2020 ICD-10-CM Diagnosis Code I42

Cardiomyopathy

    2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
  • I42 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2020 edition of ICD-10-CM I42 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of I42 - other international versions of ICD-10 I42 may differ.
Code First
Code First Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • pre-existing cardiomyopathy complicating pregnancy and puerperium (
    ICD-10-CM Diagnosis Code O99.4

    Diseases of the circulatory system complicating pregnancy, childbirth and the puerperium

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Applicable To
    Type 1 Excludes
    • peripartum cardiomyopathy (O90.3)
    Type 2 Excludes
    • hypertensive disorders (O10-O16)
    • obstetric embolism (O88.-)
    • venous complications and cerebrovenous sinus thrombosis in labor, childbirth and the puerperium (O87.-)
    • venous complications and cerebrovenous sinus thrombosis in pregnancy (O22.-)
    O99.4
    )
Type 2 Excludes
Type 2 Excludes Help
A type 2 excludes note represents "not included here". A type 2 excludes note indicates that the condition excluded is not part of the condition it is excluded from but a patient may have both conditions at the same time. When a type 2 excludes note appears under a code it is acceptable to use both the code (I42) and the excluded code together.
  • ischemic cardiomyopathy (
    ICD-10-CM Diagnosis Code I25.5

    Ischemic cardiomyopathy

      2016 2017 2018 2019 2020 Billable/Specific Code
    Type 2 Excludes
    I25.5
    )
  • peripartum cardiomyopathy (
    ICD-10-CM Diagnosis Code O90.3

    Peripartum cardiomyopathy

      2016 2017 2018 2019 2020 Billable/Specific Code Maternity Dx (12-55 years)
    Applicable To
    • Conditions in I42.- arising during pregnancy and the puerperium
    Type 1 Excludes
    • pre-existing heart disease complicating pregnancy and the puerperium (O99.4-)
    O90.3
    )
  • ventricular hypertrophy (
    ICD-10-CM Diagnosis Code I51.7

    Cardiomegaly

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Cardiac dilatation
    • Cardiac hypertrophy
    • Ventricular dilatation
    I51.7
    )
Includes
Includes Help
"Includes" further defines, or give examples of, the content of the code or category.
  • myocardiopathy
The following code(s) above I42 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to I42:
  • I00-I99
    2020 ICD-10-CM Range I00-I99

    Diseases of the circulatory system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    • systemic connective tissue disorders (M30-M36)
    • transient cerebral ischemic attacks and related syndromes (G45.-)
    Diseases of the circulatory system
Clinical Information
  • A disease of the heart muscle or myocardium proper. Cardiomyopathies may be classified as either primary or secondary, on the basis of etiology, or on the pathophysiology of the lesion: hypertrophic, dilated, or restrictive.
  • A group of diseases in which the dominant feature is the involvement of the cardiac muscle itself. Cardiomyopathies are classified according to their predominant pathophysiological features (dilated cardiomyopathy; hypertrophic cardiomyopathy; restrictive cardiomyopathy) or their etiological/pathological factors (cardiomyopathy, alcoholic; endocardial fibroelastosis).
  • Cardiomyopathy refers to diseases of the heart muscle. These diseases enlarge your heart muscle or make it thicker and more rigid than normal. In rare cases, scar tissue replaces the muscle tissue.some people live long, healthy lives with cardiomyopathy. Some people don't even realize they have it. In others, however, it can make the heart less able to pump blood through the body. This can cause serious complications, including
    • heart failure
    • abnormal heart rhythms
    • fluid buildup in your lungs or legs
    • endocarditis, an inflammation of the heart lining
    heart attacks, high blood pressure or infections can all cause cardiomyopathy. Some types of cardiomyopathy run in families. In many people, however, the cause is unknown. Treatment might involve medicines, surgery, other medical procedures and lifestyle changes.
  • Condition in which there is a deviation from or interruption of the normal structure or function of the myocardium, the middle and thickest layer of the heart wall, composed of heart muscle.
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to I42:
  • Applicable To: O90.3
    ICD-10-CM Diagnosis Code O90.3

    Peripartum cardiomyopathy

      2016 2017 2018 2019 2020 Billable/Specific Code Maternity Dx (12-55 years)
    Applicable To
    • Conditions in I42.- arising during pregnancy and the puerperium
    Type 1 Excludes
    • pre-existing heart disease complicating pregnancy and the puerperium (O99.4-)
ICD-10-CM Codes Adjacent To I42
I37.8 Other nonrheumatic pulmonary valve disorders
I37.9 Nonrheumatic pulmonary valve disorder, unspecified
I38 Endocarditis, valve unspecified
I39 Endocarditis and heart valve disorders in diseases classified elsewhere
I40 Acute myocarditis
I40.0 Infective myocarditis
I40.1 Isolated myocarditis
I40.8 Other acute myocarditis
I40.9 Acute myocarditis, unspecified
I41 Myocarditis in diseases classified elsewhere
I42 Cardiomyopathy
I42.0 Dilated cardiomyopathy
I42.1 Obstructive hypertrophic cardiomyopathy
I42.2 Other hypertrophic cardiomyopathy
I42.3 Endomyocardial (eosinophilic) disease
I42.4 Endocardial fibroelastosis
I42.5 Other restrictive cardiomyopathy
I42.6 Alcoholic cardiomyopathy
I42.7 Cardiomyopathy due to drug and external agent
I42.8 Other cardiomyopathies
I42.9 Cardiomyopathy, unspecified

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.