2019 ICD-10-CM Diagnosis Code I67.5

Moyamoya disease

    2016 2017 2018 2019 Billable/Specific Code
  • I67.5 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM I67.5 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of I67.5 - other international versions of ICD-10 I67.5 may differ.
The following code(s) above I67.5 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to I67.5:
  • I00-I99
    2019 ICD-10-CM Range I00-I99

    Diseases of the circulatory system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    • systemic connective tissue disorders (M30-M36)
    • transient cerebral ischemic attacks and related syndromes (G45.-)
    Diseases of the circulatory system
  • I60-I69
    2019 ICD-10-CM Range I60-I69

    Cerebrovascular diseases

    Type 1 Excludes
    • traumatic intracranial hemorrhage (S06.-)
    Use Additional
    • code to identify presence of:
    • alcohol abuse and dependence (F10.-)
    • exposure to environmental tobacco smoke (Z77.22)
    • history of tobacco dependence (Z87.891)
    • hypertension (I10-I16)
    • occupational exposure to environmental tobacco smoke (Z57.31)
    • tobacco dependence (F17.-)
    • tobacco use (Z72.0)
    Cerebrovascular diseases
  • I67
    ICD-10-CM Diagnosis Code I67

    Other cerebrovascular diseases

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • sequelae of the listed conditions (I69.8)
    Other cerebrovascular diseases
Clinical Information
  • A noninflammatory, progressive occlusion of the intracranial carotid arteries and the formation of netlike collateral arteries arising from the circle of willis. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial hyperplasia and fibrosis with thickening of arterial walls. This disease primarily affects children but can also occur in adults.
  • A rare inherited vascular disorder characterized by constriction of arteries at the base of the brain, resulting in the formation of collateral circulation in order to compensate for the constriction. The name "moyamoya" in japanese means "puff of smoke" and derives from the characteristic radiographic appearance of the collateral vessels.
ICD-10-CM I67.5 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 091 Other disorders of nervous system with mcc
  • 092 Other disorders of nervous system with cc
  • 093 Other disorders of nervous system without cc/mcc

Convert I67.5 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change

Diagnosis Index entries containing back-references to I67.5:
  • Disease, diseased - see also Syndrome
    • moyamoya I67.5
    • Nishimoto I67.5 (-Takeuchi)
  • Encephaloduroarteriomyosynangiosis I67.5 (EDAMS)
  • Moyamoya disease I67.5
  • Nishimoto I67.5 (-Takeuchi)

ICD-10-CM Codes Adjacent To I67.5
I66.29 Occlusion and stenosis of unspecified posterior cerebral artery
I66.3 Occlusion and stenosis of cerebellar arteries
I66.8 Occlusion and stenosis of other cerebral arteries
I66.9 Occlusion and stenosis of unspecified cerebral artery
I67 Other cerebrovascular diseases
I67.0 Dissection of cerebral arteries, nonruptured
I67.1 Cerebral aneurysm, nonruptured
I67.2 Cerebral atherosclerosis
I67.3 Progressive vascular leukoencephalopathy
I67.4 Hypertensive encephalopathy
I67.5 Moyamoya disease
I67.6 Nonpyogenic thrombosis of intracranial venous system
I67.7 Cerebral arteritis, not elsewhere classified
I67.8 Other specified cerebrovascular diseases
I67.81 Acute cerebrovascular insufficiency
I67.82 Cerebral ischemia
I67.83 Posterior reversible encephalopathy syndrome
I67.84 Cerebral vasospasm and vasoconstriction
I67.841 Reversible cerebrovascular vasoconstriction syndrome
I67.848 Other cerebrovascular vasospasm and vasoconstriction
I67.85 Hereditary cerebrovascular diseases

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.