2023 ICD-10-CM Diagnosis Code G91.4

Hydrocephalus in diseases classified elsewhere

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Manifestation Code
  • G91.4 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2023 edition of ICD-10-CM G91.4 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of G91.4 - other international versions of ICD-10 G91.4 may differ.
ICD-10-CM Coding Rules
  • G91.4 describes the manifestation of an underlying disease, not the disease itself.
Code First
Code First Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • underlying condition, such as:
  • congenital syphilis (
    ICD-10-CM Diagnosis Code A50.4

    Late congenital neurosyphilis [juvenile neurosyphilis]

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Use Additional
    • code to identify any associated mental disorder
    A50.4-
    )
  • neoplasm (C00-D49
    ICD-10-CM Range C00-D49

    Neoplasms

    • C00-C14 Malignant neoplasms of lip, oral cavity ...
    • C15-C26 Malignant neoplasms of digestive organs
    • C30-C39 Malignant neoplasms of respiratory and i...
    • C40-C41 Malignant neoplasms of bone and articula...
    • C43-C44 Melanoma and other malignant neoplasms o...
    • C45-C49 Malignant neoplasms of mesothelial and s...
    • C50-C50 Malignant neoplasms of breast
    • C51-C58 Malignant neoplasms of female genital or...
    • C60-C63 Malignant neoplasms of male genital orga...
    • C64-C68 Malignant neoplasms of urinary tract
    • C69-C72 Malignant neoplasms of eye, brain and ot...
    • C73-C75 Malignant neoplasms of thyroid and other...
    • C76-C80 Malignant neoplasms of ill-defined, othe...
    • C7A-C7A Malignant neuroendocrine tumors
    • C7B-C7B Secondary neuroendocrine tumors
    • C81-C96 Malignant neoplasms of lymphoid, hematop...
    • D00-D09 In situ neoplasms
    • D10-D36 Benign neoplasms, except benign neuroend...
    • D37-D48 Neoplasms of uncertain behavior, polycyt...
    • D3A-D3A Benign neuroendocrine tumors
    • D49-D49 Neoplasms of unspecified behavior
    )
  • plasminogen deficiency (
    ICD-10-CM Diagnosis Code E88.02

    Plasminogen deficiency

      2019 - New Code 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Dysplasminogenemia
    • Hypoplasminogenemia
    • Type 1 plasminogen deficiency
    • Type 2 plasminogen deficiency
    Code Also
    • , if applicable, ligneous conjunctivitis (H10.51)
    Use Additional
    • code for associated findings, such as:
    • hydrocephalus (G91.4)
    • otitis media (H67.-)
    • respiratory disorder related to plasminogen deficiency (J99)
    E88.02
    )
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as G91.4. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • hydrocephalus due to congenital toxoplasmosis (
    ICD-10-CM Diagnosis Code P37.1

    Congenital toxoplasmosis

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Code on Newborn Record
    Applicable To
    • Hydrocephalus due to congenital toxoplasmosis
    P37.1
    )
The following code(s) above G91.4 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to G91.4:
  • G00-G99
    2023 ICD-10-CM Range G00-G99

    Diseases of the nervous system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the nervous system
  • G91
    ICD-10-CM Diagnosis Code G91

    Hydrocephalus

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Includes
    • acquired hydrocephalus
    Type 1 Excludes
    • Arnold-Chiari syndrome with hydrocephalus (Q07.-)
    • congenital hydrocephalus (Q03.-)
    • spina bifida with hydrocephalus (Q05.-)
    Hydrocephalus
ICD-10-CM G91.4 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):
  • 056 Degenerative nervous system disorders with mcc
  • 057 Degenerative nervous system disorders without mcc

Convert G91.4 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change
Code annotations containing back-references to G91.4:
  • Type 1 Excludes: G94
    ICD-10-CM Diagnosis Code G94

    Other disorders of brain in diseases classified elsewhere

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Manifestation Code
    Code First
    • underlying disease
    Type 1 Excludes
    • encephalopathy in congenital syphilis (A50.49)
    • encephalopathy in influenza (J09.X9, J10.81, J11.81)
    • encephalopathy in syphilis (A52.19)
    • hydrocephalus in diseases classified elsewhere (G91.4)
  • Use Additional: E88.02
    ICD-10-CM Diagnosis Code E88.02

    Plasminogen deficiency

      2019 - New Code 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Dysplasminogenemia
    • Hypoplasminogenemia
    • Type 1 plasminogen deficiency
    • Type 2 plasminogen deficiency
    Code Also
    • , if applicable, ligneous conjunctivitis (H10.51)
    Use Additional
    • code for associated findings, such as:
    • hydrocephalus (G91.4)
    • otitis media (H67.-)
    • respiratory disorder related to plasminogen deficiency (J99)

Diagnosis Index entries containing back-references to G91.4:
  • Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent) G91.9
    ICD-10-CM Diagnosis Code G91.9

    Hydrocephalus, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • in (due to)
      • neoplastic disease NEC G91.4 (see also Neoplasm)
    • secondary G91.4

ICD-10-CM Codes Adjacent To G91.4
G90.529 Complex regional pain syndrome I of unspecified lower limb
G90.59 Complex regional pain syndrome I of other specified site
G90.8 Other disorders of autonomic nervous system
G90.9 Disorder of the autonomic nervous system, unspecified
G90.A Postural orthostatic tachycardia syndrome [POTS]
G91 Hydrocephalus
G91.0 Communicating hydrocephalus
G91.1 Obstructive hydrocephalus
G91.2 (Idiopathic) normal pressure hydrocephalus
G91.3 Post-traumatic hydrocephalus, unspecified
G91.4 Hydrocephalus in diseases classified elsewhere
G91.8 Other hydrocephalus
G91.9 Hydrocephalus, unspecified
G92 Toxic encephalopathy
G92.0 Immune effector cell-associated neurotoxicity syndrome
G92.00 …… grade unspecified
G92.01 …… grade 1
G92.02 …… grade 2
G92.03 …… grade 3
G92.04 …… grade 4
G92.05 …… grade 5

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.