2019

  1. ICD-10-CM Codes
    2. ›
  2. G00-G99 Diseases of the nervous system
    3. ›
  3. G70-G73 Diseases of myoneural junction and muscle
    4. ›
  4. G71- Primary disorders of muscles
    5. ›

2019 ICD-10-CM Diagnosis Code G71.3

Mitochondrial myopathy, not elsewhere classified

    2016 2017 2018 2019 Billable/Specific Code
  • G71.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM G71.3 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of G71.3 - other international versions of ICD-10 G71.3 may differ.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as G71.3. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Kearns-Sayre syndrome (
    ICD-10-CM Diagnosis Code H49.81

    Kearns-Sayre syndrome

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Applicable To
    • Progressive external ophthalmoplegia with pigmentary retinopathy
    Use Additional
    • code for other manifestation, such as:
    • heart block (I45.9)
    H49.81
    )
  • Leber's disease (
    ICD-10-CM Diagnosis Code H47.21

    Primary optic atrophy

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    H47.21
    )
  • Leigh's encephalopathy (
    ICD-10-CM Diagnosis Code G31.82

    Leigh's disease

      2016 2017 2018 2019 Billable/Specific Code
    Applicable To
    • Subacute necrotizing encephalopathy
    G31.82
    )
  • mitochondrial metabolism disorders (
    ICD-10-CM Diagnosis Code E88.4

    Mitochondrial metabolism disorders

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • disorders of pyruvate metabolism (E74.4)
    • Kearns-Sayre syndrome (H49.81)
    • Leber's disease (H47.22)
    • Leigh's encephalopathy (G31.82)
    • Mitochondrial myopathy, NEC (G71.3)
    • Reye's syndrome (G93.7)
    E88.4.-
    )
  • Reye's syndrome (
    ICD-10-CM Diagnosis Code G93.7

    Reye's syndrome

      2016 2017 2018 2019 Billable/Specific Code Pediatric Dx (0-17 years)
    Code First
    • poisoning due to salicylates, if applicable (T39.0-, with sixth character 1-4)
    Use Additional
    • code for adverse effect due to salicylates, if applicable (T39.0-, with sixth character 5)
    G93.7
    )
The following code(s) above G71.3 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G71.3:
  • G00-G99
    2019 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G71
    ICD-10-CM Diagnosis Code G71

    Primary disorders of muscles

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • arthrogryposis multiplex congenita (Q74.3)
    • metabolic disorders (E70-E88)
    • myositis (M60.-)
    Primary disorders of muscles
Approximate Synonyms
  • Mitochondrial myopathy
  • Mitochondrial ocular myopathy
  • Myopathy, mitochondrial
ICD-10-CM G71.3 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 091 Other disorders of nervous system with mcc
  • 092 Other disorders of nervous system with cc
  • 093 Other disorders of nervous system without cc/mcc

Convert G71.3 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
Code annotations containing back-references to G71.3:
  • Type 1 Excludes: E88.4
    ICD-10-CM Diagnosis Code E88.4

    Mitochondrial metabolism disorders

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • disorders of pyruvate metabolism (E74.4)
    • Kearns-Sayre syndrome (H49.81)
    • Leber's disease (H47.22)
    • Leigh's encephalopathy (G31.82)
    • Mitochondrial myopathy, NEC (G71.3)
    • Reye's syndrome (G93.7)

Diagnosis Index entries containing back-references to G71.3:
  • Myopathy G72.9
    ICD-10-CM Diagnosis Code G72.9

    Myopathy, unspecified

      2016 2017 2018 2019 Billable/Specific Code
    • mitochondrial NEC G71.3

ICD-10-CM Codes Adjacent To G71.3
G71.01 Duchenne or Becker muscular dystrophy
G71.02 Facioscapulohumeral muscular dystrophy
G71.09 Other specified muscular dystrophies
G71.1 Myotonic disorders
G71.11 Myotonic muscular dystrophy
G71.12 Myotonia congenita
G71.13 Myotonic chondrodystrophy
G71.14 Drug induced myotonia
G71.19 Other specified myotonic disorders
G71.2 Congenital myopathies
G71.3 Mitochondrial myopathy, not elsewhere classified
G71.8 Other primary disorders of muscles
G71.9 Primary disorder of muscle, unspecified
G72 Other and unspecified myopathies
G72.0 Drug-induced myopathy
G72.1 Alcoholic myopathy
G72.2 Myopathy due to other toxic agents
G72.3 Periodic paralysis
G72.4 Inflammatory and immune myopathies, not elsewhere classified
G72.41 Inclusion body myositis [IBM]
G72.49 Other inflammatory and immune myopathies, not elsewhere classified

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

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