2022 ICD-10-CM Diagnosis Code E84.0

Cystic fibrosis with pulmonary manifestations

    2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
  • E84.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2022 edition of ICD-10-CM E84.0 became effective on October 1, 2021.
  • This is the American ICD-10-CM version of E84.0 - other international versions of ICD-10 E84.0 may differ.
Use Additional
Use Additional Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • code to identify any infectious organism present, such as:
  • Pseudomonas (
    ICD-10-CM Diagnosis Code B96.5

    Pseudomonas (aeruginosa) (mallei) (pseudomallei) as the cause of diseases classified elsewhere

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
    B96.5
    )
The following code(s) above E84.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to E84.0:
  • E00-E89
    2022 ICD-10-CM Range E00-E89

    Endocrine, nutritional and metabolic diseases

    Note
    • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
    Type 1 Excludes
    • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
    Endocrine, nutritional and metabolic diseases
  • E70-E88
    2022 ICD-10-CM Range E70-E88

    Metabolic disorders

    Type 1 Excludes
    • androgen insensitivity syndrome (E34.5-)
    • congenital adrenal hyperplasia (E25.0)
    • hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan's syndrome (Q87.4)
    • 5-alpha-reductase deficiency (E29.1)
    Type 2 Excludes
    • Ehlers-Danlos syndromes (Q79.6-)
    Metabolic disorders
  • E84
    ICD-10-CM Diagnosis Code E84

    Cystic fibrosis

      2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
    Code Also
    • exocrine pancreatic insufficiency (K86.81)
    Includes
    • mucoviscidosis
    Cystic fibrosis
Approximate Synonyms
  • Cystic fibrosis of the lung
  • Cystic fibrosis, pulmonary
ICD-10-CM E84.0 is grouped within Diagnostic Related Group(s) (MS-DRG v39.0):
  • 177 Respiratory infections and inflammations with mcc
  • 178 Respiratory infections and inflammations with cc
  • 179 Respiratory infections and inflammations without cc/mcc

Convert E84.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
Code annotations containing back-references to E84.0:
  • Code Also: I27.23
    ICD-10-CM Diagnosis Code I27.23

    Pulmonary hypertension due to lung diseases and hypoxia

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
    Applicable To
    • Group 3 pulmonary hypertension
    Code Also
    • associated lung disease, if known, such as:
    • bronchiectasis (J47.-)
    • cystic fibrosis with pulmonary manifestations (E84.0)
    • interstitial lung disease (J84.-)
    • pleural effusion (J90)
    • sleep apnea (G47.3-)
  • Type 1 Excludes: J99
    , P78
    , Q33.0
    , Q45.3
    ICD-10-CM Diagnosis Code J99

    Respiratory disorders in diseases classified elsewhere

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code Manifestation Code
    Code First
    • underlying disease, such as:
    • amyloidosis (E85.-)
    • ankylosing spondylitis (M45)
    • congenital syphilis (A50.5)
    • cryoglobulinemia (D89.1)
    • early congenital syphilis (A50.0)
    • plasminogen deficiency (E88.02)
    • schistosomiasis (B65.0-B65.9)
    Type 1 Excludes
    ICD-10-CM Diagnosis Code P78

    Other perinatal digestive system disorders

      2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
    Type 1 Excludes
    ICD-10-CM Diagnosis Code Q33.0

    Congenital cystic lung

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital cystic lung disease
    • Congenital honeycomb lung
    • Congenital polycystic lung disease
    Type 1 Excludes
    • cystic fibrosis (E84.0)
    • cystic lung disease, acquired or unspecified (J98.4)
    ICD-10-CM Diagnosis Code Q45.3

    Other congenital malformations of pancreas and pancreatic duct

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code POA Exempt
    Applicable To
    • Accessory pancreas
    • Congenital malformation of pancreas or pancreatic duct NOS
    Type 1 Excludes
    • congenital diabetes mellitus (E10.-)
    • cystic fibrosis (E84.0-E84.9)
    • fibrocystic disease of pancreas (E84.-)
    • neonatal diabetes mellitus (P70.2)

Diagnosis Index entries containing back-references to E84.0:
  • Fibrosis, fibrotic
    • cystic (of pancreas) E84.9
      ICD-10-CM Diagnosis Code E84.9

      Cystic fibrosis, unspecified

        2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
      • with
        • pulmonary manifestations E84.0

ICD-10-CM Codes Adjacent To E84.0
E83.5 Disorders of calcium metabolism
E83.50 Unspecified disorder of calcium metabolism
E83.51 Hypocalcemia
E83.52 Hypercalcemia
E83.59 Other disorders of calcium metabolism
E83.8 Other disorders of mineral metabolism
E83.81 Hungry bone syndrome
E83.89 Other disorders of mineral metabolism
E83.9 Disorder of mineral metabolism, unspecified
E84 Cystic fibrosis
E84.0 Cystic fibrosis with pulmonary manifestations
E84.1 Cystic fibrosis with intestinal manifestations
E84.11 Meconium ileus in cystic fibrosis
E84.19 Cystic fibrosis with other intestinal manifestations
E84.8 Cystic fibrosis with other manifestations
E84.9 Cystic fibrosis, unspecified
E85 Amyloidosis
E85.0 Non-neuropathic heredofamilial amyloidosis
E85.1 Neuropathic heredofamilial amyloidosis
E85.2 Heredofamilial amyloidosis, unspecified
E85.3 Secondary systemic amyloidosis

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.