ICD-10-CM Codes
J00-J99
J96-J99
J99-
2023 ICD-10-CM Diagnosis Code J99

2023 ICD-10-CM Diagnosis Code J99

Respiratory disorders in diseases classified elsewhere

2016

2017

2018

2019

2020

2021

2022

2023

Billable/Specific Code

Manifestation Code

J99 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2023 edition of ICD-10-CM J99 became effective on October 1, 2022.
This is the American ICD-10-CM version of J99 - other international versions of ICD-10 J99 may differ.

ICD-10-CM Coding Rules

J99 describes the manifestation of an underlying disease, not the disease itself.

Code First

Code First Help

Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.

underlying disease, such as:
amyloidosis (
ICD-10-CM Diagnosis Code E85
- E85 Amyloidosis
  - E85.0 Non-neuropathic heredofamilial amyloidosis
  - E85.1 Neuropathic heredofamilial amyloidosis
  - E85.2 Heredofamilial amyloidosis, unspecified
  - E85.3 Secondary systemic amyloidosis
  - E85.4 Organ-limited amyloidosis
  - E85.8 Other amyloidosis
    - E85.81 Light chain (AL) amyloidosis
    - E85.82 Wild-type transthyretin-related (ATTR) amyloi...
    - E85.89 Other amyloidosis
  - E85.9 Amyloidosis, unspecified
E85.-
)
ankylosing spondylitis (
ICD-10-CM Diagnosis Code M45
Ankylosing spondylitis
Applicable To
- Rheumatoid arthritis of spine
Type 1 Excludes
- arthropathy in Reiter's disease (M02.3-)
- juvenile (ankylosing) spondylitis (M08.1)
Type 2 Excludes
- Behçet's disease (M35.2)
M45
)
congenital syphilis (
ICD-10-CM Diagnosis Code A50.5
Other late congenital syphilis, symptomatic
Applicable To
- Any congenital syphilitic condition specified as late or manifest two years or more after birth.
A50.5
)
cryoglobulinemia (
ICD-10-CM Diagnosis Code D89.1
Cryoglobulinemia
Applicable To
- Cryoglobulinemic purpura
- Cryoglobulinemic vasculitis
- Essential cryoglobulinemia
- Idiopathic cryoglobulinemia
- Mixed cryoglobulinemia
- Primary cryoglobulinemia
- Secondary cryoglobulinemia
D89.1
)
early congenital syphilis (
ICD-10-CM Diagnosis Code A50.0
Early congenital syphilis, symptomatic
Applicable To
- Any congenital syphilitic condition specified as early or manifest less than two years after birth.
A50.0
)
plasminogen deficiency (
ICD-10-CM Diagnosis Code E88.02
Plasminogen deficiency
Applicable To
- Dysplasminogenemia
- Hypoplasminogenemia
- Type 1 plasminogen deficiency
- Type 2 plasminogen deficiency
Code Also
- , if applicable, ligneous conjunctivitis (H10.51)
Use Additional
- code for associated findings, such as:
- hydrocephalus (G91.4)
- otitis media (H67.-)
- respiratory disorder related to plasminogen deficiency (J99)
E88.02
)
schistosomiasis (
ICD-10-CM Diagnosis Code B65.0
Schistosomiasis due to Schistosoma haematobium [urinary schistosomiasis]
B65.0-
ICD-10-CM Diagnosis Code B65.9
Schistosomiasis, unspecified
B65.9
)

Type 1 Excludes

Type 1 Excludes Help

A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as J99. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

respiratory disorders in:
amebiasis (
ICD-10-CM Diagnosis Code A06.5
Amebic lung abscess
Applicable To
- Amebic abscess of lung (and liver)
A06.5
)
blastomycosis (
ICD-10-CM Diagnosis Code B40.0
Acute pulmonary blastomycosis
B40.0-
ICD-10-CM Diagnosis Code B40.2
Pulmonary blastomycosis, unspecified
B40.2
)
candidiasis (
ICD-10-CM Diagnosis Code B37.1
Pulmonary candidiasis
Applicable To
- Candidal bronchitis
- Candidal pneumonia
B37.1
)
coccidioidomycosis (
ICD-10-CM Diagnosis Code B38.0
Acute pulmonary coccidioidomycosis
B38.0-
ICD-10-CM Diagnosis Code B38.2
Pulmonary coccidioidomycosis, unspecified
B38.2
)
cystic fibrosis with pulmonary manifestations (
ICD-10-CM Diagnosis Code E84.0
Cystic fibrosis with pulmonary manifestations
Use Additional
- code to identify any infectious organism present, such as:
- Pseudomonas (B96.5)
E84.0
)
dermatomyositis (
ICD-10-CM Diagnosis Code M33.01
Juvenile dermatomyositis with respiratory involvement
M33.01
,
ICD-10-CM Diagnosis Code M33.11
Other dermatomyositis with respiratory involvement
M33.11
)
histoplasmosis (
ICD-10-CM Diagnosis Code B39.0
Acute pulmonary histoplasmosis capsulati
B39.0-
ICD-10-CM Diagnosis Code B39.2
Pulmonary histoplasmosis capsulati, unspecified
B39.2
)
late syphilis (
ICD-10-CM Diagnosis Code A52.72
Syphilis of lung and bronchus
A52.72
,
ICD-10-CM Diagnosis Code A52.73
Symptomatic late syphilis of other respiratory organs
A52.73
)
polymyositis (
ICD-10-CM Diagnosis Code M33.21
Polymyositis with respiratory involvement
M33.21
)
Sjögren syndrome (
ICD-10-CM Diagnosis Code M35.02
Sjögren syndrome with lung involvement
M35.02
)
systemic lupus erythematosus (
ICD-10-CM Diagnosis Code M32.13
Lung involvement in systemic lupus erythematosus
Applicable To
- Pleural effusion due to systemic lupus erythematosus
M32.13
)
systemic sclerosis (
ICD-10-CM Diagnosis Code M34.81
Systemic sclerosis with lung involvement
Code Also
- if applicable:
- other interstitial pulmonary diseases (J84.89)
- secondary pulmonary arterial hypertension (I27.21)
M34.81
)
Wegener's granulomatosis (
ICD-10-CM Diagnosis Code M31.30
Wegener's granulomatosis without renal involvement
Applicable To
- Wegener's granulomatosis NOS
M31.30-
ICD-10-CM Diagnosis Code M31.31
Wegener's granulomatosis with renal involvement
M31.31
)

The following code(s) above J99 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to J99:

J00-J99
2023 ICD-10-CM Range J00-J99
Diseases of the respiratory system
Note
- When a respiratory condition is described as occurring in more than one site and is not specifically indexed, it should be classified to the lower anatomic site (e.g. tracheobronchitis to bronchitis in J40).
Type 2 Excludes
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- smoke inhalation (T59.81-)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Use Additional
- code, where applicable, to identify:
- exposure to environmental tobacco smoke (Z77.22)
- exposure to tobacco smoke in the perinatal period (P96.81)
- history of tobacco dependence (Z87.891)
- occupational exposure to environmental tobacco smoke (Z57.31)
- tobacco dependence (F17.-)
- tobacco use (Z72.0)
Diseases of the respiratory system

Approximate Synonyms

Interstitial lung disease due to collagen vascular disease
Lung disease in collagen vascular disease
Lung disorder, secondary
Lung involvement associated with another disorder
Restrictive lung disease due to kyphoscoliosis
Restrictive lung mechanics due to kyphoscoliosis

ICD-10-CM J99 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):

196 Interstitial lung disease with mcc
197 Interstitial lung disease with cc
198 Interstitial lung disease without cc/mcc

Convert J99 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change
2022 (effective 10/1/2021): No change
2023 (effective 10/1/2022): No change

Code annotations containing back-references to J99:

Use Additional: E88.02

ICD-10-CM Diagnosis Code E88.02
Plasminogen deficiency
Applicable To
- Dysplasminogenemia
- Hypoplasminogenemia
- Type 1 plasminogen deficiency
- Type 2 plasminogen deficiency
Code Also
- , if applicable, ligneous conjunctivitis (H10.51)
Use Additional
- code for associated findings, such as:
- hydrocephalus (G91.4)
- otitis media (H67.-)
- respiratory disorder related to plasminogen deficiency (J99)

ICD-10-CM Codes Adjacent To J99

J98.19 Other pulmonary collapse

J98.2 Interstitial emphysema

J98.3 Compensatory emphysema

J98.4 Other disorders of lung

J98.5 Diseases of mediastinum, not elsewhere classified

J98.51 Mediastinitis

J98.59 Other diseases of mediastinum, not elsewhere classified

J98.6 Disorders of diaphragm

J98.8 Other specified respiratory disorders

J98.9 Respiratory disorder, unspecified

J99 Respiratory disorders in diseases classified elsewhere

K00 Disorders of tooth development and eruption

K00.0 Anodontia

K00.1 Supernumerary teeth

K00.2 Abnormalities of size and form of teeth

K00.3 Mottled teeth

K00.4 Disturbances in tooth formation

K00.5 Hereditary disturbances in tooth structure, not elsewhere classified

K00.6 Disturbances in tooth eruption

K00.7 Teething syndrome

K00.8 Other disorders of tooth development

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2023 ICD-10-CM Diagnosis Code J99

Respiratory disorders in diseases classified elsewhere

Ankylosing spondylitis

Other late congenital syphilis, symptomatic

Cryoglobulinemia

Early congenital syphilis, symptomatic

Plasminogen deficiency

Schistosomiasis due to Schistosoma haematobium [urinary schistosomiasis]

Schistosomiasis, unspecified

Amebic lung abscess

Acute pulmonary blastomycosis

Pulmonary blastomycosis, unspecified

Pulmonary candidiasis

Acute pulmonary coccidioidomycosis

Pulmonary coccidioidomycosis, unspecified

Cystic fibrosis with pulmonary manifestations

Juvenile dermatomyositis with respiratory involvement

Other dermatomyositis with respiratory involvement

Acute pulmonary histoplasmosis capsulati

Pulmonary histoplasmosis capsulati, unspecified

Syphilis of lung and bronchus

Symptomatic late syphilis of other respiratory organs

Polymyositis with respiratory involvement

Sjögren syndrome with lung involvement

Lung involvement in systemic lupus erythematosus

Systemic sclerosis with lung involvement

Wegener's granulomatosis without renal involvement

Wegener's granulomatosis with renal involvement

Diseases of the respiratory system

Plasminogen deficiency