2019 ICD-10-CM Diagnosis Code G71.11

Myotonic muscular dystrophy

    2016 2017 2018 2019 Billable/Specific Code
  • G71.11 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM G71.11 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of G71.11 - other international versions of ICD-10 G71.11 may differ.
Applicable To
  • Dystrophia myotonica [Steinert]
  • Myotonia atrophica
  • Myotonic dystrophy
  • Proximal myotonic myopathy (PROMM)
  • Steinert disease
The following code(s) above G71.11 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G71.11:
  • G00-G99
    2019 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G71
    ICD-10-CM Diagnosis Code G71

    Primary disorders of muscles

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • arthrogryposis multiplex congenita (Q74.3)
    • metabolic disorders (E70-E88)
    • myositis (M60.-)
    Primary disorders of muscles
Approximate Synonyms
  • Myotonic dystrophy
  • Steinert myotonic dystrophy syndrome
Clinical Information
  • An autosomal dominant neuromuscular disorder which usually presents in early adulthood, characterized by progressive muscular atrophy (most frequently involving the hands, forearms, and face), myotonia, frontal baldness, lenticular opacities, and testicular atrophy. Cardiac conduction abnormalities, diaphragmatic weakness, and mild intellectual disability may also occur. Congenital myotonic dystrophy is a severe form of this disorder, characterized by neonatal muscle hypotonia, feeding difficulties, respiratory muscle weakness, and an increased incidence of intellectual disability. (from Adams et al., Principles of Neurology, 6th ed, pp1423-5; Joynt, Clinical Neurology, 1997, ch16, pp16-7)
  • An inherited progressive disorder affecting the muscles. It is characterized by muscle wasting and hypotonia, cataracts, heart conduction defects and endocrinopathies.
  • Autosomal dominant neuromuscular disorder which usually presents in early adulthood, characterized by progressive muscular atrophy (most frequently involving the hands, forearms, and face), myotonia, frontal baldness, lenticular opacities, and testicular atrophy; cardiac conduction abnormalities, diaphragmatic weakness, and mild mental retardation may also occur; congenital myotonic dystrophy is a severe form of this disorder.
ICD-10-CM G71.11 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 091 Other disorders of nervous system with mcc
  • 092 Other disorders of nervous system with cc
  • 093 Other disorders of nervous system without cc/mcc

Convert G71.11 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
Code annotations containing back-references to G71.11:
  • Type 1 Excludes: E31
    ICD-10-CM Diagnosis Code E31

    Polyglandular dysfunction

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • ataxia telangiectasia [Louis-Bar] (G11.3)
    • dystrophia myotonica [Steinert] (G71.11)
    • pseudohypoparathyroidism (E20.1)

Diagnosis Index entries containing back-references to G71.11:
  • Atrophy, atrophic (of)
    • muscle, muscular (diffuse) (general) (idiopathic) (primary) M62.50
      ICD-10-CM Diagnosis Code M62.50

      Muscle wasting and atrophy, not elsewhere classified, unspecified site

        2016 2017 2018 2019 Billable/Specific Code
      • myotonic G71.11
    • myotonia G71.11
  • Batten-Steinert syndrome G71.11
  • Cardiomyopathy (familial) (idiopathic) I42.9
    ICD-10-CM Diagnosis Code I42.9

    Cardiomyopathy, unspecified

      2016 2017 2018 2019 Billable/Specific Code
    Applicable To
    • Cardiomyopathy (primary) (secondary) NOS
    • due to
      • myotonia atrophica G71.11
  • Curschmann G71.11 (-Batten) (-Steinert)
  • Disease, diseased - see also Syndrome
    • Batten-Steinert G71.11
    • Curschmann G71.11
    • Steinert's G71.11
  • Dystrophy, dystrophia
    • muscular G71.00
      ICD-10-CM Diagnosis Code G71.00

      Muscular dystrophy, unspecified

        2019 - New Code Billable/Specific Code
      • congenital (hereditary) (progressive) (with specific morphological abnormalities of the muscle fiber) G71.09
        ICD-10-CM Diagnosis Code G71.09

        Other specified muscular dystrophies

          2019 - New Code Billable/Specific Code
        Applicable To
        • Benign scapuloperoneal muscular dystrophy with early contractures [Emery-Dreifuss]
        • Congenital muscular dystrophy NOS
        • Congenital muscular dystrophy with specific morphological abnormalities of the muscle fiber
        • Distal muscular dystrophy
        • Limb-girdle muscular dystrophy
        • Ocular muscular dystrophy
        • Oculopharyngeal muscular dystrophy
        • Scapuloperoneal muscular dystrophy
        • myotonic G71.11
      • myotonic G71.11
    • myotonic, myotonica G71.11
  • Myocardiopathy (congestive) (constrictive) (familial) (hypertrophic nonobstructive) (idiopathic) (infiltrative) (obstructive) (primary) (restrictive) (sporadic) I42.9
    - see also Cardiomyopathy
    ICD-10-CM Diagnosis Code I42.9

    Cardiomyopathy, unspecified

      2016 2017 2018 2019 Billable/Specific Code
    Applicable To
    • Cardiomyopathy (primary) (secondary) NOS
    • in (due to)
      • myotonia atrophica G71.11
  • Myopathy G72.9
    ICD-10-CM Diagnosis Code G72.9

    Myopathy, unspecified

      2016 2017 2018 2019 Billable/Specific Code
    • mytonic, proximal G71.11 (PROMM)
    • proximal myotonic G71.11 (PROMM)
  • Myotonia (acquisita) (intermittens) M62.89
    ICD-10-CM Diagnosis Code M62.89

    Other specified disorders of muscle

      2016 2017 2018 2019 Billable/Specific Code
    Applicable To
    • Muscle (sheath) hernia
    • atrophica G71.11
    • dystrophica G71.11
  • Steinert's disease G71.11
  • Syndrome - see also Disease
    • Batten-Steinert G71.11
    • Curschmann G71.11 (-Batten) (-Steinert)

ICD-10-CM Codes Adjacent To G71.11
G70.81 Lambert-Eaton syndrome in disease classified elsewhere
G70.89 Other specified myoneural disorders
G70.9 Myoneural disorder, unspecified
G71 Primary disorders of muscles
G71.0 Muscular dystrophy
G71.00 …… unspecified
G71.01 Duchenne or Becker muscular dystrophy
G71.02 Facioscapulohumeral muscular dystrophy
G71.09 Other specified muscular dystrophies
G71.1 Myotonic disorders
G71.11 Myotonic muscular dystrophy
G71.12 Myotonia congenita
G71.13 Myotonic chondrodystrophy
G71.14 Drug induced myotonia
G71.19 Other specified myotonic disorders
G71.2 Congenital myopathies
G71.3 Mitochondrial myopathy, not elsewhere classified
G71.8 Other primary disorders of muscles
G71.9 Primary disorder of muscle, unspecified
G72 Other and unspecified myopathies
G72.0 Drug-induced myopathy

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.