2021 ICD-10-CM Diagnosis Code G71.2

Congenital myopathies

    2016 2017 2018 2019 2020 2021 - Deleted Code Non-Billable/Non-Specific Code
  • G71.2 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2021 edition of ICD-10-CM G71.2 became effective on October 1, 2020.
  • This is the American ICD-10-CM version of G71.2 - other international versions of ICD-10 G71.2 may differ.
Type 2 Excludes
Type 2 Excludes Help
A type 2 excludes note represents "not included here". A type 2 excludes note indicates that the condition excluded is not part of the condition it is excluded from but a patient may have both conditions at the same time. When a type 2 excludes note appears under a code it is acceptable to use both the code (G71.2) and the excluded code together.
  • arthrogryposis multiplex congenita (
    ICD-10-CM Diagnosis Code Q74.3

    Arthrogryposis multiplex congenita

      2016 2017 2018 2019 2020 2021 Billable/Specific Code POA Exempt
    Q74.3
    )
The following code(s) above G71.2 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G71.2:
  • G00-G99
    2021 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G71
    ICD-10-CM Diagnosis Code G71

    Primary disorders of muscles

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • arthrogryposis multiplex congenita (Q74.3)
    • metabolic disorders (E70-E88)
    • myositis (M60.-)
    Primary disorders of muscles
Approximate Synonyms
  • Congenital anomaly of skeletal muscle
  • Congenital hereditary muscular dystrophy
  • Muscular dystrophy, congenital hereditary
  • Myopathy, congenital
  • Myopathy, myotubular
  • Myotubular myopathy
  • Walker warburg congenital muscular dystrophy
Clinical Information
  • A group of inherited congenital myopathic conditions characterized clinically by weakness, hypotonia, and prominent hypoplasia of proximal muscles including the face. Muscle biopsy reveals large numbers of rod-shaped structures beneath the muscle fiber plasma membrane. This disorder is genetically heterogeneous and may occasionally present in adults. (Adams et al., Principles of Neurology, 6th ed, p1453)
  • An autosomal dominant congenital disorder affecting the skeletal muscles. Microscopically, it is characterized by disorganized areas, which are called cores, seen usually in the center of the muscle fibers. Clinically it presents as mild to severe muscle weakness. It may be associated with skeletal abnormalities including scoliosis, joint deformities, and hip dislocation.
  • An inherited congenital myopathic condition characterized by weakness and hypotonia in infancy and delayed motor development. Muscle biopsy reveals a condensation of myofibrils and myofibrillar material in the central portion of each muscle fiber. (Adams et al., Principles of Neurology, 6th ed, p1452)
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): Deleted code
ICD-10-CM Codes Adjacent To G71.2
G71.00 …… unspecified
G71.01 Duchenne or Becker muscular dystrophy
G71.02 Facioscapulohumeral muscular dystrophy
G71.09 Other specified muscular dystrophies
G71.1 Myotonic disorders
G71.11 Myotonic muscular dystrophy
G71.12 Myotonia congenita
G71.13 Myotonic chondrodystrophy
G71.14 Drug induced myotonia
G71.19 Other specified myotonic disorders
G71.2 Congenital myopathies
G71.20 Congenital myopathy, unspecifed
G71.21 Nemaline myopathy
G71.22 Centronuclear myopathy
G71.220 X-linked myotubular myopathy
G71.228 Other centronuclear myopathy
G71.29 Other congenital myopathy
G71.3 Mitochondrial myopathy, not elsewhere classified
G71.8 Other primary disorders of muscles
G71.9 Primary disorder of muscle, unspecified
G72 Other and unspecified myopathies

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.