2023 ICD-10-CM Diagnosis Code G04.0

Acute disseminated encephalitis and encephalomyelitis (ADEM)

    2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
  • G04.0 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2023 edition of ICD-10-CM G04.0 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of G04.0 - other international versions of ICD-10 G04.0 may differ.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as G04.0. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • acute necrotizing hemorrhagic encephalopathy (
    ICD-10-CM Diagnosis Code G04.3

    Acute necrotizing hemorrhagic encephalopathy

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • acute disseminated encephalitis and encephalomyelitis (G04.0-)
    G04.3-
    )
  • other noninfectious acute disseminated encephalomyelitis (noninfectious ADEM) (
    ICD-10-CM Diagnosis Code G04.81

    Other encephalitis and encephalomyelitis

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Noninfectious acute disseminated encephalomyelitis (noninfectious ADEM)
    G04.81
    )
The following code(s) above G04.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G04.0:
  • G00-G99
    2023 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G04
    ICD-10-CM Diagnosis Code G04

    Encephalitis, myelitis and encephalomyelitis

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Includes
    • acute ascending myelitis
    • meningoencephalitis
    • meningomyelitis
    Type 1 Excludes
    Type 2 Excludes
    • acute transverse myelitis (G37.3-)
    • alcoholic encephalopathy (G31.2)
    • multiple sclerosis (G35)
    • myalgic encephalomyelitis (G93.32)
    • subacute necrotizing myelitis (G37.4)
    • toxic encephalitis (G92.8)
    • toxic encephalopathy (G92.8)
    Encephalitis, myelitis and encephalomyelitis
Clinical Information
  • An acute or subacute inflammatory process of the central nervous system characterized histologically by multiple foci of perivascular demyelination. Symptom onset usually occurs several days after an acute viral infection or immunization, but it may coincide with the onset of infection or rarely no antecedent event can be identified. Clinical manifestations include confusion, somnolence, fever, nuchal rigidity, and involuntary movements. The illness may progress to coma and eventually be fatal. (Adams et al., Principles of Neurology, 6th ed, p921)
  • An inflammatory process affecting the central nervous system. It is characterized by perivascular demyelination. Symptoms usually follow an acute viral infection or immunization and include fever, confusion, somnolence and involuntary movements. It may lead to coma and death.
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change
Code annotations containing back-references to G04.0:
  • Type 1 Excludes: G04.3
    ICD-10-CM Diagnosis Code G04.3

    Acute necrotizing hemorrhagic encephalopathy

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • acute disseminated encephalitis and encephalomyelitis (G04.0-)
ICD-10-CM Codes Adjacent To G04.0
G00.9 Bacterial meningitis, unspecified
G01 Meningitis in bacterial diseases classified elsewhere
G02 Meningitis in other infectious and parasitic diseases classified elsewhere
G03 Meningitis due to other and unspecified causes
G03.0 Nonpyogenic meningitis
G03.1 Chronic meningitis
G03.2 Benign recurrent meningitis [Mollaret]
G03.8 Meningitis due to other specified causes
G03.9 Meningitis, unspecified
G04 Encephalitis, myelitis and encephalomyelitis
G04.0 Acute disseminated encephalitis and encephalomyelitis (ADEM)
G04.00 Acute disseminated encephalitis and encephalomyelitis, unspecified
G04.01 Postinfectious acute disseminated encephalitis and encephalomyelitis (postinfectious ADEM)
G04.02 Postimmunization acute disseminated encephalitis, myelitis and encephalomyelitis
G04.1 Tropical spastic paraplegia
G04.2 Bacterial meningoencephalitis and meningomyelitis, not elsewhere classified
G04.3 Acute necrotizing hemorrhagic encephalopathy
G04.30 …… unspecified
G04.31 Postinfectious acute necrotizing hemorrhagic encephalopathy
G04.32 Postimmunization acute necrotizing hemorrhagic encephalopathy
G04.39 Other acute necrotizing hemorrhagic encephalopathy

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.