1. ICD-10-CM Codes
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2. G00-G99
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3. G70-G73
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4. G71-
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5. 2023 ICD-10-CM Diagnosis Code G71.11

2023 ICD-10-CM Diagnosis Code G71.11

Myotonic muscular dystrophy

2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

• G71.11 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
• The 2023 edition of ICD-10-CM G71.11 became effective on October 1, 2022.
• This is the American ICD-10-CM version of G71.11 - other international versions of ICD-10 G71.11 may differ.

• Myotonic dystrophy
• Steinert myotonic dystrophy syndrome

• An autosomal dominant neuromuscular disorder which usually presents in early adulthood, characterized by progressive muscular atrophy (most frequently involving the hands, forearms, and face), myotonia, frontal baldness, lenticular opacities, and testicular atrophy. Cardiac conduction abnormalities, diaphragmatic weakness, and mild intellectual disability may also occur. Congenital myotonic dystrophy is a severe form of this disorder, characterized by neonatal muscle hypotonia, feeding difficulties, respiratory muscle weakness, and an increased incidence of intellectual disability. (from Adams et al., Principles of Neurology, 6th ed, pp1423-5; Joynt, Clinical Neurology, 1997, ch16, pp16-7)
• An inherited progressive disorder affecting the muscles. It is characterized by muscle wasting and hypotonia, cataracts, heart conduction defects and endocrinopathies.
• Autosomal dominant neuromuscular disorder which usually presents in early adulthood, characterized by progressive muscular atrophy (most frequently involving the hands, forearms, and face), myotonia, frontal baldness, lenticular opacities, and testicular atrophy; cardiac conduction abnormalities, diaphragmatic weakness, and mild mental retardation may also occur; congenital myotonic dystrophy is a severe form of this disorder.

• 091 Other disorders of nervous system with mcc
• 092 Other disorders of nervous system with cc
• 093 Other disorders of nervous system without cc/mcc

Convert G71.11 to ICD-9-CM

• 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
• 2017 (effective 10/1/2016): No change
• 2018 (effective 10/1/2017): No change
• 2019 (effective 10/1/2018): No change
• 2020 (effective 10/1/2019): No change
• 2021 (effective 10/1/2020): No change
• 2022 (effective 10/1/2021): No change
• 2023 (effective 10/1/2022): No change

• Type 1 Excludes: E31
  ICD-10-CM Diagnosis Code E31

  Polyglandular dysfunction

  2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code

  Type 1 Excludes

  • ataxia telangiectasia [Louis-Bar] (G11.3)
  • dystrophia myotonica [Steinert] (G71.11)
  • pseudohypoparathyroidism (E20.1)

• Atrophy, atrophic (of)
  • muscle, muscular (diffuse) (general) (idiopathic) (primary) M62.50
    ICD-10-CM Diagnosis Code M62.50

    Muscle wasting and atrophy, not elsewhere classified, unspecified site

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • myotonic G71.11
  • myotonia G71.11
• Batten-Steinert syndrome G71.11
• Cardiomyopathy (familial) (idiopathic) I42.9
  ICD-10-CM Diagnosis Code I42.9

  Cardiomyopathy, unspecified

  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

  Applicable To

  • Cardiomyopathy (primary) (secondary) NOS
  • due to
    • myotonia atrophica G71.11
• Curschmann G71.11 (-Batten) (-Steinert)
• Disease, diseased - see also Syndrome
  • Batten-Steinert G71.11
  • Curschmann G71.11
  • Steinert's G71.11
• Dystrophy, dystrophia
  • muscular G71.00
    ICD-10-CM Diagnosis Code G71.00

    Muscular dystrophy, unspecified

    2019 - New Code 2020 2021 2022 2023 Billable/Specific Code
    • congenital (hereditary) (progressive) (with specific morphological abnormalities of the muscle fiber) G71.09
      ICD-10-CM Diagnosis Code G71.09

      Other specified muscular dystrophies

      2019 - New Code 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Benign scapuloperoneal muscular dystrophy with early contractures [Emery-Dreifuss]
      • Congenital muscular dystrophy NOS
      • Congenital muscular dystrophy with specific morphological abnormalities of the muscle fiber
      • Distal muscular dystrophy
      • Ocular muscular dystrophy
      • Oculopharyngeal muscular dystrophy
      • Scapuloperoneal muscular dystrophy
      • myotonic G71.11
    • myotonic G71.11
  • myotonic, myotonica G71.11
• Myocardiopathy (congestive) (constrictive) (familial) (hypertrophic nonobstructive) (idiopathic) (infiltrative) (obstructive) (primary) (restrictive) (sporadic) I42.9
  - see also Cardiomyopathy
  ICD-10-CM Diagnosis Code I42.9

  Cardiomyopathy, unspecified

  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

  Applicable To

  • Cardiomyopathy (primary) (secondary) NOS
  • in (due to)
    • myotonia atrophica G71.11
• Myopathy G72.9
  ICD-10-CM Diagnosis Code G72.9

  Myopathy, unspecified

  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • mytonic, proximal G71.11 (PROMM)
  • proximal myotonic G71.11 (PROMM)
• Myotonia (acquisita) (intermittens) M62.89
  ICD-10-CM Diagnosis Code M62.89

  Other specified disorders of muscle

  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

  Applicable To

  • Muscle (sheath) hernia
  • atrophica G71.11
  • dystrophica G71.11
• Steinert's disease G71.11
• Syndrome - see also Disease
  • Batten-Steinert G71.11
  • Curschmann G71.11 (-Batten) (-Steinert)

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.