2023 ICD-10-CM Diagnosis Code H35.53

Other dystrophies primarily involving the sensory retina

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • H35.53 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2023 edition of ICD-10-CM H35.53 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of H35.53 - other international versions of ICD-10 H35.53 may differ.
Applicable To
  • Stargardt's disease
The following code(s) above H35.53 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to H35.53:
  • H00-H59
    2023 ICD-10-CM Range H00-H59

    Diseases of the eye and adnexa

    • Use an external cause code following the code for the eye condition, if applicable, to identify the cause of the eye condition
    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury (trauma) of eye and orbit (S05.-)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    • syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)
    Diseases of the eye and adnexa
  • H35
    ICD-10-CM Diagnosis Code H35

    Other retinal disorders

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Type 2 Excludes
    Other retinal disorders
  • H35.5
    ICD-10-CM Diagnosis Code H35.5

    Hereditary retinal dystrophy

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • dystrophies primarily involving Bruch's membrane (H31.1-)
    Hereditary retinal dystrophy
Approximate Synonyms
  • Progressive cone dystrophy (without rod involvement)
  • Progressive cone retinal dystrophy
  • Sensory retinal dystrophy
  • Sensory retinal dystrophy (eye condition)
  • Stargardt's disease
  • Stargardts disease (eye condition)
Clinical Information
  • An autosomal recessive and rarely autosomal dominant inherited disorder caused by mutations in the abca4 or elovl4 genes respectively. It is characterized by macular degeneration that begins in late childhood resulting in progressive loss of vision.
ICD-10-CM H35.53 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):
  • 124 Other disorders of the eye with mcc
  • 125 Other disorders of the eye without mcc

Convert H35.53 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change

Diagnosis Index entries containing back-references to H35.53:

ICD-10-CM Codes Adjacent To H35.53
H35.459 …… unspecified eye
H35.46 Secondary vitreoretinal degeneration
H35.461 …… right eye
H35.462 …… left eye
H35.463 …… bilateral
H35.469 …… unspecified eye
H35.5 Hereditary retinal dystrophy
H35.50 Unspecified hereditary retinal dystrophy
H35.51 Vitreoretinal dystrophy
H35.52 Pigmentary retinal dystrophy
H35.53 Other dystrophies primarily involving the sensory retina
H35.54 Dystrophies primarily involving the retinal pigment epithelium
H35.6 Retinal hemorrhage
H35.60 …… unspecified eye
H35.61 …… right eye
H35.62 …… left eye
H35.63 …… bilateral
H35.7 Separation of retinal layers
H35.70 Unspecified separation of retinal layers
H35.71 Central serous chorioretinopathy
H35.711 …… right eye

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.