2023 ICD-10-CM Diagnosis Code I01

Rheumatic fever with heart involvement

    2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
  • I01 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2023 edition of ICD-10-CM I01 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of I01 - other international versions of ICD-10 I01 may differ.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as I01. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • chronic diseases of rheumatic origin (I05-I09
    ICD-10-CM Range I05-I09

    Chronic rheumatic heart diseases

    • I05 Rheumatic mitral valve diseases
    • I06 Rheumatic aortic valve diseases
    • I07 Rheumatic tricuspid valve diseases
    • I08 Multiple valve diseases
    • I09 Other rheumatic heart diseases
    ) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process.
The following code(s) above I01 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to I01:
  • I00-I99
    2023 ICD-10-CM Range I00-I99

    Diseases of the circulatory system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    • systemic connective tissue disorders (M30-M36)
    • transient cerebral ischemic attacks and related syndromes (G45.-)
    Diseases of the circulatory system
Clinical Information
  • Cardiac manifestation of systemic rheumatological conditions, such as rheumatic fever. Rheumatic heart disease can involve any part the heart, most often the heart valves and the endocardium.
  • Most important manifestation and sequel to rheumatic fever, consisting chiefly of heart valve deformities.
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change
Code annotations containing back-references to I01:
  • Applicable To: I02.0
    ICD-10-CM Diagnosis Code I02.0

    Rheumatic chorea with heart involvement

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Chorea NOS with heart involvement
    • Rheumatic chorea with heart involvement of any type classifiable under I01.-

Diagnosis Index entries containing back-references to I01:
  • Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor) R50.9
    ICD-10-CM Diagnosis Code R50.9

    Fever, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Fever NOS
    • Fever of unknown origin [FUO]
    • Fever with chills
    • Fever with rigors
    • Hyperpyrexia NOS
    • Persistent fever
    • Pyrexia NOS
    • rheumatic (active) (acute) (chronic) (subacute) I00
      ICD-10-CM Diagnosis Code I00

      Rheumatic fever without heart involvement

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Includes
      • arthritis, rheumatic, acute or subacute
      Type 1 Excludes
      • rheumatic fever with heart involvement (I01.0 -I01.9)
      • active with heart involvement I01 - see category

ICD-10-CM Codes Adjacent To I01
H95.54 Postprocedural seroma of ear and mastoid process following other procedure
H95.8 Other intraoperative and postprocedural complications and disorders of the ear and mastoid process, not elsewhere classified
H95.81 Postprocedural stenosis of external ear canal
H95.811 Postprocedural stenosis of right external ear canal
H95.812 Postprocedural stenosis of left external ear canal
H95.813 …… bilateral
H95.819 Postprocedural stenosis of unspecified external ear canal
H95.88 Other intraoperative complications and disorders of the ear and mastoid process, not elsewhere classified
H95.89 Other postprocedural complications and disorders of the ear and mastoid process, not elsewhere classified
I00 Rheumatic fever without heart involvement
I01 Rheumatic fever with heart involvement
I01.0 Acute rheumatic pericarditis
I01.1 Acute rheumatic endocarditis
I01.2 Acute rheumatic myocarditis
I01.8 Other acute rheumatic heart disease
I01.9 Acute rheumatic heart disease, unspecified
I02 Rheumatic chorea
I02.0 Rheumatic chorea with heart involvement
I02.9 Rheumatic chorea without heart involvement
I05 Rheumatic mitral valve diseases
I05.0 Rheumatic mitral stenosis

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.