ICD-10-CM Codes
I00-I99
I00-I02
I01-
2023 ICD-10-CM Diagnosis Code I01.1

2023 ICD-10-CM Diagnosis Code I01.1

Acute rheumatic endocarditis

2016

2017

2018

2019

2020

2021

2022

2023

Billable/Specific Code

I01.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2023 edition of ICD-10-CM I01.1 became effective on October 1, 2022.
This is the American ICD-10-CM version of I01.1 - other international versions of ICD-10 I01.1 may differ.

Applicable To

Any condition in
ICD-10-CM Diagnosis Code I00
Rheumatic fever without heart involvement
Includes
- arthritis, rheumatic, acute or subacute
Type 1 Excludes
- rheumatic fever with heart involvement (I01.0 -I01.9)
I00
with endocarditis or valvulitis
Acute rheumatic valvulitis

The following code(s) above I01.1 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to I01.1:

I00-I99
2023 ICD-10-CM Range I00-I99
Diseases of the circulatory system
Type 2 Excludes
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- systemic connective tissue disorders (M30-M36)
- transient cerebral ischemic attacks and related syndromes (G45.-)
Diseases of the circulatory system
I01
ICD-10-CM Diagnosis Code I01
Rheumatic fever with heart involvement
Type 1 Excludes
- chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process.
Rheumatic fever with heart involvement

Approximate Synonyms

Acute rheumatic endocarditis (infected heart valve)

ICD-10-CM I01.1 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):

306 Cardiac congenital and valvular disorders with mcc
307 Cardiac congenital and valvular disorders without mcc

Convert I01.1 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change
2022 (effective 10/1/2021): No change
2023 (effective 10/1/2022): No change

Code annotations containing back-references to I01.1:

Type 1 Excludes: I33

ICD-10-CM Diagnosis Code I33
Acute and subacute endocarditis
Type 1 Excludes
- acute rheumatic endocarditis (I01.1)
- endocarditis NOS (I38)

Diagnosis Index entries containing back-references to I01.1:

Endocarditis (chronic) (marantic) (nonbacterial) (thrombotic) (valvular) I38
ICD-10-CM Diagnosis Code I38
Endocarditis, valve unspecified
Includes
endocarditis (chronic) NOS
valvular incompetence NOS
valvular insufficiency NOS
valvular regurgitation NOS
valvular stenosis NOS
valvulitis (chronic) NOS
Type 1 Excludes
congenital insufficiency of cardiac valve NOS (Q24.8)
congenital stenosis of cardiac valve NOS (Q24.8)
endocardial fibroelastosis (I42.4)
endocarditis specified as rheumatic (I09.1)
- acute or subacute I33.9
  ICD-10-CM Diagnosis Code I33.9
  Acute and subacute endocarditis, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Acute endocarditis NOS
  Acute myoendocarditis NOS
  Acute periendocarditis NOS
  Subacute endocarditis NOS
  Subacute myoendocarditis NOS
  Subacute periendocarditis NOS
  - rheumatic (aortic) (mitral) (pulmonary) (tricuspid) I01.1
- aortic (heart) (nonrheumatic) (valve) I35.8
  ICD-10-CM Diagnosis Code I35.8
  Other nonrheumatic aortic valve disorders
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - with
    - mitral disease I08.0
      ICD-10-CM Diagnosis Code I08.0
      Rheumatic disorders of both mitral and aortic valves
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      Involvement of both mitral and aortic valves specified as rheumatic or unspecified
      - active or acute I01.1
  - rheumatic I06.9
    ICD-10-CM Diagnosis Code I06.9
    Rheumatic aortic valve disease, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    Rheumatic aortic (valve) disease NOS
    - with mitral disease I08.0
      ICD-10-CM Diagnosis Code I08.0
      Rheumatic disorders of both mitral and aortic valves
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      Involvement of both mitral and aortic valves specified as rheumatic or unspecified
      - active or acute I01.1
    - active or acute I01.1
- mitral (chronic) (double) (fibroid) (heart) (inactive) (valve) (with chorea) I05.9
  ICD-10-CM Diagnosis Code I05.9
  Rheumatic mitral valve disease, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Rheumatic mitral (valve) disorder (chronic) NOS
  - with
    - aortic (valve) I08.0
      ICD-10-CM Diagnosis Code I08.0
      Rheumatic disorders of both mitral and aortic valves
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      Involvement of both mitral and aortic valves specified as rheumatic or unspecified
      - active or acute I01.1
  - active or acute I01.1
- pulmonary (chronic) (heart) (valve) I37.8
  ICD-10-CM Diagnosis Code I37.8
  Other nonrheumatic pulmonary valve disorders
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - acute or subacute I33.9
    ICD-10-CM Diagnosis Code I33.9
    Acute and subacute endocarditis, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    Acute endocarditis NOS
    Acute myoendocarditis NOS
    Acute periendocarditis NOS
    Subacute endocarditis NOS
    Subacute myoendocarditis NOS
    Subacute periendocarditis NOS
    - rheumatic I01.1
  - rheumatic (chronic) (inactive) (with chorea) I09.89
    ICD-10-CM Diagnosis Code I09.89
    Other specified rheumatic heart diseases
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    Rheumatic disease of pulmonary valve
    - active or acute I01.1
- rheumatic (chronic) (inactive) (with chorea) I09.1
  ICD-10-CM Diagnosis Code I09.1
  Rheumatic diseases of endocardium, valve unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Rheumatic endocarditis (chronic)
  Rheumatic valvulitis (chronic)
  Type 1 Excludes
  endocarditis, valve unspecified (I38)
  - active or acute (aortic) (mitral) (pulmonary) (tricuspid) I01.1
- tricuspid (chronic) (heart) (inactive) (rheumatic) (valve) (with chorea) I07.9
  ICD-10-CM Diagnosis Code I07.9
  Rheumatic tricuspid valve disease, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Rheumatic tricuspid valve disorder NOS
  - active or acute I01.1
Insufficiency, insufficient
- mitral (valve) I34.0
  ICD-10-CM Diagnosis Code I34.0
  Nonrheumatic mitral (valve) insufficiency
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Nonrheumatic mitral (valve) incompetence NOS
  Nonrheumatic mitral (valve) regurgitation NOS
  Code Also
  , if applicable:
  nonrheumatic mitral (valve) annulus calcification (I34.81)
  - rheumatic I05.1
    ICD-10-CM Diagnosis Code I05.1
    Rheumatic mitral insufficiency
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    Rheumatic mitral incompetence
    Rheumatic mitral regurgitation
    Type 1 Excludes
    mitral insufficiency not specified as rheumatic (I34.0)
    - active or acute I01.1
Stenosis, stenotic (cicatricial) - see also Stricture
- mitral (chronic) (inactive) (valve) I05.0
  ICD-10-CM Diagnosis Code I05.0
  Rheumatic mitral stenosis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Mitral (valve) obstruction (rheumatic)
  - active or acute I01.1

ICD-10-CM Codes Adjacent To I01.1

H95.81 Postprocedural stenosis of external ear canal

H95.811 Postprocedural stenosis of right external ear canal

H95.812 Postprocedural stenosis of left external ear canal

H95.813 …… bilateral

H95.819 Postprocedural stenosis of unspecified external ear canal

H95.88 Other intraoperative complications and disorders of the ear and mastoid process, not elsewhere classified

H95.89 Other postprocedural complications and disorders of the ear and mastoid process, not elsewhere classified

I00 Rheumatic fever without heart involvement

I01 Rheumatic fever with heart involvement

I01.0 Acute rheumatic pericarditis

I01.1 Acute rheumatic endocarditis

I01.2 Acute rheumatic myocarditis

I01.8 Other acute rheumatic heart disease

I01.9 Acute rheumatic heart disease, unspecified

I02 Rheumatic chorea

I02.0 Rheumatic chorea with heart involvement

I02.9 Rheumatic chorea without heart involvement

I05 Rheumatic mitral valve diseases

I05.0 Rheumatic mitral stenosis

I05.1 Rheumatic mitral insufficiency

I05.2 Rheumatic mitral stenosis with insufficiency

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2023 ICD-10-CM Diagnosis Code I01.1

Acute rheumatic endocarditis

Rheumatic fever without heart involvement

Diseases of the circulatory system

Rheumatic fever with heart involvement

Acute and subacute endocarditis

Endocarditis, valve unspecified

Acute and subacute endocarditis, unspecified

Other nonrheumatic aortic valve disorders

Rheumatic disorders of both mitral and aortic valves

Rheumatic aortic valve disease, unspecified

Rheumatic disorders of both mitral and aortic valves

Rheumatic mitral valve disease, unspecified

Rheumatic disorders of both mitral and aortic valves

Other nonrheumatic pulmonary valve disorders

Acute and subacute endocarditis, unspecified

Other specified rheumatic heart diseases

Rheumatic diseases of endocardium, valve unspecified

Rheumatic tricuspid valve disease, unspecified

Nonrheumatic mitral (valve) insufficiency

Rheumatic mitral insufficiency

Rheumatic mitral stenosis