2019 ICD-10-CM Diagnosis Code G37.0

Diffuse sclerosis of central nervous system

    2016 2017 2018 2019 Billable/Specific Code
  • G37.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM G37.0 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of G37.0 - other international versions of ICD-10 G37.0 may differ.
Applicable To
  • Periaxial encephalitis
  • Schilder's disease
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as G37.0. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • X linked adrenoleukodystrophy (
    ICD-10-CM Diagnosis Code E71.52

    X-linked adrenoleukodystrophy

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    E71.52-
    )
The following code(s) above G37.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G37.0:
  • G00-G99
    2019 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
Approximate Synonyms
  • Schilder's disease
  • Schilders disease
Clinical Information
  • A rare central nervous system demyelinating condition affecting children and young adults. Pathologic findings include a large, sharply defined, asymmetric focus of myelin destruction that may involve an entire lobe or cerebral hemisphere. The clinical course tends to be progressive and includes dementia, cortical blindness, cortical deafness, spastic hemiplegia, and pseudobulbar palsy. Concentric sclerosis of balo is differentiated from diffuse cerebral sclerosis of schilder by the pathologic finding of alternating bands of destruction and preservation of myelin in concentric rings. Alpers' syndrome refers to a heterogeneous group of diseases that feature progressive cerebral deterioration and liver disease. (from Adams et al., Principles of Neurology, 6th ed, p914; dev neurosci 1991;13(4-5):267-73)
  • A rare congenital demyelinating disorder affecting the central nervous system. It is characterized by a demyelinating destructive lesion affecting an entire brain lobe or hemisphere. Signs and symptoms include dementia, cortical deafness and blindness, pseudobulbar palsy, and hemiplegia.
ICD-10-CM G37.0 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 058 Multiple sclerosis and cerebellar ataxia with mcc
  • 059 Multiple sclerosis and cerebellar ataxia with cc
  • 060 Multiple sclerosis and cerebellar ataxia without cc/mcc

Convert G37.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
Code annotations containing back-references to G37.0:
  • Type 1 Excludes: E71.3
    , E71.5
    ICD-10-CM Diagnosis Code E71.3

    Disorders of fatty-acid metabolism

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • peroxisomal disorders (E71.5)
    • Refsum's disease (G60.1)
    • Schilder's disease (G37.0)
    Type 2 Excludes
    • carnitine deficiency due to inborn error of metabolism (E71.42)
    ICD-10-CM Diagnosis Code E71.5

    Peroxisomal disorders

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • Schilder's disease (G37.0)

Diagnosis Index entries containing back-references to G37.0:
  • Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute) G04.90
    ICD-10-CM Diagnosis Code G04.90

    Encephalitis and encephalomyelitis, unspecified

      2016 2017 2018 2019 Billable/Specific Code
    Applicable To
    • Ventriculitis (cerebral) NOS
    • periaxial G37.0
  • Encephalopathy (acute) G93.40
    ICD-10-CM Diagnosis Code G93.40

    Encephalopathy, unspecified

      2016 2017 2018 2019 Billable/Specific Code
    • centrolobar progressive G37.0 (Schilder)
  • Flatau-Schilder disease G37.0
  • Schilder G37.0 (-Flatau)
  • Sclerosis, sclerotic
    • brain (generalized) (lobular) G37.9
      ICD-10-CM Diagnosis Code G37.9

      Demyelinating disease of central nervous system, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      • diffuse G37.0
    • diffuse G37.0 (brain) (spinal cord)

ICD-10-CM Codes Adjacent To G37.0
G32.8 Other specified degenerative disorders of nervous system in diseases classified elsewhere
G32.81 Cerebellar ataxia in diseases classified elsewhere
G32.89 Other specified degenerative disorders of nervous system in diseases classified elsewhere
G35 Multiple sclerosis
G36 Other acute disseminated demyelination
G36.0 Neuromyelitis optica [Devic]
G36.1 Acute and subacute hemorrhagic leukoencephalitis [Hurst]
G36.8 Other specified acute disseminated demyelination
G36.9 Acute disseminated demyelination, unspecified
G37 Other demyelinating diseases of central nervous system
G37.0 Diffuse sclerosis of central nervous system
G37.1 Central demyelination of corpus callosum
G37.2 Central pontine myelinolysis
G37.3 Acute transverse myelitis in demyelinating disease of central nervous system
G37.4 Subacute necrotizing myelitis of central nervous system
G37.5 Concentric sclerosis [Balo] of central nervous system
G37.8 Other specified demyelinating diseases of central nervous system
G37.9 Demyelinating disease of central nervous system, unspecified
G40 Epilepsy and recurrent seizures
G40.0 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset
G40.00 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.