Other degenerative diseases of nervous system, not elsewhere classified G31-

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Use Additional
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Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • For codes
    ICD-10-CM Diagnosis Code G31.0

    Frontotemporal dementia

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    G31.0-
    ICD-10-CM Diagnosis Code G31.83

    Neurocognitive disorder with Lewy bodies

      2016 2017 2018 2019 2020 2021 2022 2023 - Revised Code Billable/Specific Code
    Applicable To
    • Lewy body dementia
    • Lewy body disease
    Use Additional
    • code, if applicable, to identify mild neurocognitive disorders due to known physiological condition (F06.7-)
    G31.83
    ,
    ICD-10-CM Diagnosis Code G31.85

    Corticobasal degeneration

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    G31.85-
    ICD-10-CM Diagnosis Code G31.9

    Degenerative disease of nervous system, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    G31.9
    , use additional code, if applicable, to identify:
  • dementia with anxiety (
    ICD-10-CM Diagnosis Code F02.84

    Dementia in other diseases classified elsewhere, unspecified severity, with anxiety

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Major neurocognitive disorder in other diseases classified elsewhere unspecified severity, with anxiety
    F02.84
    ,
    ICD-10-CM Diagnosis Code F02.A4

    Dementia in other diseases classified elsewhere, mild, with anxiety

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Major neurocognitive disorder in other diseases classified elsewhere, mild, with anxiety
    F02.A4
    ,
    ICD-10-CM Diagnosis Code F02.B4

    Dementia in other diseases classified elsewhere, moderate, with anxiety

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Major neurocognitive disorder in other diseases classified elsewhere, moderate, with anxiety
    F02.B4
    ,
    ICD-10-CM Diagnosis Code F02.C4

    Dementia in other diseases classified elsewhere, severe, with anxiety

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Major neurocognitive disorder in other diseases classified elsewhere, severe, with anxiety
    F02.C4
    )
  • dementia with behavioral disturbance (
    ICD-10-CM Diagnosis Code F02.81

    Dementia in other diseases classified elsewhere, unspecified severity, with behavioral disturbance

      2016 2017 2018 2019 2020 2021 2022 2023 - Converted to Parent Code Non-Billable/Non-Specific Code
    F02.81-
    ,
    ICD-10-CM Diagnosis Code F02.A1

    Dementia in other diseases classified elsewhere, mild, with behavioral disturbance

      2023 - New Code Non-Billable/Non-Specific Code
    F02.A1-
    ,
    ICD-10-CM Diagnosis Code F02.B1

    Dementia in other diseases classified elsewhere, moderate, with behavioral disturbance

      2023 - New Code Non-Billable/Non-Specific Code
    F02.B1-
    ,
    ICD-10-CM Diagnosis Code F02.C1

    Dementia in other diseases classified elsewhere, severe, with behavioral disturbance

      2023 - New Code Non-Billable/Non-Specific Code
    F02.C1-
    )
  • dementia with mood disturbance (
    ICD-10-CM Diagnosis Code F02.83

    Dementia in other diseases classified elsewhere, unspecified severity, with mood disturbance

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Dementia in other diseases classified elsewhere, unspecified severity, with mood disturbance such as depression, apathy, or anhedonia
    • Major neurocognitive disorder in other diseases classified elsewhere unspecified severity, with mood disturbance such as with depression, apathy, or anhedonia
    F02.83
    ,
    ICD-10-CM Diagnosis Code F02.A3

    Dementia in other diseases classified elsewhere, mild, with mood disturbance

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Dementia in other diseases classified elsewhere, mild, with mood disturbance such as depression, apathy, or anhedonia
    • Major neurocognitive disorder in other diseases classified elsewhere, mild, with mood disturbance such as depression, apathy, or anhedonia
    F02.A3
    ,
    ICD-10-CM Diagnosis Code F02.B3

    Dementia in other diseases classified elsewhere, moderate, with mood disturbance

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Dementia in other diseases classified elsewhere, moderate, with mood disturbance such as depression, apathy, or anhedonia
    • Major neurocognitive disorder in other diseases classified elsewhere, moderate, with mood disturbance such as depression, apathy, or anhedonia
    F02.B3
    ,
    ICD-10-CM Diagnosis Code F02.C3

    Dementia in other diseases classified elsewhere, severe, with mood disturbance

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Dementia in other diseases classified elsewhere, severe, with mood disturbance such as depression, apathy, or anhedonia
    • Major neurocognitive disorder in other diseases classified elsewhere, severe, with mood disturbance such as depression, apathy, or anhedonia
    F02.C3
    )
  • dementia with psychotic disturbance (
    ICD-10-CM Diagnosis Code F02.82

    Dementia in other diseases classified elsewhere, unspecified severity, with psychotic disturbance

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Dementia in other diseases classified elsewhere, unspecified severity, with psychotic disturbance such as hallucinations, paranoia, suspiciousness, or delusional state
    • Major neurocognitive disorder in other diseases classified elsewhere, unspecified, with psychotic disturbance such as hallucinations, paranoia, suspiciousness, or delusional state
    F02.82
    ,
    ICD-10-CM Diagnosis Code F02.A2

    Dementia in other diseases classified elsewhere, mild, with psychotic disturbance

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Dementia in other diseases classified elsewhere, mild, with psychotic disturbance such as hallucinations, paranoia, suspiciousness, or delusional state
    • Major neurocognitive disorder in other diseases classified elsewhere, mild, with psychotic disturbance such as hallucinations, paranoia, suspiciousness, or delusional state
    F02.A2
    ,
    ICD-10-CM Diagnosis Code F02.B2

    Dementia in other diseases classified elsewhere, moderate, with psychotic disturbance

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Dementia in other diseases classified elsewhere, moderate, with psychotic disturbance such as hallucinations, paranoia, suspiciousness, or delusional state
    • Major neurocognitive disorder in other diseases classified elsewhere, moderate, with psychotic disturbance such as hallucinations, paranoia, suspiciousness, or delusional state
    F02.B2
    ,
    ICD-10-CM Diagnosis Code F02.C2

    Dementia in other diseases classified elsewhere, severe, with psychotic disturbance

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Dementia in other diseases classified elsewhere, severe, with psychotic disturbance such as hallucinations, paranoia, suspiciousness, or delusional state
    • Major neurocognitive disorder in other diseases classified elsewhere, severe, with psychotic disturbance such as hallucinations, paranoia, suspiciousness, or delusional state
    F02.C2
    )
  • dementia without behavioral disturbance (
    ICD-10-CM Diagnosis Code F02.80

    Dementia in other diseases classified elsewhere, unspecified severity, without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety

      2016 2017 2018 2019 2020 2021 2022 2023 - Revised Code Billable/Specific Code Manifestation Code
    Applicable To
    • Dementia in other diseases classified elsewhere NOS
    • Major neurocognitive disorder in other diseases classified elsewhere NOS
    F02.80
    ,
    ICD-10-CM Diagnosis Code F02.A0

    Dementia in other diseases classified elsewhere, mild, without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Dementia in other diseases classified elsewhere, mild, NOS
    • Major neurocognitive disorder in other diseases classified elsewhere, mild, NOS
    F02.A0
    ,
    ICD-10-CM Diagnosis Code F02.B0

    Dementia in other diseases classified elsewhere, moderate, without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Dementia in other diseases classified elsewhere, moderate, NOS
    • Major neurocognitive disorder in other diseases classified elsewhere, moderate, NOS
    F02.B0
    ,
    ICD-10-CM Diagnosis Code F02.C0

    Dementia in other diseases classified elsewhere, severe, without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety

      2023 - New Code Billable/Specific Code Manifestation Code
    Applicable To
    • Dementia in other diseases classified elsewhere, severe, NOS
    • Major neurocognitive disorder in other diseases classified elsewhere, severe, NOS
    F02.C0
    )
  • mild neurocognitive disorder due to known physiological condition (
    ICD-10-CM Diagnosis Code F06.7

    Mild neurocognitive disorder due to known physiological condition

      2023 - New Code Non-Billable/Non-Specific Code
    Applicable To
    • Mild neurocognitive impairment due to a known physiological condition
    Code First
    • the underlying physiological condition, such as:
    • Alzheimer's disease (G30.-)
    • frontotemporal neurocognitive disorder (G31.09)
    • human immunodeficiency virus [HIV] disease (B20)
    • Huntington's disease (G10)
    • Neurocognitive disorder with Lewy bodies (G31.83)
    • Parkinson's disease (G20)
    • systemic lupus erythematosus (M32.-)
    • traumatic brain injury (S06.-)
    • vitamin B deficiency (E53-)
    Type 1 Excludes
    F06.7-
    )
Type 2 Excludes
Type 2 Excludes Help
A type 2 excludes note represents "not included here". A type 2 excludes note indicates that the condition excluded is not part of the condition it is excluded from but a patient may have both conditions at the same time. When a type 2 excludes note appears under a code it is acceptable to use both the code (G31) and the excluded code together.
  • Reye's syndrome (
    ICD-10-CM Diagnosis Code G93.7

    Reye's syndrome

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Pediatric Dx (0-17 years)
    Code First
    • poisoning due to salicylates, if applicable (T39.0-, with sixth character 1-4)
    Use Additional
    • code for adverse effect due to salicylates, if applicable (T39.0-, with sixth character 5)
    G93.7
    )
Codes
  • G31 Other degenerative diseases of nervous system, not elsewhere classified
    • G31.0 Frontotemporal dementia
      • G31.01 Pick's disease
      • G31.09 Other frontotemporal neurocognitive disorder
    • G31.1 Senile degeneration of brain, not elsewhere classified
    • G31.2 Degeneration of nervous system due to alcohol
    • G31.8 Other specified degenerative diseases of nervous system
      • G31.81 Alpers disease
      • G31.82 Leigh's disease
      • G31.83 Neurocognitive disorder with Lewy bodies
      • G31.84 Mild cognitive impairment of uncertain or unknown etiology
      • G31.85 Corticobasal degeneration
      • G31.89 Other specified degenerative diseases of nervous system
    • G31.9 Degenerative disease of nervous system, unspecified