2020 ICD-10-CM Diagnosis Code G31.01

Pick's disease

    2016 2017 2018 2019 2020 Billable/Specific Code
  • G31.01 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM G31.01 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of G31.01 - other international versions of ICD-10 G31.01 may differ.
Applicable To
  • Primary progressive aphasia
  • Progressive isolated aphasia
The following code(s) above G31.01 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G31.01:
  • G00-G99
    2020 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G31
    ICD-10-CM Diagnosis Code G31

    Other degenerative diseases of nervous system, not elsewhere classified

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 2 Excludes
    Use Additional
    Other degenerative diseases of nervous system, not elsewhere classified
Approximate Synonyms
  • Dementia due to pick's disease
  • Dementia due to picks disease
  • Dementia due to picks disease w behavioral disturbance
  • Dementia due to picks disease, with behavior changes
  • Pick's disease with altered behavior
  • Picks disease
Clinical Information
  • A progressive form of dementia characterized by the global loss of language abilities and initial preservation of other cognitive functions. Fluent and nonfluent subtypes have been described. Eventually a pattern of global cognitive dysfunction, similar to alzheimer disease, emerges. Pathologically, there are no alzheimer or pick disease like changes, however, spongiform changes of cortical layers ii and iii are present in the temporal lobe and frontal lobe. (from brain 1998 jan;121(pt 1):115-26)
  • A rare form of dementia that is sometimes familial. Clinical features include aphasia; apraxia; confusion; anomia; memory loss; and personality deterioration. This pattern is consistent with the pathologic findings of circumscribed atrophy of the poles of the frontal lobe and temporal lobe. Neuronal loss is maximal in the hippocampus, entorhinal cortex, and amygdala. Some ballooned cortical neurons contain argentophylic (pick) bodies. (from brain pathol 1998 apr;8(2):339-54; Adams et al., Principles of Neurology, 6th ed, pp1057-9)
  • A rare neurodegenerative disorder leading to dementia. It is characterized by frontotemporal lobar degeneration with accumulation of tau proteins which form pick bodies.
  • A rare neurologic progressive disorder characterized by impairment of the language and speech abilities.
ICD-10-CM G31.01 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 056 Degenerative nervous system disorders with mcc
  • 057 Degenerative nervous system disorders without mcc

Convert G31.01 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to G31.01:
  • Code First: F02
    ICD-10-CM Diagnosis Code F02

    Dementia in other diseases classified elsewhere

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Code First
    • the underlying physiological condition, such as:
    • Alzheimer's (G30.-)
    • cerebral lipidosis (E75.4)
    • Creutzfeldt-Jakob disease (A81.0-)
    • dementia with Lewy bodies (G31.83)
    • dementia with Parkinsonism (G31.83)
    • epilepsy and recurrent seizures (G40.-)
    • frontotemporal dementia (G31.09)
    • hepatolenticular degeneration (E83.0)
    • human immunodeficiency virus [HIV] disease (B20)
    • Huntington's disease (G10)
    • hypercalcemia (E83.52)
    • hypothyroidism, acquired (E00-E03.-)
    • intoxications (T36-T65)
    • Jakob-Creutzfeldt disease (A81.0-)
    • multiple sclerosis (G35)
    • neurosyphilis (A52.17)
    • niacin deficiency [pellagra] (E52)
    • Parkinson's disease (G20)
    • Pick's disease (G31.01)
    • polyarteritis nodosa (M30.0)
    • prion disease (A81.9)
    • systemic lupus erythematosus (M32.-)
    • traumatic brain injury (S06.-)
    • trypanosomiasis (B56.-, B57.-)
    • vitamin B deficiency (E53.8)
    Includes
    • Major neurocognitive disorder in other diseases classified elsewhere
    Type 2 Excludes
    • dementia in alcohol and psychoactive substance disorders (F10-F19, with .17, .27, .97)
    • vascular dementia (F01.5-)
  • Type 1 Excludes: R47.01
    ICD-10-CM Diagnosis Code R47.01

    Aphasia

      2016 2017 2018 2019 2020 Billable/Specific Code
    Type 1 Excludes
    • aphasia following cerebrovascular disease (I69. with final characters -20)
    • progressive isolated aphasia (G31.01)

Diagnosis Index entries containing back-references to G31.01:
  • Aphasia (amnestic) (global) (nominal) (semantic) (syntactic) R47.01
    ICD-10-CM Diagnosis Code R47.01

    Aphasia

      2016 2017 2018 2019 2020 Billable/Specific Code
    Type 1 Excludes
    • aphasia following cerebrovascular disease (I69. with final characters -20)
    • progressive isolated aphasia (G31.01)
  • Atrophy, atrophic (of)
    • brain (cortex) (progressive) G31.9
      ICD-10-CM Diagnosis Code G31.9

      Degenerative disease of nervous system, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code
  • Dementia (degenerative (primary)) (old age) (persisting) F03.90
    ICD-10-CM Diagnosis Code F03.90

    Unspecified dementia without behavioral disturbance

      2016 2017 2018 2019 2020 Billable/Specific Code Adult Dx (15-124 years)
    Applicable To
    • Dementia NOS
    • in (due to)
      • Pick's G31.01
        • with behavioral disturbance G31.01
  • Disease, diseased - see also Syndrome
    • Pick's G31.01
      • brain G31.01
        • with behavioral disturbance G31.01
      • with behavioral disturbance G31.01
  • Pick's

ICD-10-CM Codes Adjacent To G31.01
G25.89 Other specified extrapyramidal and movement disorders
G25.9 Extrapyramidal and movement disorder, unspecified
G26 Extrapyramidal and movement disorders in diseases classified elsewhere
G30 Alzheimer's disease
G30.0 Alzheimer's disease with early onset
G30.1 Alzheimer's disease with late onset
G30.8 Other Alzheimer's disease
G30.9 Alzheimer's disease, unspecified
G31 Other degenerative diseases of nervous system, not elsewhere classified
G31.0 Frontotemporal dementia
G31.01 Pick's disease
G31.09 Other frontotemporal dementia
G31.1 Senile degeneration of brain, not elsewhere classified
G31.2 Degeneration of nervous system due to alcohol
G31.8 Other specified degenerative diseases of nervous system
G31.81 Alpers disease
G31.82 Leigh's disease
G31.83 Dementia with Lewy bodies
G31.84 Mild cognitive impairment, so stated
G31.85 Corticobasal degeneration
G31.89 Other specified degenerative diseases of nervous system

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.