2020 ICD-10-CM Diagnosis Code J43.0

Unilateral pulmonary emphysema [MacLeod's syndrome]

    2016 2017 2018 2019 2020 Billable/Specific Code
  • J43.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM J43.0 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of J43.0 - other international versions of ICD-10 J43.0 may differ.
Applicable To
  • Swyer-James syndrome
  • Unilateral emphysema
  • Unilateral hyperlucent lung
  • Unilateral pulmonary artery functional hypoplasia
  • Unilateral transparency of lung
The following code(s) above J43.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to J43.0:
  • J00-J99
    2020 ICD-10-CM Range J00-J99

    Diseases of the respiratory system

    Note
    • When a respiratory condition is described as occurring in more than one site and is not specifically indexed, it should be classified to the lower anatomic site (e.g. tracheobronchitis to bronchitis in J40).
    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • smoke inhalation (T59.81-)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Use Additional
    • code, where applicable, to identify:
    • exposure to environmental tobacco smoke (Z77.22)
    • exposure to tobacco smoke in the perinatal period (P96.81)
    • history of tobacco dependence (Z87.891)
    • occupational exposure to environmental tobacco smoke (Z57.31)
    • tobacco dependence (F17.-)
    • tobacco use (Z72.0)
    Diseases of the respiratory system
  • J40-J47
    2020 ICD-10-CM Range J40-J47

    Chronic lower respiratory diseases

    Type 1 Excludes
    • bronchitis due to chemicals, gases, fumes and vapors (J68.0)
    Type 2 Excludes
    Chronic lower respiratory diseases
  • J43
    ICD-10-CM Diagnosis Code J43

    Emphysema

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • compensatory emphysema (J98.3)
    • emphysema due to inhalation of chemicals, gases, fumes or vapors (J68.4)
    • emphysema with chronic (obstructive) bronchitis (J44.-)
    • emphysematous (obstructive) bronchitis (J44.-)
    • interstitial emphysema (J98.2)
    • mediastinal emphysema (J98.2)
    • neonatal interstitial emphysema (P25.0)
    • surgical (subcutaneous) emphysema (T81.82)
    • traumatic subcutaneous emphysema (T79.7)
    Use Additional
    • code to identify:
    • exposure to environmental tobacco smoke (Z77.22)
    • history of tobacco dependence (Z87.891)
    • occupational exposure to environmental tobacco smoke (Z57.31)
    • tobacco dependence (F17.-)
    • tobacco use (Z72.0)
    Emphysema
Approximate Synonyms
  • Unilateral emphysema
Clinical Information
  • A pneumothorax condition marked by complete absence of markings in the chest radiograph.
  • A rare syndrome characterized by the presence of a small lung as a result of unilateral post-infectious bronchiolitis obliterans.
ICD-10-CM J43.0 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 190 Chronic obstructive pulmonary disease with mcc
  • 191 Chronic obstructive pulmonary disease with cc
  • 192 Chronic obstructive pulmonary disease without cc/mcc

Convert J43.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to J43.0:
  • Emphysema (atrophic) (bullous) (chronic) (interlobular) (lung) (obstructive) (pulmonary) (senile) (vesicular) J43.9
    ICD-10-CM Diagnosis Code J43.9

    Emphysema, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Bullous emphysema (lung)(pulmonary)
    • Emphysema (lung)(pulmonary) NOS
    • Emphysematous bleb
    • Vesicular emphysema (lung)(pulmonary)
    • unilateral J43.0
  • Hyperlucent lung, unilateral J43.0
  • Hypoplasia, hypoplastic
    • artery (peripheral) Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix
      Type 1 Excludes
      • arteriovenous malformation (Q27.3-)
      • pulmonary Q25.79
        ICD-10-CM Diagnosis Code Q25.79

        Other congenital malformations of pulmonary artery

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Aberrant pulmonary artery
        • Agenesis of pulmonary artery
        • Congenital aneurysm of pulmonary artery
        • Congenital anomaly of pulmonary artery
        • Hypoplasia of pulmonary artery
        • functional, unilateral J43.0
    • pulmonary (not associated with short gestation) Q33.6
      ICD-10-CM Diagnosis Code Q33.6

      Congenital hypoplasia and dysplasia of lung

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Type 1 Excludes
      • pulmonary hypoplasia associated with short gestation (P28.0)
      • artery, functional J43.0
  • MacLeod's syndrome J43.0
  • Transparency, lung, unilateral J43.0

ICD-10-CM Codes Adjacent To J43.0
J39.3 Upper respiratory tract hypersensitivity reaction, site unspecified
J39.8 Other specified diseases of upper respiratory tract
J39.9 Disease of upper respiratory tract, unspecified
J40 Bronchitis, not specified as acute or chronic
J41 Simple and mucopurulent chronic bronchitis
J41.0 Simple chronic bronchitis
J41.1 Mucopurulent chronic bronchitis
J41.8 Mixed simple and mucopurulent chronic bronchitis
J42 Unspecified chronic bronchitis
J43 Emphysema
J43.0 Unilateral pulmonary emphysema [MacLeod's syndrome]
J43.1 Panlobular emphysema
J43.2 Centrilobular emphysema
J43.8 Other emphysema
J43.9 Emphysema, unspecified
J44 Other chronic obstructive pulmonary disease
J44.0 Chronic obstructive pulmonary disease with (acute) lower respiratory infection
J44.1 Chronic obstructive pulmonary disease with (acute) exacerbation
J44.9 Chronic obstructive pulmonary disease, unspecified
J45 Asthma
J45.2 Mild intermittent asthma

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.