2019 ICD-10-CM Diagnosis Code I28.0

Arteriovenous fistula of pulmonary vessels

    2016 2017 2018 2019 Billable/Specific Code
  • I28.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM I28.0 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of I28.0 - other international versions of ICD-10 I28.0 may differ.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as I28.0. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • congenital arteriovenous fistula (
    ICD-10-CM Diagnosis Code Q25.72

    Congenital pulmonary arteriovenous malformation

      2016 2017 2018 2019 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital pulmonary arteriovenous aneurysm
    Q25.72
    )
The following code(s) above I28.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to I28.0:
  • I00-I99
    2019 ICD-10-CM Range I00-I99

    Diseases of the circulatory system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    • systemic connective tissue disorders (M30-M36)
    • transient cerebral ischemic attacks and related syndromes (G45.-)
    Diseases of the circulatory system
Clinical Information
  • A congenital or acquired malformation characterized by abnormal communication between the pulmonary arteries and pulmonary veins in the lungs.
ICD-10-CM I28.0 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 314 Other circulatory system diagnoses with mcc
  • 315 Other circulatory system diagnoses with cc
  • 316 Other circulatory system diagnoses without cc/mcc

Convert I28.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change

Diagnosis Index entries containing back-references to I28.0:
  • Aneurysm (anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular) I72.9
    ICD-10-CM Diagnosis Code I72.9

    Aneurysm of unspecified site

      2016 2017 2018 2019 Billable/Specific Code
    • arteriovenous (congenital) - see also Malformation, arteriovenous
      • acquired I77.0
        ICD-10-CM Diagnosis Code I77.0

        Arteriovenous fistula, acquired

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Aneurysmal varix
        • Arteriovenous aneurysm, acquired
        Type 1 Excludes
        • arteriovenous aneurysm NOS (Q27.3-)
        • presence of arteriovenous shunt (fistula) for dialysis (Z99.2)
        • traumatic - see injury of blood vessel by body region
        Type 2 Excludes
        • pulmonary I28.0
    • pulmonary I28.1
      ICD-10-CM Diagnosis Code I28.1

      Aneurysm of pulmonary artery

        2016 2017 2018 2019 Billable/Specific Code
      Type 1 Excludes
      • congenital aneurysm (Q25.79)
      • congenital arteriovenous aneurysm (Q25.72)
      • arteriovenous Q25.72
        ICD-10-CM Diagnosis Code Q25.72

        Congenital pulmonary arteriovenous malformation

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital pulmonary arteriovenous aneurysm
        • acquired I28.0
  • Fistula (cutaneous) L98.8
    ICD-10-CM Diagnosis Code L98.8

    Other specified disorders of the skin and subcutaneous tissue

      2016 2017 2018 2019 Billable/Specific Code
    • arteriovenous (acquired) (nonruptured) I77.0
      ICD-10-CM Diagnosis Code I77.0

      Arteriovenous fistula, acquired

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Aneurysmal varix
      • Arteriovenous aneurysm, acquired
      Type 1 Excludes
      • arteriovenous aneurysm NOS (Q27.3-)
      • presence of arteriovenous shunt (fistula) for dialysis (Z99.2)
      • traumatic - see injury of blood vessel by body region
      Type 2 Excludes
    • pulmonary J86.0
      ICD-10-CM Diagnosis Code J86.0

      Pyothorax with fistula

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Bronchocutaneous fistula
      • Bronchopleural fistula
      • Hepatopleural fistula
      • Mediastinal fistula
      • Pleural fistula
      • Thoracic fistula
      • Any condition classifiable to J86.9 with fistula
  • Shunt

ICD-10-CM Codes Adjacent To I28.0
I27.23 Pulmonary hypertension due to lung diseases and hypoxia
I27.24 Chronic thromboembolic pulmonary hypertension
I27.29 Other secondary pulmonary hypertension
I27.8 Other specified pulmonary heart diseases
I27.81 Cor pulmonale (chronic)
I27.82 Chronic pulmonary embolism
I27.83 Eisenmenger's syndrome
I27.89 Other specified pulmonary heart diseases
I27.9 Pulmonary heart disease, unspecified
I28 Other diseases of pulmonary vessels
I28.0 Arteriovenous fistula of pulmonary vessels
I28.1 Aneurysm of pulmonary artery
I28.8 Other diseases of pulmonary vessels
I28.9 Disease of pulmonary vessels, unspecified
I30 Acute pericarditis
I30.0 Acute nonspecific idiopathic pericarditis
I30.1 Infective pericarditis
I30.8 Other forms of acute pericarditis
I30.9 Acute pericarditis, unspecified
I31 Other diseases of pericardium
I31.0 Chronic adhesive pericarditis

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.