2020 ICD-10-CM Diagnosis Code G60.0

Hereditary motor and sensory neuropathy

    2016 2017 2018 2019 2020 Billable/Specific Code
  • G60.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM G60.0 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of G60.0 - other international versions of ICD-10 G60.0 may differ.
Applicable To
  • Charcot-Marie-Tooth disease
  • Déjérine-Sottas disease
  • Hereditary motor and sensory neuropathy, types I-IV
  • Hypertrophic neuropathy of infancy
  • Peroneal muscular atrophy (axonal type) (hypertrophic type)
  • Roussy-Levy syndrome
The following code(s) above G60.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G60.0:
  • G00-G99
    2020 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G60-G65
    2020 ICD-10-CM Range G60-G65

    Polyneuropathies and other disorders of the peripheral nervous system

    Type 1 Excludes
    Polyneuropathies and other disorders of the peripheral nervous system
Approximate Synonyms
  • Charcot marie tooth disease
  • Charcot marie tooth disease, type 1
  • Charcot marie tooth disease, type 2
  • Charcot marie tooth disease, type 3
  • Charcot marie tooth disease, type 4
  • Charcot-marie-tooth disease type 4
  • Charcot-marie-tooth disease, type i
  • Charcot-marie-tooth disease, type ii
  • Dejerine sottas disease
  • Dèjèrine-sottas disease
  • Hereditary motor and sensory neuropathy with optic atrophy
  • Neuropathy (nerve damage) hereditary motor and sensory
Clinical Information
  • A group of slowly progressive inherited disorders affecting motor and sensory peripheral nerves. Subtypes include hmsns i-vii. Hmsn i and ii both refer to charcot-marie-tooth disease. Hmsn iii refers to hypertrophic neuropathy of infancy. Hmsn iv refers to refsum disease. Hmsn v refers to a condition marked by a hereditary motor and sensory neuropathy associated with spastic paraplegia (see spastic paraplegia, hereditary). Hmsn vi refers to hmsn associated with an inherited optic atrophy (optic atrophies, hereditary), and hmsn vii refers to hmsn associated with retinitis pigmentosa. (from Adams et al., Principles of Neurology, 6th ed, p1343)
  • A hereditary motor and sensory neuropathy transmitted most often as an autosomal dominant trait and characterized by progressive distal wasting and loss of reflexes in the muscles of the legs (and occasionally involving the arms). Onset is usually in the second to fourth decade of life. This condition has been divided into two subtypes, hereditary motor and sensory neuropathy (hmsn) types i and ii. Hmsn i is associated with abnormal nerve conduction velocities and nerve hypertrophy, features not seen in hmsn ii. (Adams et al., Principles of Neurology, 6th ed, p1343)
  • A progressive hereditary disorder that causes nerve damage
  • An inherited degenerative disorder involving the peripheral nerves. It is caused by mutations in the genes that are responsible for the production of proteins necessary for the function and structure of the peripheral nerves. It is characterized by muscle atrophy and weakness in the feet, legs, hands, and arms and loss of sensation in the limbs.
  • Charcot-marie-tooth disease (cmt) is a group of genetic nerve disorders. It is named after the three doctors who first identified it. In the United States, cmt affects about 1 in 3,300 people. Cmt affects your peripheral nerves. Peripheral nerves carry movement and sensation signals between the brain and spinal cord and the rest of the body. Symptoms usually start around the teen years. Foot problems such as high arches or hammertoes can be early symptoms. As cmt progresses, your lower legs may weaken. Later, your hands may also become weak. There is no cure. The disease can be so mild you don't realize you have it or severe enough to make you weak. Many people with cmt lead active lives and have a normal life span. Physical therapy, occupational therapy, braces and other devices and sometimes surgery can help you cope. genetics home reference
  • Group of peripheral nervous system hereditary disorders with varying course, symptoms, neuropathology, and genetics, but generally involving gradual loss of nerve conduction, distal wasting, deformity, and disability.
ICD-10-CM G60.0 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 073 Cranial and peripheral nerve disorders with mcc
  • 074 Cranial and peripheral nerve disorders without mcc

Convert G60.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to G60.0:
  • Code First: M49
    ICD-10-CM Diagnosis Code M49

    Spondylopathies in diseases classified elsewhere

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Code First
    • underlying disease, such as:
    • brucellosis (A23.-)
    • Charcot-Marie-Tooth disease (G60.0)
    • enterobacterial infections (A01-A04)
    • osteitis fibrosa cystica (E21.0)
    Includes
    • curvature of spine in diseases classified elsewhere
    • deformity of spine in diseases classified elsewhere
    • kyphosis in diseases classified elsewhere
    • scoliosis in diseases classified elsewhere
    • spondylopathy in diseases classified elsewhere
    Type 1 Excludes
    • curvature of spine in tuberculosis [Pott's] (A18.01)
    • enteropathic arthropathies (M07.-)
    • gonococcal spondylitis (A54.41)
    • neuropathic [tabes dorsalis] spondylitis (A52.11)
    • neuropathic spondylopathy in syringomyelia (G95.0)
    • neuropathic spondylopathy in tabes dorsalis (A52.11)
    • nonsyphilitic neuropathic spondylopathy NEC (G98.0)
    • spondylitis in syphilis (acquired) (A52.77)
    • tuberculous spondylitis (A18.01)
    • typhoid fever spondylitis (A01.05)

Diagnosis Index entries containing back-references to G60.0:
  • Ataxia, ataxy, ataxic R27.0
    ICD-10-CM Diagnosis Code R27.0

    Ataxia, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    Type 1 Excludes
    • ataxia following cerebrovascular disease (I69. with final characters -93)
    • Roussy-Lévy G60.0
  • Atrophy, atrophic (of)
    • muscle, muscular (diffuse) (general) (idiopathic) (primary) M62.50
      ICD-10-CM Diagnosis Code M62.50

      Muscle wasting and atrophy, not elsewhere classified, unspecified site

        2016 2017 2018 2019 2020 Billable/Specific Code
      • neuropathic G60.0 (peroneal) (progressive)
      • peroneal G60.0
    • Charcot-Marie-Tooth G60.0
  • Charcot-Marie-Tooth disease, paralysis or syndrome G60.0
  • Curvature
  • Déjérine-Sottas disease or neuropathy G60.0 (hypertrophic)
  • Dystrophy, dystrophia
    • muscular G71.00
      ICD-10-CM Diagnosis Code G71.00

      Muscular dystrophy, unspecified

        2019 - New Code 2020 Billable/Specific Code
      • progressive (hereditary) G71.09
        ICD-10-CM Diagnosis Code G71.09

        Other specified muscular dystrophies

          2019 - New Code 2020 Billable/Specific Code
        Applicable To
        • Benign scapuloperoneal muscular dystrophy with early contractures [Emery-Dreifuss]
        • Congenital muscular dystrophy NOS
        • Congenital muscular dystrophy with specific morphological abnormalities of the muscle fiber
        • Distal muscular dystrophy
        • Limb-girdle muscular dystrophy
        • Ocular muscular dystrophy
        • Oculopharyngeal muscular dystrophy
        • Scapuloperoneal muscular dystrophy
        • Charcot-Marie G60.0 (-Tooth)
  • Marie-Charcot-Tooth neuropathic muscular atrophy G60.0
  • Neuritis (rheumatoid) M79.2
    ICD-10-CM Diagnosis Code M79.2

    Neuralgia and neuritis, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    Type 1 Excludes
    • Déjérine-Sottas G60.0
    • interstitial hypertrophic progressive G60.0
    • progressive hypertrophic interstitial G60.0
  • Neuropathy, neuropathic G62.9
    ICD-10-CM Diagnosis Code G62.9

    Polyneuropathy, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Neuropathy NOS
    • hereditary G60.9
      ICD-10-CM Diagnosis Code G60.9

      Hereditary and idiopathic neuropathy, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code
      • motor and sensory G60.0 (types I-IV)
    • hypertrophic G60.0
      • Charcot-Marie-Tooth G60.0
      • Déjérine-Sottas G60.0
      • interstitial progressive G60.0
      • of infancy G60.0
    • motor and sensory - see also Polyneuropathy
      • hereditary G60.0 (types I-IV)
    • progressive
      • hypertrophic interstitial G60.0
    • Déjérine-Sottas G60.0
  • Paralysis, paralytic (complete) (incomplete) G83.9
    ICD-10-CM Diagnosis Code G83.9

    Paralytic syndrome, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    • Charcot-Marie-Tooth type G60.0
  • Roussy-Lévy syndrome G60.0

ICD-10-CM Codes Adjacent To G60.0
G57.91 Unspecified mononeuropathy of right lower limb
G57.92 Unspecified mononeuropathy of left lower limb
G57.93 Unspecified mononeuropathy of bilateral lower limbs
G58 Other mononeuropathies
G58.0 Intercostal neuropathy
G58.7 Mononeuritis multiplex
G58.8 Other specified mononeuropathies
G58.9 Mononeuropathy, unspecified
G59 Mononeuropathy in diseases classified elsewhere
G60 Hereditary and idiopathic neuropathy
G60.0 Hereditary motor and sensory neuropathy
G60.1 Refsum's disease
G60.2 Neuropathy in association with hereditary ataxia
G60.3 Idiopathic progressive neuropathy
G60.8 Other hereditary and idiopathic neuropathies
G60.9 Hereditary and idiopathic neuropathy, unspecified
G61 Inflammatory polyneuropathy
G61.0 Guillain-Barre syndrome
G61.1 Serum neuropathy
G61.8 Other inflammatory polyneuropathies
G61.81 Chronic inflammatory demyelinating polyneuritis

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.