2020 ICD-10-CM Diagnosis Code G11.4

Hereditary spastic paraplegia

    2016 2017 2018 2019 2020 Billable/Specific Code
  • G11.4 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM G11.4 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of G11.4 - other international versions of ICD-10 G11.4 may differ.
The following code(s) above G11.4 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G11.4:
  • G00-G99
    2020 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G11
    ICD-10-CM Diagnosis Code G11

    Hereditary ataxia

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • cerebral palsy (G80.-)
    • hereditary and idiopathic neuropathy (G60.-)
    • metabolic disorders (E70-E88)
    Hereditary ataxia
Approximate Synonyms
  • Paraplegia (paralysis of legs), hereditary spastic
Clinical Information
  • A group of inherited diseases that share similar phenotypes but are genetically diverse. Different genetic loci for autosomal recessive, autosomal dominant, and x-linked forms of hereditary spastic paraplegia have been identified. Clinically, patients present with slowly progressive distal limb weakness and lower extremity spasticity. Peripheral sensory neurons may be affected in the later stages of the disease. (j neurol neurosurg psychiatry 1998 jan;64(1):61-6; curr opin neurol 1997 aug;10(4):313-8)
ICD-10-CM G11.4 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 058 Multiple sclerosis and cerebellar ataxia with mcc
  • 059 Multiple sclerosis and cerebellar ataxia with cc
  • 060 Multiple sclerosis and cerebellar ataxia without cc/mcc

Convert G11.4 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to G11.4:
  • Type 1 Excludes: G80
    ICD-10-CM Diagnosis Code G80

    Cerebral palsy

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • hereditary spastic paraplegia (G11.4)

Diagnosis Index entries containing back-references to G11.4:
  • Ataxia, ataxy, ataxic R27.0
    ICD-10-CM Diagnosis Code R27.0

    Ataxia, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    Type 1 Excludes
    • ataxia following cerebrovascular disease (I69. with final characters -93)
    • hereditary G11.9
      ICD-10-CM Diagnosis Code G11.9

      Hereditary ataxia, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Hereditary cerebellar ataxia NOS
      • Hereditary cerebellar degeneration
      • Hereditary cerebellar disease
      • Hereditary cerebellar syndrome
      • spastic G11.4
    • spastic hereditary G11.4
  • Paralysis, paralytic (complete) (incomplete) G83.9
    ICD-10-CM Diagnosis Code G83.9

    Paralytic syndrome, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    • familial (recurrent) (periodic) G72.3
      ICD-10-CM Diagnosis Code G72.3

      Periodic paralysis

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Familial periodic paralysis
      • Hyperkalemic periodic paralysis (familial)
      • Hypokalemic periodic paralysis (familial)
      • Myotonic periodic paralysis (familial)
      • Normokalemic paralysis (familial)
      • Potassium sensitive periodic paralysis
      Type 1 Excludes
      • paramyotonia congenita (of von Eulenburg) (G71.19)
      • spastic G11.4
    • spastic G83.9
      ICD-10-CM Diagnosis Code G83.9

      Paralytic syndrome, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code
      • familial G11.4
      • hereditary G11.4
  • Paraplegia (lower) G82.20
    ICD-10-CM Diagnosis Code G82.20

    Paraplegia, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    • spastic
      • hereditary G11.4
    • familial spastic G11.4
    • hereditary, spastic G11.4

ICD-10-CM Codes Adjacent To G11.4
G06.2 Extradural and subdural abscess, unspecified
G07 Intracranial and intraspinal abscess and granuloma in diseases classified elsewhere
G08 Intracranial and intraspinal phlebitis and thrombophlebitis
G09 Sequelae of inflammatory diseases of central nervous system
G10 Huntington's disease
G11 Hereditary ataxia
G11.0 Congenital nonprogressive ataxia
G11.1 Early-onset cerebellar ataxia
G11.2 Late-onset cerebellar ataxia
G11.3 Cerebellar ataxia with defective DNA repair
G11.4 Hereditary spastic paraplegia
G11.8 Other hereditary ataxias
G11.9 Hereditary ataxia, unspecified
G12 Spinal muscular atrophy and related syndromes
G12.0 Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
G12.1 Other inherited spinal muscular atrophy
G12.2 Motor neuron disease
G12.20 …… unspecified
G12.21 Amyotrophic lateral sclerosis
G12.22 Progressive bulbar palsy
G12.23 Primary lateral sclerosis

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.