2020 ICD-10-CM Diagnosis Code F84.2

Rett's syndrome

    2016 2017 2018 2019 2020 Billable/Specific Code
  • F84.2 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM F84.2 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of F84.2 - other international versions of ICD-10 F84.2 may differ.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as F84.2. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Asperger's syndrome (
    ICD-10-CM Diagnosis Code F84.5

    Asperger's syndrome

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Asperger's disorder
    • Autistic psychopathy
    • Schizoid disorder of childhood
    F84.5
    )
  • Autistic disorder (
    ICD-10-CM Diagnosis Code F84.0

    Autistic disorder

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Autism spectrum disorder
    • Infantile autism
    • Infantile psychosis
    • Kanner's syndrome
    Type 1 Excludes
    • Asperger's syndrome (F84.5)
    F84.0
    )
  • Other childhood disintegrative disorder (
    ICD-10-CM Diagnosis Code F84.3

    Other childhood disintegrative disorder

      2016 2017 2018 2019 2020 Billable/Specific Code Pediatric Dx (0-17 years)
    Applicable To
    • Dementia infantilis
    • Disintegrative psychosis
    • Heller's syndrome
    • Symbiotic psychosis
    Type 1 Excludes
    • Asperger's syndrome (F84.5)
    • Autistic disorder (F84.0)
    • Rett's syndrome (F84.2)
    Use Additional
    • code to identify any associated neurological condition.
    F84.3
    )
The following code(s) above F84.2 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to F84.2:
  • F01-F99
    2020 ICD-10-CM Range F01-F99

    Mental, Behavioral and Neurodevelopmental disorders

    Includes
    • disorders of psychological development
    Type 2 Excludes
    • symptoms, signs and abnormal clinical laboratory findings, not elsewhere classified (R00-R99)
    Mental, Behavioral and Neurodevelopmental disorders
  • F84
    ICD-10-CM Diagnosis Code F84

    Pervasive developmental disorders

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Use Additional
    • code to identify any associated medical condition and intellectual disabilities.
    Pervasive developmental disorders
Approximate Synonyms
  • Dementia and behavioral disturbance due to rett's syndrome
  • Dementia due rett's syndrome
  • Dementia due to rett's syndrome
  • Rett syndrome
  • Rett syndrome w dementia
  • Rett syndrome w dementia w behavioral disturbance
  • Rett's disorder
  • Retts syndrome
  • Retts syndrome with dementia
Clinical Information
  • A progressive neurologic disorder caused by mutations in the mecp2 gene on chromosome x. It almost exclusively affects girls. It is characterized by language and learning difficulties, poor communication skills, and repetitive hand motions. Other signs and symptoms include microcephaly, scoliosis, breathing abnormalities, and sleep disturbances.
  • An inherited neurological developmental disorder that is associated with x-linked inheritance and may be lethal in utero to hemizygous males. The affected female is normal until the age of 6-25 months when progressive loss of voluntary control of hand movements and communication skills; ataxia; seizures; autistic behavior; intermittent hyperventilation; and hyperammonemia appear. (from menkes, textbook of child neurology, 5th ed, p199)
  • Progressive disorder affecting the cerebral cortex of females; present from birth; manifested by autistic behavior, ataxia, dementia, seizures, loss of purposeful usefulness of the hands, cerebral atrophy, and mild hyperammonemia.
  • Progressive encephalopathy occurring almost exclusively in females. The affected children are generally born clinically normal in most but not all cases. Their neurological and mental development begins to stagnate between the ages of 7 and 18 months with slowing down of the growth of head circumference and a rapid deterioration of brain functions marked by autistic behavior, dementia, apraxia of gait, loss of facial expression, deterioration of purposeful use of hands, ataxia, and severe dementia. There is an intermediate period of relative stable mental status, sometimes lasting several decades, which is followed by further neurological degradation, marked mainly by spasticity of the lower limbs and epilepsy.
  • Rett syndrome is a rare inherited disease that causes developmental and nervous system problems, mostly in girls. It's related to autism. Babies with rett syndrome seem to grow and develop normally at first. Between 3 months and 3 years of age, though, they stop developing and even lose some skills. Symptoms include
    • loss of speech
    • loss of hand movements such as grasping
    • compulsive movements such as hand wringing
    • balance problems
    • breathing problems
    • behavior problems
    • learning problems or mental retardation
    rett syndrome has no cure. You can treat some of the symptoms with medicines, surgery, and physical and speech therapy. Most people with rett syndrome live into middle age and beyond. They will usually need care throughout their lives. nih: national institute of child health and human development
ICD-10-CM F84.2 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 056 Degenerative nervous system disorders with mcc
  • 057 Degenerative nervous system disorders without mcc

Convert F84.2 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to F84.2:
  • Type 1 Excludes: F84.3
    ICD-10-CM Diagnosis Code F84.3

    Other childhood disintegrative disorder

      2016 2017 2018 2019 2020 Billable/Specific Code Pediatric Dx (0-17 years)
    Applicable To
    • Dementia infantilis
    • Disintegrative psychosis
    • Heller's syndrome
    • Symbiotic psychosis
    Type 1 Excludes
    • Asperger's syndrome (F84.5)
    • Autistic disorder (F84.0)
    • Rett's syndrome (F84.2)
    Use Additional
    • code to identify any associated neurological condition.

Diagnosis Index entries containing back-references to F84.2:
  • Rett's disease or syndrome F84.2

ICD-10-CM Codes Adjacent To F84.2
F81 Specific developmental disorders of scholastic skills
F81.0 Specific reading disorder
F81.2 Mathematics disorder
F81.8 Other developmental disorders of scholastic skills
F81.81 Disorder of written expression
F81.89 Other developmental disorders of scholastic skills
F81.9 Developmental disorder of scholastic skills, unspecified
F82 Specific developmental disorder of motor function
F84 Pervasive developmental disorders
F84.0 Autistic disorder
F84.2 Rett's syndrome
F84.3 Other childhood disintegrative disorder
F84.5 Asperger's syndrome
F84.8 Other pervasive developmental disorders
F84.9 Pervasive developmental disorder, unspecified
F88 Other disorders of psychological development
F89 Unspecified disorder of psychological development
F90 Attention-deficit hyperactivity disorders
F90.0 Attention-deficit hyperactivity disorder, predominantly inattentive type
F90.1 Attention-deficit hyperactivity disorder, predominantly hyperactive type
F90.2 Attention-deficit hyperactivity disorder, combined type

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.