ICD-10-CM Codes
E00-E89
E70-E88
E84-
2023 ICD-10-CM Diagnosis Code E84.0

2023 ICD-10-CM Diagnosis Code E84.0

Cystic fibrosis with pulmonary manifestations

2016

2017

2018

2019

2020

2021

2022

2023

Billable/Specific Code

E84.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2023 edition of ICD-10-CM E84.0 became effective on October 1, 2022.
This is the American ICD-10-CM version of E84.0 - other international versions of ICD-10 E84.0 may differ.

Use Additional

Use Additional Help

Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.

code to identify any infectious organism present, such as:
Pseudomonas (
ICD-10-CM Diagnosis Code B96.5
Pseudomonas (aeruginosa) (mallei) (pseudomallei) as the cause of diseases classified elsewhere
B96.5
)

The following code(s) above E84.0 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to E84.0:

E00-E89
2023 ICD-10-CM Range E00-E89
Endocrine, nutritional and metabolic diseases
Note
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Type 1 Excludes
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Endocrine, nutritional and metabolic diseases
E70-E88
2023 ICD-10-CM Range E70-E88
Metabolic disorders
Type 1 Excludes
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan's syndrome (Q87.4)
- 5-alpha-reductase deficiency (E29.1)
Type 2 Excludes
- Ehlers-Danlos syndromes (Q79.6-)
Metabolic disorders
E84
ICD-10-CM Diagnosis Code E84
Cystic fibrosis
Code Also
- exocrine pancreatic insufficiency (K86.81)
Includes
- mucoviscidosis
Cystic fibrosis

Approximate Synonyms

Cystic fibrosis of the lung
Cystic fibrosis, pulmonary

ICD-10-CM E84.0 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):

177 Respiratory infections and inflammations with mcc
178 Respiratory infections and inflammations with cc
179 Respiratory infections and inflammations without cc/mcc

Convert E84.0 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change
2022 (effective 10/1/2021): No change
2023 (effective 10/1/2022): No change

Code annotations containing back-references to E84.0:

Code Also: I27.23

ICD-10-CM Diagnosis Code I27.23
Pulmonary hypertension due to lung diseases and hypoxia
Applicable To
- Group 3 pulmonary hypertension
Code Also
- associated lung disease, if known, such as:
- bronchiectasis (J47.-)
- cystic fibrosis with pulmonary manifestations (E84.0)
- interstitial lung disease (J84.-)
- pleural effusion (J90)
- sleep apnea (G47.3-)
Type 1 Excludes: P78
, Q33.0
, Q45.3
, J99

ICD-10-CM Diagnosis Code P78
Other perinatal digestive system disorders
Type 1 Excludes
- cystic fibrosis (E84.0-E84.9)
- neonatal gastrointestinal hemorrhages (P54.0-P54.3)
ICD-10-CM Diagnosis Code Q33.0
Congenital cystic lung
Applicable To
- Congenital cystic lung disease
- Congenital honeycomb lung
- Congenital polycystic lung disease
Type 1 Excludes
- cystic fibrosis (E84.0)
- cystic lung disease, acquired or unspecified (J98.4)
ICD-10-CM Diagnosis Code Q45.3
Other congenital malformations of pancreas and pancreatic duct
Applicable To
- Accessory pancreas
- Congenital malformation of pancreas or pancreatic duct NOS
Type 1 Excludes
- congenital diabetes mellitus (E10.-)
- cystic fibrosis (E84.0-E84.9)
- fibrocystic disease of pancreas (E84.-)
- neonatal diabetes mellitus (P70.2)
ICD-10-CM Diagnosis Code J99
Respiratory disorders in diseases classified elsewhere
Code First
- underlying disease, such as:
- amyloidosis (E85.-)
- ankylosing spondylitis (M45)
- congenital syphilis (A50.5)
- cryoglobulinemia (D89.1)
- early congenital syphilis (A50.0)
- plasminogen deficiency (E88.02)
- schistosomiasis (B65.0-B65.9)
Type 1 Excludes
- respiratory disorders in:
- amebiasis (A06.5)
- blastomycosis (B40.0-B40.2)
- candidiasis (B37.1)
- coccidioidomycosis (B38.0-B38.2)
- cystic fibrosis with pulmonary manifestations (E84.0)
- dermatomyositis (M33.01, M33.11)
- histoplasmosis (B39.0-B39.2)
- late syphilis (A52.72, A52.73)
- polymyositis (M33.21)
- Sjögren syndrome (M35.02)
- systemic lupus erythematosus (M32.13)
- systemic sclerosis (M34.81)
- Wegener's granulomatosis (M31.30-M31.31)

Diagnosis Index entries containing back-references to E84.0:

Fibrosis, fibrotic
- cystic (of pancreas) E84.9
  ICD-10-CM Diagnosis Code E84.9
  Cystic fibrosis, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - with
    - pulmonary manifestations E84.0

ICD-10-CM Codes Adjacent To E84.0

E83.5 Disorders of calcium metabolism

E83.50 Unspecified disorder of calcium metabolism

E83.51 Hypocalcemia

E83.52 Hypercalcemia

E83.59 Other disorders of calcium metabolism

E83.8 Other disorders of mineral metabolism

E83.81 Hungry bone syndrome

E83.89 Other disorders of mineral metabolism

E83.9 Disorder of mineral metabolism, unspecified

E84 Cystic fibrosis

E84.0 Cystic fibrosis with pulmonary manifestations

E84.1 Cystic fibrosis with intestinal manifestations

E84.11 Meconium ileus in cystic fibrosis

E84.19 Cystic fibrosis with other intestinal manifestations

E84.8 Cystic fibrosis with other manifestations

E84.9 Cystic fibrosis, unspecified

E85 Amyloidosis

E85.0 Non-neuropathic heredofamilial amyloidosis

E85.1 Neuropathic heredofamilial amyloidosis

E85.2 Heredofamilial amyloidosis, unspecified

E85.3 Secondary systemic amyloidosis

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2023 ICD-10-CM Diagnosis Code E84.0

Cystic fibrosis with pulmonary manifestations

Pseudomonas (aeruginosa) (mallei) (pseudomallei) as the cause of diseases classified elsewhere

Endocrine, nutritional and metabolic diseases

Metabolic disorders

Cystic fibrosis

Pulmonary hypertension due to lung diseases and hypoxia

Other perinatal digestive system disorders

Congenital cystic lung

Other congenital malformations of pancreas and pancreatic duct

Respiratory disorders in diseases classified elsewhere

Cystic fibrosis, unspecified