2022 ICD-10-CM Diagnosis Code G71.19

Other specified myotonic disorders

    2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
  • G71.19 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2022 edition of ICD-10-CM G71.19 became effective on October 1, 2021.
  • This is the American ICD-10-CM version of G71.19 - other international versions of ICD-10 G71.19 may differ.
Applicable To
  • Myotonia fluctuans
  • Myotonia permanens
  • Neuromyotonia [Isaacs]
  • Paramyotonia congenita (of von Eulenburg)
  • Pseudomyotonia
  • Symptomatic myotonia
The following code(s) above G71.19 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G71.19:
  • G00-G99
    2022 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G71
    ICD-10-CM Diagnosis Code G71

    Primary disorders of muscles

      2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • arthrogryposis multiplex congenita (Q74.3)
    • metabolic disorders (E70-E88)
    • myositis (M60.-)
    Primary disorders of muscles
Approximate Synonyms
  • Bilateral myotonic cataract
  • Left myotonic cataract
  • Myotonic cataract
  • Myotonic disorder
  • Paramyotonia congenita
  • Right myotonic cataract
Clinical Information
  • A rare neuromuscular disorder with onset usually in late childhood or early adulthood, characterized by intermittent or continuous widespread involuntary muscle contractions; fasciculation; hyporeflexia; muscle cramp; muscle weakness; hyperhidrosis; tachycardia; and myokymia. Involvement of pharyngeal or laryngeal muscles may interfere with speech and breathing. The continuous motor activity persists during sleep and general anesthesia (distinguishing this condition from stiff-person syndrome). Familial and acquired (primarily autoimmune) forms have been reported. (from ann ny acad sci 1998 may 13;841:482-496; Adams et al., Principles of Neurology, 6th ed, p1491)
ICD-10-CM G71.19 is grouped within Diagnostic Related Group(s) (MS-DRG v39.0):
  • 091 Other disorders of nervous system with mcc
  • 092 Other disorders of nervous system with cc
  • 093 Other disorders of nervous system without cc/mcc

Convert G71.19 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
Code annotations containing back-references to G71.19:
  • Type 1 Excludes: G72.3
    ICD-10-CM Diagnosis Code G72.3

    Periodic paralysis

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
    Applicable To
    • Familial periodic paralysis
    • Hyperkalemic periodic paralysis (familial)
    • Hypokalemic periodic paralysis (familial)
    • Myotonic periodic paralysis (familial)
    • Normokalemic paralysis (familial)
    • Potassium sensitive periodic paralysis
    Type 1 Excludes
    • paramyotonia congenita (of von Eulenburg) (G71.19)

Diagnosis Index entries containing back-references to G71.19:
  • Cataract (cortical) (immature) (incipient) H26.9
    ICD-10-CM Diagnosis Code H26.9

    Unspecified cataract

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
    • associated with
      • myotonic disorders G71.19
    • in (due to)
      • myotonic disorders G71.19
    • myotonic G71.19
  • Disease, diseased - see also Syndrome
    • Eulenburg's G71.19 (congenital paramyotonia)
    • von Eulenburg's G71.19 (congenital paramyotonia)
  • Disorder (of) - see also Disease
    • myotonic NEC G71.19
  • Eulenburg's disease G71.19 (congenital paramyotonia)
  • Myotonia (acquisita) (intermittens) M62.89
    ICD-10-CM Diagnosis Code M62.89

    Other specified disorders of muscle

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
    Applicable To
    • Muscle (sheath) hernia
    • fluctuans G71.19
    • permanens G71.19
    • symptomatic G71.19
  • Neuromyotonia G71.19 (Isaacs)
  • Paramyotonia G71.19 (congenita)
  • Pseudomyotonia G71.19
  • Von Eulenburg's disease G71.19

ICD-10-CM Codes Adjacent To G71.19
G71.0 Muscular dystrophy
G71.00 …… unspecified
G71.01 Duchenne or Becker muscular dystrophy
G71.02 Facioscapulohumeral muscular dystrophy
G71.09 Other specified muscular dystrophies
G71.1 Myotonic disorders
G71.11 Myotonic muscular dystrophy
G71.12 Myotonia congenita
G71.13 Myotonic chondrodystrophy
G71.14 Drug induced myotonia
G71.19 Other specified myotonic disorders
G71.2 Congenital myopathies
G71.20 Congenital myopathy, unspecified
G71.21 Nemaline myopathy
G71.22 Centronuclear myopathy
G71.220 X-linked myotubular myopathy
G71.228 Other centronuclear myopathy
G71.29 Other congenital myopathy
G71.3 Mitochondrial myopathy, not elsewhere classified
G71.8 Other primary disorders of muscles
G71.9 Primary disorder of muscle, unspecified

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.