ICD-10-CM Codes
G00-G99
G40-G47
G40-
2023 ICD-10-CM Diagnosis Code G40.3

2023 ICD-10-CM Diagnosis Code G40.3

Generalized idiopathic epilepsy and epileptic syndromes

2016

2017

2018

2019

2020

2021

2022

2023

Non-Billable/Non-Specific Code

G40.3 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
The 2023 edition of ICD-10-CM G40.3 became effective on October 1, 2022.
This is the American ICD-10-CM version of G40.3 - other international versions of ICD-10 G40.3 may differ.

Code Also

Code Also Help

A code also note instructs that 2 codes may be required to fully describe a condition but the sequencing of the two codes is discretionary, depending on the severity of the conditions and the reason for the encounter.

MERRF syndrome, if applicable (
ICD-10-CM Diagnosis Code E88.42
MERRF syndrome
Applicable To
- Myoclonic epilepsy associated with ragged-red fibers
Code Also
- progressive myoclonic epilepsy (G40.3-)
E88.42
)

The following code(s) above G40.3 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to G40.3:

G00-G99
2023 ICD-10-CM Range G00-G99
Diseases of the nervous system
Type 2 Excludes
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Diseases of the nervous system
G40
ICD-10-CM Diagnosis Code G40
Epilepsy and recurrent seizures
Note
- the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled
Type 1 Excludes
- conversion disorder with seizures (F44.5)
- convulsions NOS (R56.9)
- post traumatic seizures (R56.1)
- seizure (convulsive) NOS (R56.9)
- seizure of newborn (P90)
Type 2 Excludes
- hippocampal sclerosis (G93.81)
- mesial temporal sclerosis (G93.81)
- temporal sclerosis (G93.81)
- Todd's paralysis (G83.84)
Epilepsy and recurrent seizures

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change
2022 (effective 10/1/2021): No change
2023 (effective 10/1/2022): No change

Code annotations containing back-references to G40.3:

Code Also: E88.42

ICD-10-CM Diagnosis Code E88.42
MERRF syndrome
Applicable To
- Myoclonic epilepsy associated with ragged-red fibers
Code Also
- progressive myoclonic epilepsy (G40.3-)
Type 1 Excludes: P90
, P90

ICD-10-CM Diagnosis Code P90
Convulsions of newborn
Type 1 Excludes
- benign myoclonic epilepsy in infancy (G40.3-)
- benign neonatal convulsions (familial) (G40.3-)
ICD-10-CM Diagnosis Code P90
Convulsions of newborn
Type 1 Excludes
- benign myoclonic epilepsy in infancy (G40.3-)
- benign neonatal convulsions (familial) (G40.3-)

ICD-10-CM Codes Adjacent To G40.3

G40.11 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable

G40.111 …… with status epilepticus

G40.119 …… without status epilepticus

G40.2 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures

G40.20 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable

G40.201 …… with status epilepticus

G40.209 …… without status epilepticus

G40.21 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable

G40.211 …… with status epilepticus

G40.219 …… without status epilepticus

G40.3 Generalized idiopathic epilepsy and epileptic syndromes

G40.30 Generalized idiopathic epilepsy and epileptic syndromes, not intractable

G40.301 …… with status epilepticus

G40.309 …… without status epilepticus

G40.31 Generalized idiopathic epilepsy and epileptic syndromes, intractable

G40.311 …… with status epilepticus

G40.319 …… without status epilepticus

G40.A Absence epileptic syndrome

G40.A0 Absence epileptic syndrome, not intractable

G40.A01 …… with status epilepticus

G40.A09 …… without status epilepticus

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2023 ICD-10-CM Diagnosis Code G40.3

Generalized idiopathic epilepsy and epileptic syndromes

MERRF syndrome

Diseases of the nervous system

Epilepsy and recurrent seizures

MERRF syndrome

Convulsions of newborn

Convulsions of newborn