2023 ICD-10-CM Diagnosis Code G40.83

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Dravet syndrome

    2021 - New Code 2022 2023 Non-Billable/Non-Specific Code
  • G40.83 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2023 edition of ICD-10-CM G40.83 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of G40.83 - other international versions of ICD-10 G40.83 may differ.
Applicable To
  • Polymorphic epilepsy in infancy (PMEI)
  • Severe myoclonic epilepsy in infancy (SMEI)
The following code(s) above G40.83 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G40.83:
  • G00-G99
    2023 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G40
    ICD-10-CM Diagnosis Code G40

    Epilepsy and recurrent seizures

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    • the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled
    Type 1 Excludes
    • conversion disorder with seizures (F44.5)
    • convulsions NOS (R56.9)
    • post traumatic seizures (R56.1)
    • seizure (convulsive) NOS (R56.9)
    • seizure of newborn (P90)
    Type 2 Excludes
    Epilepsy and recurrent seizures
  • G40.8
    ICD-10-CM Diagnosis Code G40.8

    Other epilepsy and recurrent seizures

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Applicable To
    • Epilepsies and epileptic syndromes undetermined as to whether they are focal or generalized
    • Landau-Kleffner syndrome
    Other epilepsy and recurrent seizures
Code History
  • 2021 (effective 10/1/2020): New code
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change

Diagnosis Index entries containing back-references to G40.83:
  • Epilepsy, epileptic, epilepsia (attack) (cerebral) (convulsion) (fit) (seizure) G40.909
    ICD-10-CM Diagnosis Code G40.909

    Epilepsy, unspecified, not intractable, without status epilepticus

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Epilepsy NOS
    • Epileptic convulsions NOS
    • Epileptic fits NOS
    • Epileptic seizures NOS
    • Recurrent seizures NOS
    • Seizure disorder NOS
  • PMEI G40.83- (polymorphic epilepsy in infancy)
  • SMEI G40.83- (severe myoclonic epilepsy in infancy)

ICD-10-CM Codes Adjacent To G40.83
G40.81 Lennox-Gastaut syndrome
G40.811 …… not intractable, with status epilepticus
G40.812 …… not intractable, without status epilepticus
G40.813 …… intractable, with status epilepticus
G40.814 …… intractable, without status epilepticus
G40.82 Epileptic spasms
G40.821 …… not intractable, with status epilepticus
G40.822 …… not intractable, without status epilepticus
G40.823 …… intractable, with status epilepticus
G40.824 …… intractable, without status epilepticus
G40.83 Dravet syndrome
G40.833 …… intractable, with status epilepticus
G40.834 …… intractable, without status epilepticus
G40.89 Other seizures
G40.9 Epilepsy, unspecified
G40.90 Epilepsy, unspecified, not intractable
G40.901 …… with status epilepticus
G40.909 …… without status epilepticus
G40.91 Epilepsy, unspecified, intractable
G40.911 …… with status epilepticus
G40.919 …… without status epilepticus

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.