2023 ICD-10-CM Diagnosis Code G71.0

Muscular dystrophy

    2016 2017 2018 2019 - Converted to Parent Code 2020 2021 2022 2023 Non-Billable/Non-Specific Code
  • G71.0 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2023 edition of ICD-10-CM G71.0 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of G71.0 - other international versions of ICD-10 G71.0 may differ.
The following code(s) above G71.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G71.0:
  • G00-G99
    2023 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G71
    ICD-10-CM Diagnosis Code G71

    Primary disorders of muscles

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • arthrogryposis multiplex congenita (Q74.3)
    • metabolic disorders (E70-E88)
    • myositis (M60.-)
    Primary disorders of muscles
Approximate Synonyms
  • Becker muscular dystrophy
  • Distal muscular dystrophy
  • Duchenne muscular dystrophy
  • Emery-dreifuss muscular dystrophy
  • Erb's muscular dystrophy
  • Facioscapulohumeral muscular dystrophy
  • Hereditary progressive muscular dystrophy
  • Limb-girdle muscular dystrophy
  • Mitochondrial ocular myopathy
  • Muscular dystrophy, becker
  • Muscular dystrophy, distal
  • Muscular dystrophy, duchenne
  • Muscular dystrophy, emery dreifuss
  • Muscular dystrophy, erbs
  • Muscular dystrophy, facioscapulohumeral
  • Muscular dystrophy, hereditary progressive
  • Muscular dystrophy, limb girdle
  • Muscular dystrophy, neuropathic
  • Muscular dystrophy, ocular
  • Muscular dystrophy, oculopharyngeal
  • Neuropathic muscular dystrophy
  • Ocular muscular dystrophy
  • Oculopharyngeal muscular dystrophy
  • Restrictive lung disease due to muscular dystrophy
  • Restrictive lung mechanics due to muscular dystrophy
Clinical Information
  • A group of autosomal recessive and less frequently autosomal dominant muscular dystrophies affecting the muscles of the hips and shoulders.
  • A group of genetic degenerative muscle disorders affecting the muscles of the lower arms, hands, lower legs, and feet.
  • A group of inherited progressive muscle disorders characterized by muscle weakness and eventual death of the muscle tissues. Examples include duchenne muscular dystrophy, becker's muscular dystrophy, emery-dreifuss muscular dystrophy, facioscapulohumeral muscular dystrophy, and limb-girdle muscular dystrophy.
  • A heterogeneous group of genetic disorders characterized by progressive muscular atrophy and muscle weakness beginning in the hands, the legs, or the feet. Most are adult-onset autosomal dominant forms. Others are autosomal recessive.
  • A heterogeneous group of inherited myopathies, characterized by wasting and weakness of the skeletal muscle. They are categorized by the sites of muscle weakness; age of onset; and inheritance patterns.
  • A heterogenous group of inherited muscular dystrophy that can be autosomal dominant or autosomal recessive. There are many forms (called lgmds) involving genes encoding muscle membrane proteins such as the sarcoglycan (sarcoglycans) complex that interacts with dystrophin. The disease is characterized by progressing wasting and weakness of the proximal muscles of arms and legs around the hips and shoulders (the pelvic and shoulder girdles).
  • A progressive disorder involving pelvic and scapular girdle muscles marked by weakness of proximal muscles of hip and shoulder areas with variable psychiatric disorders and occasional mild mental retardation. Type ia (lgmd1a) synonym: proximal limb-girdle muscular dystrophy type 1a a slowly progressive form of muscular dystrophy affecting the proximal limb muscles but sparing the face. (159000) type ib (lgmd1b) synonym: proximal limb-girdle muscular dystrophy type 1b a slowly progressive form of muscular dystrophy differing from lgmd1a by the nasal quality of speech. (omim 159001) type 2 (lgmd2, lgmd2a) synonyms: leyden-mobius syndrome distal muscular dystrophy pelvofemoral muscular dystrophy pelvofemoral syndrome tibial muscular dystrophy muscular dystrophy involving first the pelvic or, less commonly, shoulder girdle with occasional pseudohypertrophy of the calves with onset usually in childhood but sometimes in later stages of life. Muscle wasting tends to be asymmetric when the upper limbs are first involved. Progression of disease varies with inability to walk usually taking place at about 20 to 30 years of onset. Facial weakness and contractures may occur later. (omim 253600) type 3 (lgmd3, lgmd2b) a slowly progressive form of muscular dystrophy involving the pelvic girdle with onset in the late teens. (omim 253601)
  • An autosomal dominant degenerative muscle disease characterized by slowly progressive weakness of the muscles of the face, upper-arm, and shoulder girdle. The onset of symptoms usually occurs in the first or second decade of life. Affected individuals usually present with impairment of upper extremity elevation. This tends to be followed by facial weakness, primarily involving the orbicularis oris and orbicularis oculi muscles. (neuromuscul disord 1997;7(1):55-62; Adams et al., Principles of Neurology, 6th ed, p1420)
  • An autosomal dominant disorder affecting the skeletal muscles of the face, scapula, and upper arm. Patients present with muscle weakness in these anatomic areas. The muscle weakness eventually spreads to other skeletal muscles as well.
  • An autosomal dominant hereditary disease that presents in late in life and is characterized by dysphagia and progressive ptosis of the eyelids. Mutations in the gene for poly(a)-binding protein ii have been associated with oculopharyngeal muscular dystrophy.
  • An autosomal dominant inherited disorder caused by mutations in the pabpn1 gene. It is characterized by late-onset eyelid ptosis and dysphagia. Patients have a positive family history involving at least two generations.
  • An inherited disease where skeletal muscles are progressively weakened and wasted.
  • An x-linked inherited disorder characterized by slowly progressing weakness in the muscles of the legs and pelvis.
  • General term for a group of inherited disorders which are characterized by progressive degeneration of skeletal muscles.
  • Muscular dystrophy (md) refers to a group of more than 30 inherited diseases that cause muscle weakness and muscle loss. Some forms of md appear in infancy or childhood, while others may not appear until middle age or later. The different muscular dystrophies vary in who they affect and the symptoms. All forms of md grow worse as the person's muscles get weaker. Most people with md eventually lose the ability to walk. There is no cure for muscular dystrophy. Treatments include physical and speech therapy, orthopedic devices, surgery and medications. Some people with muscular dystrophy have mild cases that worsen slowly. Other cases are disabling and severe.
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): Deleted code
  • 2019 (effective 10/1/2018): New code
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change
Code annotations containing back-references to G71.0:
  • Code First: Z99.3
    ICD-10-CM Diagnosis Code Z99.3

    Dependence on wheelchair

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    • Wheelchair confinement status
    Code First
    • cause of dependence, such as:
    • muscular dystrophy (G71.0-)
    • obesity (E66.-)
ICD-10-CM Codes Adjacent To G71.0
G70.00 …… without (acute) exacerbation
G70.01 …… with (acute) exacerbation
G70.1 Toxic myoneural disorders
G70.2 Congenital and developmental myasthenia
G70.8 Other specified myoneural disorders
G70.80 Lambert-Eaton syndrome, unspecified
G70.81 Lambert-Eaton syndrome in disease classified elsewhere
G70.89 Other specified myoneural disorders
G70.9 Myoneural disorder, unspecified
G71 Primary disorders of muscles
G71.0 Muscular dystrophy
G71.00 …… unspecified
G71.01 Duchenne or Becker muscular dystrophy
G71.02 Facioscapulohumeral muscular dystrophy
G71.03 Limb girdle muscular dystrophies
G71.031 Autosomal dominant limb girdle muscular dystrophy
G71.032 Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
G71.033 Limb girdle muscular dystrophy due to dysferlin dysfunction
G71.034 Limb girdle muscular dystrophy due to sarcoglycan dysfunction
G71.0340 …… unspecified
G71.0341 Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.