2023 ICD-10-CM Diagnosis Code K00.4

Disturbances in tooth formation

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • K00.4 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2023 edition of ICD-10-CM K00.4 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of K00.4 - other international versions of ICD-10 K00.4 may differ.
Applicable To
  • Aplasia and hypoplasia of cementum
  • Dilaceration of tooth
  • Enamel hypoplasia (neonatal) (postnatal) (prenatal)
  • Regional odontodysplasia
  • Turner's tooth
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as K00.4. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Hutchinson's teeth and mulberry molars in congenital syphilis (
    ICD-10-CM Diagnosis Code A50.5

    Other late congenital syphilis, symptomatic

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Applicable To
    • Any congenital syphilitic condition specified as late or manifest two years or more after birth.
    A50.5
    )
Type 2 Excludes
Type 2 Excludes Help
A type 2 excludes note represents "not included here". A type 2 excludes note indicates that the condition excluded is not part of the condition it is excluded from but a patient may have both conditions at the same time. When a type 2 excludes note appears under a code it is acceptable to use both the code (K00.4) and the excluded code together.
  • mottled teeth (
    ICD-10-CM Diagnosis Code K00.3

    Mottled teeth

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Dental fluorosis
    • Mottling of enamel
    • Nonfluoride enamel opacities
    Type 2 Excludes
    • deposits [accretions] on teeth (K03.6)
    K00.3
    )
The following code(s) above K00.4 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to K00.4:
  • K00-K95
    2023 ICD-10-CM Range K00-K95

    Diseases of the digestive system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the digestive system
  • K00
    ICD-10-CM Diagnosis Code K00

    Disorders of tooth development and eruption

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • embedded and impacted teeth (K01.-)
    Disorders of tooth development and eruption
Approximate Synonyms
  • Disturbance of tooth formation
  • Tooth formation, abnormal
Clinical Information
  • A localized arrested tooth development which appears to involve most commonly the anterior teeth, usually on one side of the midline, most often the maxillary central and lateral incisors. Roentgenographically, the teeth have a ghostlike appearance. Calcification and bits of prismatic enamel may be found in the pulp and the enamel is thin and absent in part. (jablonski, illustrated dictionary of dentistry, 1982)
ICD-10-CM K00.4 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):
  • 011 Tracheostomy for face, mouth and neck diagnoses or laryngectomy with mcc
  • 012 Tracheostomy for face, mouth and neck diagnoses or laryngectomy with cc
  • 013 Tracheostomy for face, mouth and neck diagnoses or laryngectomy without cc/mcc
  • 157 Dental and oral diseases with mcc
  • 158 Dental and oral diseases with cc
  • 159 Dental and oral diseases without cc/mcc

Convert K00.4 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change

Diagnosis Index entries containing back-references to K00.4:
  • Amelogenesis imperfecta K00.5
    ICD-10-CM Diagnosis Code K00.5

    Hereditary disturbances in tooth structure, not elsewhere classified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Amelogenesis imperfecta
    • Dentinogenesis imperfecta
    • Odontogenesis imperfecta
    • Dentinal dysplasia
    • Shell teeth
    • nonhereditaria K00.4 (segmentalis)
  • Aplasia - see also Agenesis
    • cementum K00.4
  • Calcification
    • dentinal papilla K00.4
  • Dilaceration, tooth K00.4
  • Disturbance(s) - see also Disease
  • Ghost
    • teeth K00.4
  • Hypoplasia, hypoplastic
    • cementum K00.4
    • enamel of teeth K00.4 (neonatal) (postnatal) (prenatal)
    • Turner's K00.4
  • Odontodysplasia, regional K00.4
  • Pitting R60.9
    - see also Edema
    ICD-10-CM Diagnosis Code R60.9

    Edema, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    • Fluid retention NOS
    • teeth K00.4
  • Turner's
    • hypoplasia K00.4 (tooth)
    • tooth K00.4

ICD-10-CM Codes Adjacent To K00.4
J98.59 Other diseases of mediastinum, not elsewhere classified
J98.6 Disorders of diaphragm
J98.8 Other specified respiratory disorders
J98.9 Respiratory disorder, unspecified
J99 Respiratory disorders in diseases classified elsewhere
K00 Disorders of tooth development and eruption
K00.0 Anodontia
K00.1 Supernumerary teeth
K00.2 Abnormalities of size and form of teeth
K00.3 Mottled teeth
K00.4 Disturbances in tooth formation
K00.5 Hereditary disturbances in tooth structure, not elsewhere classified
K00.6 Disturbances in tooth eruption
K00.7 Teething syndrome
K00.8 Other disorders of tooth development
K00.9 Disorder of tooth development, unspecified
K01 Embedded and impacted teeth
K01.0 Embedded teeth
K01.1 Impacted teeth
K02 Dental caries
K02.3 Arrested dental caries

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.