ICD-10-CM Codes
G00-G99 Diseases of the nervous system
G70-G73 Diseases of myoneural junction and muscle
G71- Primary disorders of muscles
2022 ICD-10-CM Diagnosis Code G71.3

2022 ICD-10-CM Diagnosis Code G71.3

Mitochondrial myopathy, not elsewhere classified

2016

2017

2018

2019

2020

2021

2022

Billable/Specific Code

G71.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2022 edition of ICD-10-CM G71.3 became effective on October 1, 2021.
This is the American ICD-10-CM version of G71.3 - other international versions of ICD-10 G71.3 may differ.

Type 1 Excludes

Type 1 Excludes Help

A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as G71.3. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

Kearns-Sayre syndrome (
ICD-10-CM Diagnosis Code H49.81
Kearns-Sayre syndrome
Applicable To
- Progressive external ophthalmoplegia with pigmentary retinopathy
Use Additional
- code for other manifestation, such as:
- heart block (I45.9)
H49.81
)
Leber's disease (
ICD-10-CM Diagnosis Code H47.21
Primary optic atrophy
H47.21
)
Leigh's encephalopathy (
ICD-10-CM Diagnosis Code G31.82
Leigh's disease
Applicable To
- Subacute necrotizing encephalopathy
G31.82
)
mitochondrial metabolism disorders (
ICD-10-CM Diagnosis Code E88.4
Mitochondrial metabolism disorders
Type 1 Excludes
- disorders of pyruvate metabolism (E74.4)
- Kearns-Sayre syndrome (H49.81)
- Leber's disease (H47.22)
- Leigh's encephalopathy (G31.82)
- Mitochondrial myopathy, NEC (G71.3)
- Reye's syndrome (G93.7)
E88.4.-
)
Reye's syndrome (
ICD-10-CM Diagnosis Code G93.7
Reye's syndrome
Code First
- poisoning due to salicylates, if applicable (T39.0-, with sixth character 1-4)
Use Additional
- code for adverse effect due to salicylates, if applicable (T39.0-, with sixth character 5)
G93.7
)

The following code(s) above G71.3 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to G71.3:

G00-G99
2022 ICD-10-CM Range G00-G99
Diseases of the nervous system
Type 2 Excludes
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Diseases of the nervous system
G71
ICD-10-CM Diagnosis Code G71
Primary disorders of muscles
Type 2 Excludes
- arthrogryposis multiplex congenita (Q74.3)
- metabolic disorders (E70-E88)
- myositis (M60.-)
Primary disorders of muscles

Approximate Synonyms

Mitochondrial myopathy
Mitochondrial ocular myopathy
Myopathy, mitochondrial

ICD-10-CM G71.3 is grouped within Diagnostic Related Group(s) (MS-DRG v39.0):

091 Other disorders of nervous system with mcc
092 Other disorders of nervous system with cc
093 Other disorders of nervous system without cc/mcc

Convert G71.3 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change
2022 (effective 10/1/2021): No change

Code annotations containing back-references to G71.3:

Type 1 Excludes: E88.4

ICD-10-CM Diagnosis Code E88.4
Mitochondrial metabolism disorders
Type 1 Excludes
- disorders of pyruvate metabolism (E74.4)
- Kearns-Sayre syndrome (H49.81)
- Leber's disease (H47.22)
- Leigh's encephalopathy (G31.82)
- Mitochondrial myopathy, NEC (G71.3)
- Reye's syndrome (G93.7)

Diagnosis Index entries containing back-references to G71.3:

Myopathy G72.9
ICD-10-CM Diagnosis Code G72.9
Myopathy, unspecified
- mitochondrial NEC G71.3

ICD-10-CM Codes Adjacent To G71.3

G71.13 Myotonic chondrodystrophy

G71.14 Drug induced myotonia

G71.19 Other specified myotonic disorders

G71.2 Congenital myopathies

G71.20 Congenital myopathy, unspecified

G71.21 Nemaline myopathy

G71.22 Centronuclear myopathy

G71.220 X-linked myotubular myopathy

G71.228 Other centronuclear myopathy

G71.29 Other congenital myopathy

G71.3 Mitochondrial myopathy, not elsewhere classified

G71.8 Other primary disorders of muscles

G71.9 Primary disorder of muscle, unspecified

G72 Other and unspecified myopathies

G72.0 Drug-induced myopathy

G72.1 Alcoholic myopathy

G72.2 Myopathy due to other toxic agents

G72.3 Periodic paralysis

G72.4 Inflammatory and immune myopathies, not elsewhere classified

G72.41 Inclusion body myositis [IBM]

G72.49 Other inflammatory and immune myopathies, not elsewhere classified

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2022 ICD-10-CM Diagnosis Code G71.3

Mitochondrial myopathy, not elsewhere classified

Kearns-Sayre syndrome

Primary optic atrophy

Leigh's disease

Mitochondrial metabolism disorders

Reye's syndrome

Diseases of the nervous system

Primary disorders of muscles

Mitochondrial metabolism disorders

Myopathy, unspecified