2021 ICD-10-CM Diagnosis Code G11.1

Early-onset cerebellar ataxia

    2016 2017 2018 2019 2020 2021 - Converted to Parent Code Non-Billable/Non-Specific Code
  • G11.1 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • ICD-10-CM G11.1 is a new 2021 ICD-10-CM code that became effective on October 1, 2020.
  • This is the American ICD-10-CM version of G11.1 - other international versions of ICD-10 G11.1 may differ.
The following code(s) above G11.1 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G11.1:
  • G00-G99
    2021 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G11
    ICD-10-CM Diagnosis Code G11

    Hereditary ataxia

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • cerebral palsy (G80.-)
    • hereditary and idiopathic neuropathy (G60.-)
    • metabolic disorders (E70-E88)
    Hereditary ataxia
Approximate Synonyms
  • Azorean disease
  • Cerebellar ataxia (loss of muscle coordination)
  • Cervical neuromuscular scoliosis due to friedreich's ataxia
  • Cervical scoliosis due to friedreichs ataxia
  • Cervicothoracic neuromuscular scoliosis due to friedreich's ataxia
  • Cervicothoracic scoliosis due to friedreichs ataxia
  • Early onset cerebellar ataxia
  • Friedreich's ataxia
  • Friedreichs ataxia
  • Josephs disease
  • Lumbar neuromuscular scoliosis due to friedreich's ataxia
  • Lumbar scoliosis due to friedreichs ataxia
  • Lumbosacral neuromuscular scoliosis due to friedreich's ataxia
  • Lumbosacral scoliosis due to friedreichs ataxia
  • Machado joseph disease
  • Neuromuscular scoliosis due to friedreich's ataxia
  • Neuromuscular scoliosis due to friedreichs ataxia
  • Occipitoatlantoaxial neuromuscular scoliosis due to friedreich's ataxia
  • Occipitoatlantoaxial scoliosis in friedreichs ataxia
  • Spinocerebellar ataxia
  • Thoracic neuromuscular scoliosis due to friedreich's ataxia
  • Thoracic scoliosis due to friedreichs ataxia
  • Thoracolumbar neuromuscular scoliosis due to friedreich's ataxia
  • Thoracolumbarscoliosis due to friedreichs ataxia
Clinical Information
  • A condition marked by progressive cerebellar ataxia combined with myoclonus usually presenting in the third decade of life or later. Additional clinical features may include generalized and focal seizures, spasticity, and dyskinesias. Autosomal recessive and autosomal dominant patterns of inheritance have been reported. Pathologically, the dentate nucleus and brachium conjunctivum of the cerebellum are atrophic, with variable involvement of the spinal cord, cerebellar cortex, and basal ganglia. (from Joynt, Clinical Neurology, 1991, ch37, pp60-1)
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): Deleted code
  • 2021 (effective 10/1/2020): New code
ICD-10-CM Codes Adjacent To G11.1
G06 Intracranial and intraspinal abscess and granuloma
G06.0 Intracranial abscess and granuloma
G06.1 Intraspinal abscess and granuloma
G06.2 Extradural and subdural abscess, unspecified
G07 Intracranial and intraspinal abscess and granuloma in diseases classified elsewhere
G08 Intracranial and intraspinal phlebitis and thrombophlebitis
G09 Sequelae of inflammatory diseases of central nervous system
G10 Huntington's disease
G11 Hereditary ataxia
G11.0 Congenital nonprogressive ataxia
G11.1 Early-onset cerebellar ataxia
G11.10 …… unspecified
G11.11 Friedreich ataxia
G11.19 Other early-onset cerebellar ataxia
G11.2 Late-onset cerebellar ataxia
G11.3 Cerebellar ataxia with defective DNA repair
G11.4 Hereditary spastic paraplegia
G11.8 Other hereditary ataxias
G11.9 Hereditary ataxia, unspecified
G12 Spinal muscular atrophy and related syndromes
G12.0 Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.