ICD-10-CM Codes
H00-H59 Diseases of the eye and adnexa
H30-H36 Disorders of choroid and retina
H31- Other disorders of choroid

2019 ICD-10-CM Diagnosis Code H31.21

Choroideremia

2016

2017

2018

2019

Billable/Specific Code

H31.21 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2019 edition of ICD-10-CM H31.21 became effective on October 1, 2018.
This is the American ICD-10-CM version of H31.21 - other international versions of ICD-10 H31.21 may differ.

The following code(s) above H31.21 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to H31.21:

H00-H59
2019 ICD-10-CM Range H00-H59
Diseases of the eye and adnexa
Note
- Use an external cause code following the code for the eye condition, if applicable, to identify the cause of the eye condition
Type 2 Excludes
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury (trauma) of eye and orbit (S05.-)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)
Diseases of the eye and adnexa
H31.2
ICD-10-CM Diagnosis Code H31.2
Hereditary choroidal dystrophy
Type 2 Excludes
- hyperornithinemia (E72.4)
- ornithinemia (E72.4)
Hereditary choroidal dystrophy

Approximate Synonyms

Choroideremia (eye condition)

Clinical Information

A rare, x-linked inherited disorder characterized by choroid atrophy and retinal degeneration. It leads to progressive loss of vision.
An x chromosome-linked abnormality characterized by atrophy of the choroid and degeneration of the retinal pigment epithelium causing night blindness.

ICD-10-CM H31.21 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):

124 Other disorders of the eye with mcc
125 Other disorders of the eye without mcc

Convert H31.21 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change

Diagnosis Index entries containing back-references to H31.21:

Choroideremia H31.21
Dystrophy, dystrophia
- choroid (hereditary) H31.20
  ICD-10-CM Diagnosis Code H31.20
  Hereditary choroidal dystrophy, unspecified
  2016 2017 2018 2019 Billable/Specific Code
  - choroideremia H31.21

ICD-10-CM Codes Adjacent To H31.21

H31.112 …… left eye

H31.113 …… bilateral

H31.119 …… unspecified eye

H31.12 Diffuse secondary atrophy of choroid

H31.121 …… right eye

H31.122 …… left eye

H31.123 …… bilateral

H31.129 …… unspecified eye

H31.2 Hereditary choroidal dystrophy

H31.20 …… unspecified

H31.21 Choroideremia

H31.22 Choroidal dystrophy (central areolar) (generalized) (peripapillary)

H31.23 Gyrate atrophy, choroid

H31.29 Other hereditary choroidal dystrophy

H31.3 Choroidal hemorrhage and rupture

H31.30 Unspecified choroidal hemorrhage

H31.301 …… right eye

H31.302 …… left eye

H31.303 …… bilateral

H31.309 …… unspecified eye

H31.31 Expulsive choroidal hemorrhage

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2019 ICD-10-CM Diagnosis Code H31.21

Choroideremia

Diseases of the eye and adnexa

Hereditary choroidal dystrophy

Hereditary choroidal dystrophy, unspecified