2020 ICD-10-CM Diagnosis Code E88.89

Other specified metabolic disorders

    2016 2017 2018 2019 2020 Billable/Specific Code
  • E88.89 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM E88.89 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of E88.89 - other international versions of ICD-10 E88.89 may differ.
Applicable To
  • Launois-Bensaude adenolipomatosis
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as E88.89. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • adult pulmonary Langerhans cell histiocytosis (
    ICD-10-CM Diagnosis Code J84.82

    Adult pulmonary Langerhans cell histiocytosis

      2016 2017 2018 2019 2020 Billable/Specific Code Adult Dx (15-124 years)
    Applicable To
    • Adult PLCH
    J84.82
    )
The following code(s) above E88.89 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to E88.89:
  • E00-E89
    2020 ICD-10-CM Range E00-E89

    Endocrine, nutritional and metabolic diseases

    Note
    • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
    Type 1 Excludes
    • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
    Endocrine, nutritional and metabolic diseases
  • E70-E88
    2020 ICD-10-CM Range E70-E88

    Metabolic disorders

    Type 1 Excludes
    • androgen insensitivity syndrome (E34.5-)
    • congenital adrenal hyperplasia (E25.0)
    • Ehlers-Danlos syndrome (Q79.6-)
    • hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan's syndrome (Q87.4)
    • 5-alpha-reductase deficiency (E29.1)
    Metabolic disorders
  • E88
    ICD-10-CM Diagnosis Code E88

    Other and unspecified metabolic disorders

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • histiocytosis X (chronic) (C96.6)
    Use Additional
    • codes for associated conditions
    Other and unspecified metabolic disorders
Approximate Synonyms
  • Disorder of lysosomal enzyme
  • Disorder of organic acid metabolism
  • Ketosis
  • Lysosomal enzyme defect
  • Lysosomal storage disease
  • Organic acid metabolism disorder
ICD-10-CM E88.89 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 642 Inborn and other disorders of metabolism

Convert E88.89 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to E88.89:
  • Adenolipomatosis, Launois-Bensaude E88.89
  • Deficiency, deficient
    • dihydropyrimidine dehydrogenase E88.89 (DPD)
  • Dihydropyrimidine dehydrogenase disease E88.89 (DPD)
  • Disease, diseased - see also Syndrome
    • Erdheim-Chester E88.89 (ECD)
  • Disorder (of) - see also Disease
    • metabolism NOS E88.9
      ICD-10-CM Diagnosis Code E88.9

      Metabolic disorder, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code
      • specified NEC E88.89
  • DPD E88.89 (dihydropyrimidine dehydrogenase deficiency)
  • Hoffa-Kastert disease E88.89
  • Hoffa's disease E88.89
  • Ketosis NEC E88.89
  • Launois-Bensaude adenolipomatosis E88.89
  • Lipomatosis E88.2
    ICD-10-CM Diagnosis Code E88.2

    Lipomatosis, not elsewhere classified

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Lipomatosis NOS
    • Lipomatosis (Check) dolorosa [Dercum]
    • Launois-Bensaude E88.89
  • Liposynovitis prepatellaris E88.89
  • Madelung's
    • disease
      • symmetrical lipomas, neck E88.89
  • Steatosis E88.89
  • Syndrome - see also Disease
    • Erdheim-Chester E88.89 (ECD)

ICD-10-CM Codes Adjacent To E88.89
E88.1 Lipodystrophy, not elsewhere classified
E88.2 Lipomatosis, not elsewhere classified
E88.3 Tumor lysis syndrome
E88.4 Mitochondrial metabolism disorders
E88.40 Mitochondrial metabolism disorder, unspecified
E88.41 MELAS syndrome
E88.42 MERRF syndrome
E88.49 Other mitochondrial metabolism disorders
E88.8 Other specified metabolic disorders
E88.81 Metabolic syndrome
E88.89 Other specified metabolic disorders
E88.9 Metabolic disorder, unspecified
E89 Postprocedural endocrine and metabolic complications and disorders, not elsewhere classified
E89.0 Postprocedural hypothyroidism
E89.1 Postprocedural hypoinsulinemia
E89.2 Postprocedural hypoparathyroidism
E89.3 Postprocedural hypopituitarism
E89.4 Postprocedural ovarian failure
E89.40 Asymptomatic postprocedural ovarian failure
E89.41 Symptomatic postprocedural ovarian failure
E89.5 Postprocedural testicular hypofunction

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.