2020 ICD-10-CM Diagnosis Code J84.01

Alveolar proteinosis

    2016 2017 2018 2019 2020 Billable/Specific Code
  • J84.01 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM J84.01 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of J84.01 - other international versions of ICD-10 J84.01 may differ.
The following code(s) above J84.01 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to J84.01:
  • J00-J99
    2020 ICD-10-CM Range J00-J99

    Diseases of the respiratory system

    Note
    • When a respiratory condition is described as occurring in more than one site and is not specifically indexed, it should be classified to the lower anatomic site (e.g. tracheobronchitis to bronchitis in J40).
    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • smoke inhalation (T59.81-)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Use Additional
    • code, where applicable, to identify:
    • exposure to environmental tobacco smoke (Z77.22)
    • exposure to tobacco smoke in the perinatal period (P96.81)
    • history of tobacco dependence (Z87.891)
    • occupational exposure to environmental tobacco smoke (Z57.31)
    • tobacco dependence (F17.-)
    • tobacco use (Z72.0)
    Diseases of the respiratory system
  • J84
    ICD-10-CM Diagnosis Code J84

    Other interstitial pulmonary diseases

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • drug-induced interstitial lung disorders (J70.2-J70.4)
    • interstitial emphysema (J98.2)
    Type 2 Excludes
    • lung diseases due to external agents (J60-J70)
    Other interstitial pulmonary diseases
Approximate Synonyms
  • Pulmonary alveolar proteinosis
Clinical Information
  • A pulmonary alveoli-filling disease, characterized by dense phospholipoproteinaceous deposits in the alveoli, cough, and dyspnea. This disease is often related to, congenital or acquired, impaired processing of pulmonary surfactants by alveolar macrophages, a process dependent on granulocyte-macrophage colony-stimulating factor.
  • A rare lung disorder characterized by the filling of the pulmonary alveoli with proteinaceous material which stains positive with periodic acid-schiff stain. It may be idiopathic or secondary due to hematologic malignancies or the inhalation of mineral dusts. Signs and symptoms include dyspnea, cough and low grade fever.
  • Unknown etiology marked by chronic filling of alveoli with proteinaceous, lipid-rich, granular material consisting of surfactant and debris of necrotic cells.
ICD-10-CM J84.01 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 196 Interstitial lung disease with mcc
  • 197 Interstitial lung disease with cc
  • 198 Interstitial lung disease without cc/mcc

Convert J84.01 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to J84.01:

ICD-10-CM Codes Adjacent To J84.01
J70.5 Respiratory conditions due to smoke inhalation
J70.8 Respiratory conditions due to other specified external agents
J70.9 Respiratory conditions due to unspecified external agent
J80 Acute respiratory distress syndrome
J81 Pulmonary edema
J81.0 Acute pulmonary edema
J81.1 Chronic pulmonary edema
J82 Pulmonary eosinophilia, not elsewhere classified
J84 Other interstitial pulmonary diseases
J84.0 Alveolar and parieto-alveolar conditions
J84.01 Alveolar proteinosis
J84.02 Pulmonary alveolar microlithiasis
J84.03 Idiopathic pulmonary hemosiderosis
J84.09 Other alveolar and parieto-alveolar conditions
J84.1 Other interstitial pulmonary diseases with fibrosis
J84.10 Pulmonary fibrosis, unspecified
J84.11 Idiopathic interstitial pneumonia
J84.111 …… not otherwise specified
J84.112 Idiopathic pulmonary fibrosis
J84.113 Idiopathic non-specific interstitial pneumonitis
J84.114 Acute interstitial pneumonitis

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.