2021 ICD-10-CM Diagnosis Code G11.11

Friedreich ataxia

    2021 - New Code Billable/Specific Code
  • G11.11 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • ICD-10-CM G11.11 is a new 2021 ICD-10-CM code that became effective on October 1, 2020.
  • This is the American ICD-10-CM version of G11.11 - other international versions of ICD-10 G11.11 may differ.
Applicable To
  • Autosomal recessive Friedreich ataxia
  • Friedreich ataxia with retained reflexes
The following code(s) above G11.11 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G11.11:
  • G00-G99
    2021 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G11
    ICD-10-CM Diagnosis Code G11

    Hereditary ataxia

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • cerebral palsy (G80.-)
    • hereditary and idiopathic neuropathy (G60.-)
    • metabolic disorders (E70-E88)
    Hereditary ataxia
ICD-10-CM G11.11 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):
  • 058 Multiple sclerosis and cerebellar ataxia with mcc
  • 059 Multiple sclerosis and cerebellar ataxia with cc
  • 060 Multiple sclerosis and cerebellar ataxia without cc/mcc
Code History
  • 2021 (effective 10/1/2020): New code

Diagnosis Index entries containing back-references to G11.11:
  • Ataxia, ataxy, ataxic R27.0
    ICD-10-CM Diagnosis Code R27.0

    Ataxia, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Type 1 Excludes
    • ataxia following cerebrovascular disease (I69. with final characters -93)
    • hereditary G11.9
      ICD-10-CM Diagnosis Code G11.9

      Hereditary ataxia, unspecified

        2016 2017 2018 2019 2020 2021 Billable/Specific Code
      Applicable To
      • Hereditary cerebellar ataxia NOS
      • Hereditary cerebellar degeneration
      • Hereditary cerebellar disease
      • Hereditary cerebellar syndrome
      • spinal G11.11 (Friedreich's)
    • spinal
      • hereditary G11.11 (Friedreich's)
    • autosomal recessive Friedreich G11.11
    • Friedreich's G11.11 (heredofamilial) (cerebellar) (spinal) (with retained reflexes)
  • Cardiomyopathy (familial) (idiopathic) I42.9
    ICD-10-CM Diagnosis Code I42.9

    Cardiomyopathy, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Cardiomyopathy (primary) (secondary) NOS
    • due to
      • Friedreich's ataxia G11.11
  • Disease, diseased - see also Syndrome
  • Friedreich's
    • ataxia G11.11
    • combined systemic disease G11.11
    • sclerosis G11.11 (cerebellum) (spinal cord)
  • Myocardiopathy (congestive) (constrictive) (familial) (hypertrophic nonobstructive) (idiopathic) (infiltrative) (obstructive) (primary) (restrictive) (sporadic) I42.9
    - see also Cardiomyopathy
    ICD-10-CM Diagnosis Code I42.9

    Cardiomyopathy, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Cardiomyopathy (primary) (secondary) NOS
    • in (due to)
      • Friedreich's ataxia G11.11
  • Sclerosis, sclerotic
    • hereditary
      • spinal G11.11 (Friedreich's ataxia)
    • spinal (cord) (progressive) G95.89
      ICD-10-CM Diagnosis Code G95.89

      Other specified diseases of spinal cord

        2016 2017 2018 2019 2020 2021 Billable/Specific Code
      Applicable To
      • Cord bladder NOS
      • Drug-induced myelopathy
      • Radiation-induced myelopathy
      Type 1 Excludes
      • hereditary G11.11 (Friedreich's) (mixed form)
    • Friedreich's G11.11 (spinal cord)

ICD-10-CM Codes Adjacent To G11.11
G06.1 Intraspinal abscess and granuloma
G06.2 Extradural and subdural abscess, unspecified
G07 Intracranial and intraspinal abscess and granuloma in diseases classified elsewhere
G08 Intracranial and intraspinal phlebitis and thrombophlebitis
G09 Sequelae of inflammatory diseases of central nervous system
G10 Huntington's disease
G11 Hereditary ataxia
G11.0 Congenital nonprogressive ataxia
G11.1 Early-onset cerebellar ataxia
G11.10 …… unspecified
G11.11 Friedreich ataxia
G11.19 Other early-onset cerebellar ataxia
G11.2 Late-onset cerebellar ataxia
G11.3 Cerebellar ataxia with defective DNA repair
G11.4 Hereditary spastic paraplegia
G11.8 Other hereditary ataxias
G11.9 Hereditary ataxia, unspecified
G12 Spinal muscular atrophy and related syndromes
G12.0 Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
G12.1 Other inherited spinal muscular atrophy
G12.2 Motor neuron disease

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.