2021 ICD-10-CM Diagnosis Code I00

Rheumatic fever without heart involvement

    2016 2017 2018 2019 2020 2021 Billable/Specific Code
  • I00 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2021 edition of ICD-10-CM I00 became effective on October 1, 2020.
  • This is the American ICD-10-CM version of I00 - other international versions of ICD-10 I00 may differ.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as I00. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • rheumatic fever with heart involvement (
    ICD-10-CM Diagnosis Code I01.0

    Acute rheumatic pericarditis

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Any condition in I00 with pericarditis
    • Rheumatic pericarditis (acute)
    Type 1 Excludes
    • acute pericarditis not specified as rheumatic (I30.-)
    I01.0
    -
    ICD-10-CM Diagnosis Code I01.9

    Acute rheumatic heart disease, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Any condition in I00 with unspecified type of heart involvement
    • Rheumatic carditis, acute
    • Rheumatic heart disease, active or acute
    I01.9
    )
Includes
Includes Help
"Includes" further defines, or give examples of, the content of the code or category.
  • arthritis, rheumatic, acute or subacute
The following code(s) above I00 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to I00:
  • I00-I99
    2021 ICD-10-CM Range I00-I99

    Diseases of the circulatory system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    • systemic connective tissue disorders (M30-M36)
    • transient cerebral ischemic attacks and related syndromes (G45.-)
    Diseases of the circulatory system
Approximate Synonyms
  • Migratory polyarthritis
  • Rheumatic fever
ICD-10-CM I00 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):
  • 545 Connective tissue disorders with mcc
  • 546 Connective tissue disorders with cc
  • 547 Connective tissue disorders without cc/mcc

Convert I00 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
Code annotations containing back-references to I00:
  • Code First: J17
    ICD-10-CM Diagnosis Code J17

    Pneumonia in diseases classified elsewhere

      2016 2017 2018 2019 2020 2021 Billable/Specific Code Manifestation Code
    Code First
    • underlying disease, such as:
    • Q fever (A78)
    • rheumatic fever (I00)
    • schistosomiasis (B65.0-B65.9)
    Type 1 Excludes
    • candidial pneumonia (B37.1)
    • chlamydial pneumonia (J16.0)
    • gonorrheal pneumonia (A54.84)
    • histoplasmosis pneumonia (B39.0-B39.2)
    • measles pneumonia (B05.2)
    • nocardiosis pneumonia (A43.0)
    • pneumocystosis (B59)
    • pneumonia due to Pneumocystis carinii (B59)
    • pneumonia due to Pneumocystis jiroveci (B59)
    • pneumonia in actinomycosis (A42.0)
    • pneumonia in anthrax (A22.1)
    • pneumonia in ascariasis (B77.81)
    • pneumonia in aspergillosis (B44.0-B44.1)
    • pneumonia in coccidioidomycosis (B38.0-B38.2)
    • pneumonia in cytomegalovirus disease (B25.0)
    • pneumonia in toxoplasmosis (B58.3)
    • rubella pneumonia (B06.81)
    • salmonella pneumonia (A02.22)
    • spirochetal infection NEC with pneumonia (A69.8)
    • tularemia pneumonia (A21.2)
    • typhoid fever with pneumonia (A01.03)
    • varicella pneumonia (B01.2)
    • whooping cough with pneumonia (A37 with fifth-character 1)
  • Type 1 Excludes: M02
    , M05
    ICD-10-CM Diagnosis Code M02

    Postinfective and reactive arthropathies

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Code First
    • underlying disease, such as:
    • congenital syphilis [Clutton's joints] (A50.5)
    • enteritis due to Yersinia enterocolitica (A04.6)
    • infective endocarditis (I33.0)
    • viral hepatitis (B15-B19)
    Type 1 Excludes
    • Behçet's disease (M35.2)
    • direct infections of joint in infectious and parasitic diseases classified elsewhere (M01.-)
    • postmeningococcal arthritis (A39.84)
    • mumps arthritis (B26.85)
    • rubella arthritis (B06.82)
    • syphilis arthritis (late) (A52.77)
    • rheumatic fever (I00)
    • tabetic arthropathy [Charcôt's] (A52.16)
    ICD-10-CM Diagnosis Code M05

    Rheumatoid arthritis with rheumatoid factor

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • rheumatic fever (I00)
    • juvenile rheumatoid arthritis (M08.-)
    • rheumatoid arthritis of spine (M45.-)
  • Applicable To: I01.0
    , I01.1
    , I01.2
    , I01.8
    , I01.9
    ICD-10-CM Diagnosis Code I01.0

    Acute rheumatic pericarditis

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Any condition in I00 with pericarditis
    • Rheumatic pericarditis (acute)
    Type 1 Excludes
    • acute pericarditis not specified as rheumatic (I30.-)
    ICD-10-CM Diagnosis Code I01.1

    Acute rheumatic endocarditis

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Any condition in I00 with endocarditis or valvulitis
    • Acute rheumatic valvulitis
    ICD-10-CM Diagnosis Code I01.2

    Acute rheumatic myocarditis

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Any condition in I00 with myocarditis
    ICD-10-CM Diagnosis Code I01.8

    Other acute rheumatic heart disease

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Any condition in I00 with other or multiple types of heart involvement
    • Acute rheumatic pancarditis
    ICD-10-CM Diagnosis Code I01.9

    Acute rheumatic heart disease, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Any condition in I00 with unspecified type of heart involvement
    • Rheumatic carditis, acute
    • Rheumatic heart disease, active or acute

Diagnosis Index entries containing back-references to I00:
  • Erythema, erythematous (infectional) (inflammation) L53.9
    ICD-10-CM Diagnosis Code L53.9

    Erythematous condition, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Erythema NOS
    • Erythroderma NOS
    • marginatum L53.2
      ICD-10-CM Diagnosis Code L53.2

      Erythema marginatum

        2016 2017 2018 2019 2020 2021 Billable/Specific Code
      • in I00 (due to)
  • Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor) R50.9
    ICD-10-CM Diagnosis Code R50.9

    Fever, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Fever NOS
    • Fever of unknown origin [FUO]
    • Fever with chills
    • Fever with rigors
    • Hyperpyrexia NOS
    • Persistent fever
    • Pyrexia NOS
    • rheumatic (active) (acute) (chronic) (subacute) I00
  • Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) J18.9
    ICD-10-CM Diagnosis Code J18.9

    Pneumonia, unspecified organism

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    • in (due to)
      • rheumatic fever I00
    • rheumatic I00
  • Rheumatic (acute) (subacute)
    • pneumonia I00

ICD-10-CM Codes Adjacent To I00
H95.53 Postprocedural seroma of ear and mastoid process following a procedure on the ear and mastoid process
H95.54 Postprocedural seroma of ear and mastoid process following other procedure
H95.8 Other intraoperative and postprocedural complications and disorders of the ear and mastoid process, not elsewhere classified
H95.81 Postprocedural stenosis of external ear canal
H95.811 Postprocedural stenosis of right external ear canal
H95.812 Postprocedural stenosis of left external ear canal
H95.813 …… bilateral
H95.819 Postprocedural stenosis of unspecified external ear canal
H95.88 Other intraoperative complications and disorders of the ear and mastoid process, not elsewhere classified
H95.89 Other postprocedural complications and disorders of the ear and mastoid process, not elsewhere classified
I00 Rheumatic fever without heart involvement
I01 Rheumatic fever with heart involvement
I01.0 Acute rheumatic pericarditis
I01.1 Acute rheumatic endocarditis
I01.2 Acute rheumatic myocarditis
I01.8 Other acute rheumatic heart disease
I01.9 Acute rheumatic heart disease, unspecified
I02 Rheumatic chorea
I02.0 Rheumatic chorea with heart involvement
I02.9 Rheumatic chorea without heart involvement
I05 Rheumatic mitral valve diseases

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.