2023

  1. ICD-10-CM Codes
    2. ›
  2. I00-I99
    3. ›
  3. I26-I28
    4. ›
  4. I27-
    5. ›
  5. 2023 ICD-10-CM Diagnosis Code I27.0

2023 ICD-10-CM Diagnosis Code I27.0

Primary pulmonary hypertension

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • I27.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2023 edition of ICD-10-CM I27.0 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of I27.0 - other international versions of ICD-10 I27.0 may differ.
Applicable To
  • Heritable pulmonary arterial hypertension
  • Idiopathic pulmonary arterial hypertension
  • Primary group 1 pulmonary hypertension
  • Primary pulmonary arterial hypertension
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as I27.0. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • persistent pulmonary hypertension of newborn (
    ICD-10-CM Diagnosis Code P29.30

    Pulmonary hypertension of newborn

      2018 - New Code 2019 2020 2021 2022 2023 Billable/Specific Code Code on Newborn Record POA Exempt
    Applicable To
    • Persistent pulmonary hypertension of newborn
    P29.30
    )
  • pulmonary hypertension NOS (
    ICD-10-CM Diagnosis Code I27.20

    Pulmonary hypertension, unspecified

      2018 - New Code 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Pulmonary hypertension NOS
    I27.20
    )
  • secondary pulmonary arterial hypertension (
    ICD-10-CM Diagnosis Code I27.21

    Secondary pulmonary arterial hypertension

      2018 - New Code 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • (Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
    • (Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension
    Code Also
    • associated conditions if applicable, or adverse effects of drugs or toxins, such as:
    • adverse effect of appetite depressants (T50.5X5)
    • congenital heart disease (Q20-Q28)
    • human immunodeficiency virus [HIV] disease (B20)
    • polymyositis (M33.2-)
    • portal hypertension (K76.6)
    • rheumatoid arthritis (M05.-)
    • schistosomiasis (B65.-)
    • Sjögren syndrome (M35.0-)
    • systemic sclerosis (M34.-)
    I27.21
    )
  • secondary pulmonary hypertension (
    ICD-10-CM Diagnosis Code I27.29

    Other secondary pulmonary hypertension

      2018 - New Code 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Group 5 pulmonary hypertension
    • Pulmonary hypertension with unclear multifactorial mechanisms
    • Pulmonary hypertension due to hematologic disorders
    • Pulmonary hypertension due to metabolic disorders
    • Pulmonary hypertension due to other systemic disorders
    Code Also
    • other associated disorders, if known, such as:
    • chronic myeloid leukemia (C92.10-C92.22)
    • essential thrombocythemia (D47.3)
    • Gaucher disease (E75.22)
    • hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
    • hyperthyroidism (E05.-)
    • hypothyroidism (E00-E03)
    • polycythemia vera (D45)
    • sarcoidosis (D86.-)
    I27.29
    )
The following code(s) above I27.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to I27.0:
  • I00-I99
    2023 ICD-10-CM Range I00-I99

    Diseases of the circulatory system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    • systemic connective tissue disorders (M30-M36)
    • transient cerebral ischemic attacks and related syndromes (G45.-)
    Diseases of the circulatory system
Approximate Synonyms
  • Ayerza's syndrome
  • Ayerzas syndrome
  • Idiopathic pulmonary arterial hypertension
Clinical Information
  • Increased blood pressure in the arteries of the lungs; the etiology is unknown.
ICD-10-CM I27.0 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):
  • 314 Other circulatory system diagnoses with mcc
  • 315 Other circulatory system diagnoses with cc
  • 316 Other circulatory system diagnoses without cc/mcc

Convert I27.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change
Code annotations containing back-references to I27.0:
  • Code First: I5A
    ICD-10-CM Diagnosis Code I5A

    Non-ischemic myocardial injury (non-traumatic)

      2022 - New Code 2023 Billable/Specific Code
    Applicable To
    • Acute (non-ischemic) myocardial injury
    • Chronic (non-ischemic) myocardial injury
    • Unspecified (non-ischemic) myocardial injury
    Code First
    • the underlying cause, if known and applicable, such as:
    • acute kidney failure (N17.-)
    • acute myocarditis (I40.-)
    • cardiomyopathy (I42.-)
    • chronic kidney disease (CKD) (N18.-)
    • heart failure (I50.-)
    • hypertensive urgency (I16.0)
    • nonrheumatic aortic valve disorders (I35.-)
    • paroxysmal tachycardia (I47.-)
    • pulmonary embolism (I26.-)
    • pulmonary hypertension (I27.0, I27.2-)
    • sepsis (A41.-)
    • takotsubo syndrome (I51.81)
    Type 1 Excludes
    • acute myocardial infarction (I21.-)
    • injury of heart (S26.-)
    Type 2 Excludes
    • other acute ischemic heart diseases (I24.-)
  • Type 2 Excludes: I70
    ICD-10-CM Diagnosis Code I70

    Atherosclerosis

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Includes
    • arteriolosclerosis
    • arterial degeneration
    • arteriosclerosis
    • arteriosclerotic vascular disease
    • arteriovascular degeneration
    • atheroma
    • endarteritis deformans or obliterans
    • senile arteritis
    • senile endarteritis
    • vascular degeneration
    Type 2 Excludes
    • arteriosclerotic cardiovascular disease (I25.1-)
    • arteriosclerotic heart disease (I25.1-)
    • atheroembolism (I75.-)
    • cerebral atherosclerosis (I67.2)
    • coronary atherosclerosis (I25.1-)
    • mesenteric atherosclerosis (K55.1)
    • precerebral atherosclerosis (I67.2)
    • primary pulmonary atherosclerosis (I27.0)
    Use Additional
    • code to identify:
    • exposure to environmental tobacco smoke (Z77.22)
    • history of tobacco dependence (Z87.891)
    • occupational exposure to environmental tobacco smoke (Z57.31)
    • tobacco dependence (F17.-)
    • tobacco use (Z72.0)

Diagnosis Index entries containing back-references to I27.0:
  • Arrillaga-Ayerza syndrome I27.0 (pulmonary sclerosis with pulmonary hypertension)
  • Arteriosclerosis, arteriosclerotic (diffuse) (obliterans) (of) (senile) (with calcification) I70.90
    ICD-10-CM Diagnosis Code I70.90

    Unspecified atherosclerosis

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Adult Dx (15-124 years)
    • pulmonary I27.0 (idiopathic)
  • Ayerza's disease or syndrome I27.0 (pulmonary artery sclerosis with pulmonary hypertension)
  • Cardiopathia nigra I27.0
  • Disease, diseased - see also Syndrome
    • heart (organic) I51.9
      ICD-10-CM Diagnosis Code I51.9

      Heart disease, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      • black I27.0
    • pulmonary - see also Disease, lung
      • hypertensive (vascular) I27.20
        - see also Hypertension, pulmonary
        ICD-10-CM Diagnosis Code I27.20

        Pulmonary hypertension, unspecified

          2018 - New Code 2019 2020 2021 2022 2023 Billable/Specific Code
        Applicable To
        • Pulmonary hypertension NOS
        • primary I27.0 (idiopathic)
    • Ayerza's I27.0 (pulmonary artery sclerosis with pulmonary hypertension)
  • Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic) I10
    ICD-10-CM Diagnosis Code I10

    Essential (primary) hypertension

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Questionable As Admission Dx
    Includes
    • high blood pressure
    • hypertension (arterial) (benign) (essential) (malignant) (primary) (systemic)
    Type 1 Excludes
    • hypertensive disease complicating pregnancy, childbirth and the puerperium (O10-O11, O13-O16)
    Type 2 Excludes
    • essential (primary) hypertension involving vessels of brain (I60-I69)
    • essential (primary) hypertension involving vessels of eye (H35.0-)
    • pulmonary I27.20
      ICD-10-CM Diagnosis Code I27.20

      Pulmonary hypertension, unspecified

        2018 - New Code 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Pulmonary hypertension NOS
      • primary I27.0 (idiopathic)
    • lesser circulation I27.0
  • Sclerosis, sclerotic
  • Syndrome - see also Disease
    • pulmonary
      • arteriosclerosis I27.0
    • Arrillaga-Ayerza I27.0
    • Ayerza I27.0 (-Arrillaga)
    • cardiacos negros I27.0

ICD-10-CM Codes Adjacent To I27.0
I26.01 Septic pulmonary embolism with acute cor pulmonale
I26.02 Saddle embolus of pulmonary artery with acute cor pulmonale
I26.09 Other pulmonary embolism with acute cor pulmonale
I26.9 Pulmonary embolism without acute cor pulmonale
I26.90 Septic pulmonary embolism without acute cor pulmonale
I26.92 Saddle embolus of pulmonary artery without acute cor pulmonale
I26.93 Single subsegmental pulmonary embolism without acute cor pulmonale
I26.94 Multiple subsegmental pulmonary emboli without acute cor pulmonale
I26.99 Other pulmonary embolism without acute cor pulmonale
I27 Other pulmonary heart diseases
I27.0 Primary pulmonary hypertension
I27.1 Kyphoscoliotic heart disease
I27.2 Other secondary pulmonary hypertension
I27.20 Pulmonary hypertension, unspecified
I27.21 Secondary pulmonary arterial hypertension
I27.22 Pulmonary hypertension due to left heart disease
I27.23 Pulmonary hypertension due to lung diseases and hypoxia
I27.24 Chronic thromboembolic pulmonary hypertension
I27.29 Other secondary pulmonary hypertension
I27.8 Other specified pulmonary heart diseases
I27.81 Cor pulmonale (chronic)

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

Advertise with Us | License ICD10 Data

Copyright © | ICD10data.com