromatosis
E83.111 …… due to repeated red blood cell transfusions
E83.118 Other hemochromatosis
E83.119 …… unspecified
E83.19 Other disorders of iron metabolism
E83.2 Disorders of zinc metabolism
E83.3 Disorders of phosphorus metabolism and phosphatases
E83.30 Disorder of phosphorus metabolism, unspecified
E83.31 Familial hypophosphatemia
E83.32 Hereditary vitamin D-dependent rickets (type 1) (type 2)
E83.39 Other disorders of phosphorus metabolism
E83.4 Disorders of magnesium metabolism
E83.40 …… unspecified
E83.41 Hypermagnesemia
E83.42 Hypomagnesemia
E83.49 Other disorders of magnesium metabolism
E83.5 Disorders of calcium metabolism
E83.50 Unspecified disorder of calcium metabolism
E83.51 Hypocalcemia

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.