Cardiomyopathy I42-

Code First
Code First Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • pre-existing cardiomyopathy complicating pregnancy and puerperium (
    ICD-10-CM Diagnosis Code O99.4

    Diseases of the circulatory system complicating pregnancy, childbirth and the puerperium

      2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
    Applicable To
    Type 1 Excludes
    • peripartum cardiomyopathy (O90.3)
    Type 2 Excludes
    • hypertensive disorders (O10-O16)
    • obstetric embolism (O88.-)
    • venous complications and cerebrovenous sinus thrombosis in labor, childbirth and the puerperium (O87.-)
    • venous complications and cerebrovenous sinus thrombosis in pregnancy (O22.-)
Type 2 Excludes
Type 2 Excludes Help
A type 2 excludes note represents "not included here". A type 2 excludes note indicates that the condition excluded is not part of the condition it is excluded from but a patient may have both conditions at the same time. When a type 2 excludes note appears under a code it is acceptable to use both the code (I42) and the excluded code together.
  • ischemic cardiomyopathy (
    ICD-10-CM Diagnosis Code I25.5

    Ischemic cardiomyopathy

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
    Type 2 Excludes
  • peripartum cardiomyopathy (
    ICD-10-CM Diagnosis Code O90.3

    Peripartum cardiomyopathy

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code Maternity Dx (12-55 years)
    Applicable To
    • Conditions in I42.- arising during pregnancy and the puerperium
    Type 1 Excludes
    • pre-existing heart disease complicating pregnancy and the puerperium (O99.4-)
  • ventricular hypertrophy (
    ICD-10-CM Diagnosis Code I51.7


      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
    Applicable To
    • Cardiac dilatation
    • Cardiac hypertrophy
    • Ventricular dilatation
Includes Help
"Includes" further defines, or give examples of, the content of the code or category.
  • myocardiopathy
Clinical Information
  • A disease of the heart muscle or myocardium proper. Cardiomyopathies may be classified as either primary or secondary, on the basis of etiology, or on the pathophysiology of the lesion: hypertrophic, dilated, or restrictive.
  • A group of diseases in which the dominant feature is the involvement of the cardiac muscle itself. Cardiomyopathies are classified according to their predominant pathophysiological features (dilated cardiomyopathy; hypertrophic cardiomyopathy; restrictive cardiomyopathy) or their etiological/pathological factors (cardiomyopathy, alcoholic; endocardial fibroelastosis).
  • Cardiomyopathy refers to diseases of the heart muscle. These diseases enlarge your heart muscle or make it thicker and more rigid than normal. In rare cases, scar tissue replaces the muscle tissue.some people live long, healthy lives with cardiomyopathy. Some people don't even realize they have it. In others, however, it can make the heart less able to pump blood through the body. This can cause serious complications, including
    • heart failure
    • abnormal heart rhythms
    • fluid buildup in your lungs or legs
    • endocarditis, an inflammation of the heart lining
    heart attacks, high blood pressure or infections can all cause cardiomyopathy. Some types of cardiomyopathy run in families. In many people, however, the cause is unknown. Treatment might involve medicines, surgery, other medical procedures and lifestyle changes.
  • Condition in which there is a deviation from or interruption of the normal structure or function of the myocardium, the middle and thickest layer of the heart wall, composed of heart muscle.
  • I42 Cardiomyopathy
    • I42.0 Dilated cardiomyopathy
    • I42.1 Obstructive hypertrophic cardiomyopathy
    • I42.2 Other hypertrophic cardiomyopathy
    • I42.3 Endomyocardial (eosinophilic) disease
    • I42.4 Endocardial fibroelastosis
    • I42.5 Other restrictive cardiomyopathy
    • I42.6 Alcoholic cardiomyopathy
    • I42.7 Cardiomyopathy due to drug and external agent
    • I42.8 Other cardiomyopathies
    • I42.9 Cardiomyopathy, unspecified