2023 ICD-10-CM Diagnosis Code I40.1

Isolated myocarditis

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • I40.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2023 edition of ICD-10-CM I40.1 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of I40.1 - other international versions of ICD-10 I40.1 may differ.
Applicable To
  • Fiedler's myocarditis
  • Giant cell myocarditis
  • Idiopathic myocarditis
The following code(s) above I40.1 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to I40.1:
  • I00-I99
    2023 ICD-10-CM Range I00-I99

    Diseases of the circulatory system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    • systemic connective tissue disorders (M30-M36)
    • transient cerebral ischemic attacks and related syndromes (G45.-)
    Diseases of the circulatory system
  • I40
    ICD-10-CM Diagnosis Code I40

    Acute myocarditis

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Includes
    • subacute myocarditis
    Type 1 Excludes
    • acute rheumatic myocarditis (I01.2)
    Acute myocarditis
Approximate Synonyms
  • Idiopathic myocarditis
Clinical Information
  • An often fatal inflammatory disorder that affects the myocardium. Morphologically, it is characterized by the presence of an inflammatory infiltrate in the myocardial tissue that includes multinucleated giant cells. It is often associated with the presence of an autoimmune disorder. Patients present with arrhythmias and/or heart failure. Heart transplantation is the only treatment option available.
ICD-10-CM I40.1 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):
  • 314 Other circulatory system diagnoses with mcc
  • 315 Other circulatory system diagnoses with cc
  • 316 Other circulatory system diagnoses without cc/mcc
  • 974 Hiv with major related condition with mcc
  • 975 Hiv with major related condition with cc
  • 976 Hiv with major related condition without cc/mcc

Convert I40.1 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change

Diagnosis Index entries containing back-references to I40.1:
  • Abramov-Fiedler myocarditis I40.1 (acute isolated myocarditis)
  • Fiedler's
    • myocarditis I40.1 (acute)
  • Myocarditis (with arteriosclerosis)(chronic)(fibroid) (interstitial) (old) (progressive) (senile) I51.4
    ICD-10-CM Diagnosis Code I51.4

    Myocarditis, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Chronic (interstitial) myocarditis
    • Myocardial fibrosis
    • Myocarditis NOS
    Type 1 Excludes
    • acute or subacute myocarditis (I40.-)
    • acute or subacute (interstitial) I40.9
      ICD-10-CM Diagnosis Code I40.9

      Acute myocarditis, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      • idiopathic I40.1
    • eosinophilic I40.1
    • Fiedler's I40.1 (acute) (isolated)
    • giant cell I40.1 (acute) (subacute)
    • granulomatous I40.1 (idiopathic) (isolated) (nonspecific)
    • idiopathic I40.1 (granulomatous)
    • isolated I40.1 (acute)
  • Syndrome - see also Disease
    • Fiedler's I40.1

ICD-10-CM Codes Adjacent To I40.1
I37 Nonrheumatic pulmonary valve disorders
I37.0 Nonrheumatic pulmonary valve stenosis
I37.1 Nonrheumatic pulmonary valve insufficiency
I37.2 Nonrheumatic pulmonary valve stenosis with insufficiency
I37.8 Other nonrheumatic pulmonary valve disorders
I37.9 Nonrheumatic pulmonary valve disorder, unspecified
I38 Endocarditis, valve unspecified
I39 Endocarditis and heart valve disorders in diseases classified elsewhere
I40 Acute myocarditis
I40.0 Infective myocarditis
I40.1 Isolated myocarditis
I40.8 Other acute myocarditis
I40.9 Acute myocarditis, unspecified
I41 Myocarditis in diseases classified elsewhere
I42 Cardiomyopathy
I42.0 Dilated cardiomyopathy
I42.1 Obstructive hypertrophic cardiomyopathy
I42.2 Other hypertrophic cardiomyopathy
I42.3 Endomyocardial (eosinophilic) disease
I42.4 Endocardial fibroelastosis
I42.5 Other restrictive cardiomyopathy

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.