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ICD-10-CM Codes
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G00-G99
Diseases of the nervous system
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G70-G73
Diseases of myoneural junction and muscle
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G71-
Primary disorders of muscles
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2022 ICD-10-CM Diagnosis Code G71.3
2022 ICD-10-CM Diagnosis Code G71.3
Mitochondrial myopathy, not elsewhere classified
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
- G71.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
- The 2022 edition of ICD-10-CM G71.3 became effective on October 1, 2021.
- This is the American ICD-10-CM version of G71.3 - other international versions of ICD-10 G71.3 may differ.
Type 1 ExcludesType 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as G71.3. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- Kearns-Sayre syndrome (
ICD-10-CM Diagnosis Code H49.81
Kearns-Sayre syndrome
2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
Applicable To- Progressive external ophthalmoplegia with pigmentary retinopathy
Use Additional- code for other manifestation, such as:
- heart block (I45.9)
H49.81) - Leber's disease (
ICD-10-CM Diagnosis Code H47.21
Primary optic atrophy
2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
H47.21) - Leigh's encephalopathy (
ICD-10-CM Diagnosis Code G31.82
Leigh's disease
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
Applicable To- Subacute necrotizing encephalopathy
G31.82) - mitochondrial metabolism disorders (
ICD-10-CM Diagnosis Code E88.4
Mitochondrial metabolism disorders
2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
Type 1 Excludes- disorders of pyruvate metabolism (E74.4)
- Kearns-Sayre syndrome (H49.81)
- Leber's disease (H47.22)
- Leigh's encephalopathy (G31.82)
- Mitochondrial myopathy, NEC (G71.3)
- Reye's syndrome (G93.7)
E88.4.-) - Reye's syndrome (
ICD-10-CM Diagnosis Code G93.7
Reye's syndrome
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code Pediatric Dx (0-17 years)
Code First- poisoning due to salicylates, if applicable (T39.0-, with sixth character 1-4)
Use Additional- code for adverse effect due to salicylates, if applicable (T39.0-, with sixth character 5)
G93.7)
The following code(s) above
G71.3 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
- Applicable To annotations, or
- Code Also annotations, or
- Code First annotations, or
- Excludes1 annotations, or
- Excludes2 annotations, or
- Includes annotations, or
- Note annotations, or
- Use Additional annotations
that may be applicable to
G71.3:
Approximate Synonyms
- Mitochondrial myopathy
- Mitochondrial ocular myopathy
- Myopathy, mitochondrial
ICD-10-CM G71.3 is grouped within Diagnostic Related Group(s) (MS-DRG v39.0):
- 091 Other disorders of nervous system with mcc
- 092 Other disorders of nervous system with cc
- 093 Other disorders of nervous system without cc/mcc
Convert G71.3 to ICD-9-CM
Code History
- 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
- 2017 (effective 10/1/2016): No change
- 2018 (effective 10/1/2017): No change
- 2019 (effective 10/1/2018): No change
- 2020 (effective 10/1/2019): No change
- 2021 (effective 10/1/2020): No change
- 2022 (effective 10/1/2021): No change
Code annotations containing back-references to G71.3:
- Myopathy G72.9
ICD-10-CM Diagnosis Code G72.9
Myopathy, unspecified
2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
ICD-10-CM Codes Adjacent To G71.3
G71.13 Myotonic chondrodystrophy
G71.19 Other specified myotonic disorders
G71.2 Congenital myopathies
G71.20 Congenital myopathy, unspecified
G71.220 X-linked myotubular myopathy
G71.228 Other centronuclear myopathy
G71.29 Other congenital myopathy
G71.3
Mitochondrial myopathy, not elsewhere classified
G71.8 Other primary disorders of muscles
G71.9 Primary disorder of muscle, unspecified
G72 Other and unspecified myopathies
G72.0 Drug-induced myopathy
G72.2 Myopathy due to other toxic agents
G72.4 Inflammatory and immune myopathies, not elsewhere classified
G72.41 Inclusion body myositis [IBM]
G72.49 Other inflammatory and immune myopathies, not elsewhere classified
Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.